Dysfunctional Mitochondrial Dynamic and Oxidative Phosphorylation Precedes Cardiac Dysfunction in R120G-αB-Crystallin-Induced Desmin-Related Cardiomyopathy
R120G-αB-晶状体蛋白诱导的结蛋白相关心肌病中,线粒体动力学和氧化磷酸化功能障碍先于心脏功能障碍发生。
期刊:Journal of the American Heart Association
影响因子:5.3
doi:10.1161/JAHA.120.017195
Alam, Shafiul; Abdullah, Chowdhury S; Aishwarya, Richa; Morshed, Mahboob; Nitu, Sadia S; Miriyala, Sumitra; Panchatcharam, Manikandan; Kevil, Christopher G; Orr, A Wayne; Bhuiyan, Md Shenuarin