日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Modulating Innate and Adaptive Immunity by (R)-Roscovitine: Potential Therapeutic Opportunity in Cystic Fibrosis

(R)-Roscovitine调节先天性和适应性免疫:囊性纤维化的潜在治疗机会

Meijer, Laurent; Nelson, Deborah J; Riazanski, Vladimir; Gabdoulkhakova, Aida G; Hery-Arnaud, Geneviève; Le Berre, Rozenn; Loaëc, Nadège; Oumata, Nassima; Galons, Hervé; Nowak, Emmanuel; Gueganton, Laetitia; Dorothée, Guillaume; Prochazkova, Michaela; Hall, Bradford; Kulkarni, Ashok B; Gray, Robert D; Rossi, Adriano G; Witko-Sarsat, Véronique; Norez, Caroline; Becq, Frédéric; Ravel, Denis; Mottier, Dominique; Rault, Gilles

Mutations in FBXL4 Cause Mitochondrial Encephalopathy and a Disorder of Mitochondrial DNA Maintenance

FBXL4基因突变导致线粒体脑病和线粒体DNA维持障碍

Dirami, Thassadite; Rode, Baptiste; Jollivet, Mathilde; Da Silva, Nathalie; Escalier, Denise; Gaitch, Natacha; Norez, Caroline; Tuffery, Pierre; Wolf, Jean-Philippe; Becq, Frédéric; Ray, Pierre F; Dulioust, Emmanuel; Gacon, Gérard; Bienvenu, Thierry; Touré, Aminata; Ratzel, Sarah; Cullinan, Sara B; Garber, Kathryn B; Bonnen, Penelope E; Yarham, John W; Besse, Arnaud; Wu, Ping; Faqeih, Eissa A; Al-Asmari, Ali Mohammad; Saleh, Mohammad AM; Eyaid, Wafaa; Hadeel, Alrukban; He, Langping; Smith, Frances; Yau, Shu; Simcox, Eve M; Miwa, Satomi; Donti, Taraka; Abu-Amero, Khaled K; Wong, Lee-Jun; Craigen, William J; Graham, Brett H; Scott, Kenneth L; McFarland, Robert; Taylor, Robert W

CFTR and Ca Signaling in Cystic Fibrosis

囊性纤维化中的CFTR和Ca信号传导

Antigny, Fabrice; Norez, Caroline; Becq, Frédéric; Vandebrouck, Clarisse

Orphan missense mutations in the cystic fibrosis transmembrane conductance regulator: A three-step biological approach to establishing a correlation between genotype and phenotype

囊性纤维化跨膜传导调节因子中的孤儿错义突变:建立基因型与表型相关性的三步生物学方法

Fresquet, Fleur; Clement, Romain; Norez, Caroline; Sterlin, Adélaïde; Melin, Patricia; Becq, Frédéric; Kitzis, Alain; Thoreau, Vincent; Bilan, Frédéric

4-C-Me-DAB and 4-C-Me-LAB - enantiomeric alkyl-branched pyrrolidine iminosugars - are specific and potent α-glucosidase inhibitors; acetone as the sole protecting group

4-C-Me-DAB 和 4-C-Me-LAB 是一对对映异构的烷基支链吡咯烷亚氨基糖,是特异性强且高效的α-葡萄糖苷酶抑制剂;丙酮是唯一的保护基。

da Cruz, Filipa P; Newberry, Scott; Jenkinson, Sarah F; Wormald, Mark R; Butters, Terry D; Alonzi, Dominic S; Nakagawa, Shinpei; Becq, Frederic; Norez, Caroline; Nash, Robert J; Kato, Atsushi; Fleet, George W J

Abnormal spatial diffusion of Ca2+ in F508del-CFTR airway epithelial cells

F508del-CFTR 气道上皮细胞中 Ca2+ 的空间扩散异常

Antigny, Fabrice; Norez, Caroline; Cantereau, Anne; Becq, Frédéric; Vandebrouck, Clarisse

Evidence that CFTR is expressed in rat tracheal smooth muscle cells and contributes to bronchodilation.

有证据表明,CFTR 在大鼠气管平滑肌细胞中表达,并有助于支气管扩张

Vandebrouck Clarisse, Melin Patricia, Norez Caroline, Robert Renaud, Guibert Christelle, Mettey Yvette, Becq Frédéric

Disruption of CFTR chloride channel alters mechanical properties and cAMP-dependent Cl- transport of mouse aortic smooth muscle cells.

CFTR氯离子通道的破坏会改变小鼠主动脉平滑肌细胞的机械特性和cAMP依赖性Cl-转运

Robert Renaud, Norez Caroline, Becq Frédéric