日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Hematopoietic cell transplantation for Wiskott-Aldrich syndrome: a PIDTC report

造血干细胞移植治疗威斯科特-奥尔德里奇综合征:PIDTC报告

Alexander, Jessie L; Dávila Saldaña, Blachy J; Brazauskas, Ruta; Dammalapati, Sravya Gethika; Griffith, Linda M; Shah, Ami J; Shimano, Kristin A; Ochs, Hans D; Bleesing, Jack J; Ebens, Christen L; Kapadia, Malika; Bauchat, Andrea; Kapoor, Neena; Oved, Joseph H; Eissa, Hesham; Lust, Hannah; Keller, Michael D; Haines, Hilary; Chandrakasan, Shanmuganathan; Talano, Julie-An; Rayes, Ahmad; Madden, Lisa; Shereck, Evan; Miller, Holly K; Satter, Lisa Forbes; Martinez, Caridad; Rozmus, Jacob; Bednarski, Jeffrey J; Yu, Lolie C; Chellapandian, Deepakbabu; Aquino, Victor M; Knutsen, Alan; Chong, Hey; Chopek, Ashley; Gillio, Alfred P; Joshi, Avni; Rangarajan, Hemalatha; Moore, Theodore B; Andolina, Jeffrey R; DeSantes, Kenneth B; Vander Lugt, Mark; Prockop, Susan E; Shyr, David C; Sullivan, Kathleen E; Parikh, Suhag; Weinacht, Katja G; Torgerson, Troy R; Marsh, Rebecca; Dvorak, Christopher C; Chan, Alice Y; Haddad, Elie; Heimall, Jennifer R; Pulsipher, Michael A; Leiding, Jennifer W; Kohn, Donald B; Puck, Jennifer M; Notarangelo, Luigi D; Rawlings, David J; Cowan, Morton J; Petrovic, Aleksandra; Pai, Sung-Yun; Burroughs, Lauri M

Clinical spectrum of Wiskott-Aldrich syndrome carriers: Self-reported survey of 193 carriers

Wiskott-Aldrich综合征携带者的临床表现谱:193名携带者的自我报告调查

Chandrakasan, Shanmuganathan; Westbrook, Adrianna; Griffith, Linda M; Hagin, David; Iyengar, Sumathi; Mangurian, Christina; Scalchunes, Chris; Sullivan, Kathleen E; Zablocki, Akiva; Bakshi, Nitya; Sinha, Cynthia; Burroughs, Lauri M; Chan, Alice Y; Dvorak, Christopher C; Haddad, Elie; Heimall, Jennifer; Kohn, Donald B; Leiding, Jennifer W; Notarangelo, Luigi D; Pai, Sung-Yun; Puck, Jennifer M; Pulsipher, Michael A; Marsh, Rebecca A; Torgerson, Troy; Cowan, Morton J; Ochs, Hans D; Parikh, Suhag

222. Rabies Vaccination to Assess Vaccine Responsiveness after B Cell Targeted Chimeric Antigen Receptor (CAR)-T Cell Therapies: The RAVCAR Study

222. 狂犬病疫苗接种评估B细胞靶向嵌合抗原受体(CAR)-T细胞疗法后的疫苗反应性:RAVCAR研究

Warwick, Richard; Palmer, Kenneth; Johnson, Ian; Poullis, Michael; Flaherty, Patrick W; Jatt, Lauren; Krantz, Elizabeth M; Konchan, Anne; Priyamvada, Lalita; Greenberg, Lauren A; Tindbaek, Karyn A; Briggs, Molly; Munoz, Julian; Chalal, Clementine; Gopal, Ajay K; Carpenter, Paul A; Shadman, Mazyar; Cowan, Andrew J; Ochs, Hans D; Kublin, James G; Hahn, William; Panayampalli, Subbian Satheshkumar; Boeckh, Michael J; Hill, Joshua A

Treatment of canine hemophilia A via intraosseous delivery of a platelet-specific factor VIII-lentiviral vector

通过骨内注射血小板特异性因子VIII慢病毒载体治疗犬血友病A

Rementer, Cameron W; Li, Chong; Nichols, Timothy C; Cai, Xiaohe; Joo, Julia; Wang, Xuefeng; Kloos, Mark; George, Nneka; Chao, Ting-Yen; Xu, Yuanyi; Poncz, Mortimer; Ochs, Hans D; Rawlings, David J; Miao, Carol H

COVID-19 vaccination atlas using an integrative systems vaccinology approach

采用整合系统疫苗学方法的 COVID-19 疫苗接种图谱

Prates-Syed, Wasim Aluísio; Fonseca, Dennyson Leandro Mathias da; Pour, Shahab Zaki; Lira, Aline; Cortes, Nelson; Silva, Jaqueline Dinis Queiroz; Carvalho, Evelyn; Filgueiras, Igor Salerno; Vinces, Tania Geraldine Churascari; Schimke, Lena F; Chaves, Lorena C S; Wunderlich, Gerhard; Durães-Carvalho, Ricardo; Dias, Haroldo Dutra; Ochs, Hans D; Câmara, Niels O S; Nakaya, Helder I; Krieger, José E; Cabral-Marques, Otavio; Cabral-Miranda, Gustavo

Case Report: CD40LG Arg203Ile variant underlies atypical phenotype of X-linked hyper IgM syndrome

病例报告:CD40LG Arg203Ile变异是X连锁高IgM综合征非典型表型的致病因素

Nishikawa, Takuro; Tomomasa, Dan; Hijikata, Atsushi; Kasabata, Hiroshi; Okamoto, Yasuhiro; Ochs, Hans D; Kanegane, Hirokazu

Integrative immunology identified interferome signatures in uveitis and systemic disease-associated uveitis

整合免疫学鉴定了葡萄膜炎和系统性疾病相关性葡萄膜炎中的干扰素组特征

Munhoz, Danielle Dias; Fonseca, Dennyson Leandro M; Filgueiras, Igor Salerno; Dias, Haroldo Dutra; Nakaya, Helder I; Jurisica, Igor; Ochs, Hans D; Schimke, Lena F; Rizzo, Luiz Vicente; Cabral-Marques, Otavio

Hypomorphic RAG2 Deficiency Promotes Selection of Self-Reactive B Cells

RAG2功能减退缺陷促进自身反应性B细胞的选择

Thouvenel, Christopher D; Tipton, Christopher M; Yamazaki, Yasuhiro; Zhang, Ting-Ting; Rylaarsdam, Stacey; Hom, Jennifer R; Snead, Catherine; Zhu, Chengsong; Li, Quan-Zhen; Lee, Yu Nee; Kawai, Tomoki; Haque, Neshatul; Zimmermann, Michael T; Ponnan, Sivasankaran Munusamy; Jackson, Shaun W; James, Rich G; Sanz, Ignacio; Notarangelo, Luigi D; Torgerson, Troy R; Ochs, Hans D; Rawlings, David J; Allenspach, Eric J

Dysregulated autoantibodies targeting AGTR1 are associated with the accumulation of COVID-19 symptoms

针对 AGTR1 的失调自身抗体与 COVID-19 症状的累积有关

Fonseca, Dennyson Leandro M; Jäpel, Maj; Gyamfi, Michael Adu; Filgueiras, Igor Salerno; Baiochi, Gabriela Crispim; Ostrinski, Yuri; Halpert, Gilad; Lavi, Yael Bublil; Vojdani, Elroy; Silva-Sousa, Thayna; Usuda, Júlia Nakanishi; E Silva, Juan Carlo Santos; Freire, Paula P; Nóbile, Adriel Leal; Adri, Anny Silva; Barcelos, Pedro Marçal; Corrêa, Yohan Lucas Gonçalves; do Vale, Fernando Yuri Nery; Lopes, Letícia Oliveira; Schmidt, Solveig Lea; Wang, Xiaoqing; Vahldieck, Carl; Fels, Benedikt; Schimke, Lena F; Cabral-Miranda, Gustavo; Hirata, Mario Hiroyuki; AKhan, Taj Ali; Yu, Yen-Rei A; Dalmolin, Rodrigo Js; Amital, Howard; Vojdani, Aristo; Dias, Haroldo Dutra; Nakaya, Helder; Ochs, Hans D; Silverberg, Jonathan I; Zimmerman, Jason; Zyskind, Israel; Rosenberg, Avi Z; Schulze-Forster, Kai; Heidecke, Harald; Catar, Rusan; Moll, Guido; Hackel, Alexander; Kusche-Vihrog, Kristina; Shoenfeld, Yehuda; Riemekasten, Gabriela; Akbarzadeh, Reza; Marques, Alexandre H C; Cabral-Marques, Otavio

Clinical and molecular findings in actin-related inborn errors of immunity: the middle East and North Africa registry

肌动蛋白相关先天性免疫缺陷的临床和分子研究结果:中东和北非登记研究

Chavoshzadeh, Zahra; Fallah, Shahrzad; Zeinali, Vahide; Sharafian, Samin; Delavari, Samaneh; Mesdaghi, Mehrnaz; Djidjik, Reda; Belaid, Brahim; Ikinciogullari, Aydan; Haskologlu, Sule; Dogu, Figen; Genel, Ferah; Gulez, Nesrin; Baris, Safa; Ozen, Ahmet; Karakoc-Aydiner, Elif; Kiykim, Ayça; Meric, Zeynep; Kutukculer, Necil; Aygun, Ayse; Aksu, Guzide; Karaca, Neslihan Edeer; Geyik, Mehmet; Keles, Sevgi; Reisli, Ismail; Nail Guner, Sukru; Boukari, Rachida; Hakem, Saliha; Belbouab, Reda; Barbouche, Mohamed-Ridha; Ben-Mustapha, Imen; Mekki, Najla; Ben-Ali, Meriem; Sobh, Ali; Elnagdy, Marwa; Djenouhat, Kamel; Tahiat, Azzeddine; Shendi, Hiba Mohammed; Alkuwaiti, Amna; Nasrullayeva, Gulnara; Alfars, Tariq; Alsukaiti, Nashat; Massaad, Michel; Mehawej, Cybel; Megarbane, Andre; Irani, Carla; Elghazali, Gehad; Al-Tamemi, Salem; Khalifa, Nisreen; Alzyoud, Raed; Gultekin, Sara Sebnem Kilic; Kose, Hulya; Khodaverdy, Hedieh; Shamsian, Bibi Shahin; Eslami, Narges; Momen, Tooba; Sherkat, Roya; Aleyasin, Soheila; Esmaeilzadeh, Hossein; Ahanchian, Hamid; Salami, Fereshte; Fekrvand, Saba; Dupre, Loïc; Ochs, Hans D; Rezaei, Nima; Al-Herz, Waleed; Abolhassani, Hassan