Folliculin Deletion in the Mouse Kidney Results in Cystogenesis of the Loops of Henle via Aberrant TFEB Activation.
小鼠肾脏中滤泡蛋白的缺失导致亨利氏袢囊肿形成,这是由于 TFEB 异常激活所致。
期刊:American Journal of Pathology
影响因子:3.6
doi:10.1016/j.ajpath.2025.05.010
Shalaby Ola, Ohmori Tomoko, Miike Koichiro, Tanigawa Shunsuke, Wilan Krisna Luh Ade, Calcagnì Alessia, Ballabio Andrea, Kubota Yoshiaki, Schmidt Laura S, Linehan W Marston, Ito Takaaki, Baba Masaya, Nishinakamura Ryuichi