Blunted fat oxidation upon submaximal exercise is partially compensated by enhanced glucose metabolism in children, adolescents, and young adults with Barth syndrome
巴特综合征患儿、青少年和青年在次最大运动强度下脂肪氧化受损,但葡萄糖代谢增强可部分代偿这些受损的脂肪氧化。
期刊:Journal of Inherited Metabolic Disease
影响因子:3.8
doi:10.1002/jimd.12094
Cade, William Todd; Bohnert, Kathryn L; Peterson, Linda R; Patterson, Bruce W; Bittel, Adam J; Okunade, Adewole L; de las Fuentes, Lisa; Steger-May, Karen; Bashir, Adil; Schweitzer, George G; Chacko, Shaji K; Wanders, Ronald J; Pacak, Christina A; Byrne, Barry J; Reeds, Dominic N