日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

RNA Therapeutics for Duchenne Muscular Dystrophy: Exon Skipping, RNA Editing, and Translational Insights from Genome-Edited Microminipig Models

RNA疗法治疗杜氏肌营养不良症:外显子跳跃、RNA编辑以及来自基因组编辑微型猪模型的转化医学见解

Chassin, Alex; Ono, Hiroya; Ashida, Yuki; Imamura, Michihiro; Aoki, Yoshitsugu

Distinct Spectral and Directional Thalamocortical Network Dynamics Define Focal Seizure Evolution

独特的频谱和方向性丘脑皮质网络动力学定义了局灶性癫痫发作的演变

Panchavati, Saarang; Daida, Atsuro; Kanai, Sotaro; Oana, Shingo; Ono, Hiroya; Izumi, Masaki; Kaneko, Kikuko; Fallah, Aria; Qiao, Joe X; Salamon, Noriko; Sankar, Raman; Arnold, Corey; Speier, William; Nariai, Hiroki

Extensive striated muscle damage in a rat model of Duchenne muscular dystrophy with Dmd exons 10-17 duplication.

在患有杜氏肌营养不良症的大鼠模型中,Dmd 外显子 10-17 重复导致广泛的横纹肌损伤

Masson Jean-Daniel, Taglietti Valentina, Ruby François, Ono Hiroya, Mouri Nadir, Jorge Alan, Guillaud Laurent, Tiret Laurent, Relaix Frederic

Dynamic cortical and tractography atlases of proactive and reactive alpha and high-gamma activities

动态皮层和纤维束成像图谱:主动和被动α波和高γ波活动

Ono, Hiroya; Sonoda, Masaki; Sakakura, Kazuki; Kitazawa, Yu; Mitsuhashi, Takumi; Firestone, Ethan; Jeong, Jeong-Won; Luat, Aimee F; Marupudi, Neena I; Sood, Sandeep; Asano, Eishi

Reduced PHOX2B stability causes axonal growth impairment in motor neurons with TARDBP mutations

PHOX2B稳定性降低会导致TARDBP突变运动神经元的轴突生长受损。

Mitsuzawa, Shio; Suzuki, Naoki; Akiyama, Tetsuya; Ishikawa, Mitsuru; Sone, Takefumi; Kawada, Jiro; Funayama, Ryo; Shirota, Matsuyuki; Mitsuhashi, Hiroaki; Morimoto, Satoru; Ikeda, Kensuke; Shijo, Tomomi; Ohno, Akiyuki; Nakamura, Naoko; Ono, Hiroya; Ono, Risako; Osana, Shion; Nakagawa, Tadashi; Nishiyama, Ayumi; Izumi, Rumiko; Kaneda, Shohei; Ikeuchi, Yoshiho; Nakayama, Keiko; Fujii, Teruo; Warita, Hitoshi; Okano, Hideyuki; Aoki, Masashi

Spontaneous modulations of high-frequency cortical activity

高频皮层活动的自发性调节

Ono, Hiroya; Sonoda, Masaki; Silverstein, Brian H; Sonoda, Kaori; Kubota, Takafumi; Luat, Aimee F; Rothermel, Robert; Sood, Sandeep; Asano, Eishi

Distinction between benign and malignant soft tissue tumors based on an ultrasonographic evaluation of vascularity and elasticity

基于超声血管分布和弹性评估区分良性和恶性软组织肿瘤

Ohshika, Shusa; Saruga, Tatsuro; Ogawa, Tetsuya; Ono, Hiroya; Ishibashi, Yasuyuki

The updated retrospective questionnaire study of sporadic inclusion body myositis in Japan

日本散发性包涵体肌炎的最新回顾性问卷调查研究

Suzuki, Naoki; Mori-Yoshimura, Madoka; Yamashita, Satoshi; Nakano, Satoshi; Murata, Ken-Ya; Mori, Megumi; Inamori, Yukie; Matsui, Naoko; Kimura, En; Kusaka, Hirofumi; Kondo, Tomoyoshi; Ito, Hidefumi; Higuchi, Itsuro; Hashiguchi, Akihiro; Nodera, Hiroyuki; Kaji, Ryuji; Tateyama, Maki; Izumi, Rumiko; Ono, Hiroya; Kato, Masaaki; Warita, Hitoshi; Takahashi, Toshiaki; Nishino, Ichizo; Aoki, Masashi

Childhood-onset cerebellar ataxia in Japan: A questionnaire-based survey

日本儿童期发病的小脑共济失调:一项基于问卷调查的研究

Ono, Hiroya; Shimizu-Motohashi, Yuko; Maruo, Kazushi; Takeshita, Eri; Ishiyama, Akihiko; Saito, Takashi; Komaki, Hirofumi; Nakagawa, Eiji; Sasaki, Masayuki

Multicenter questionnaire survey for sporadic inclusion body myositis in Japan

日本散发性包涵体肌炎多中心问卷调查

Suzuki, Naoki; Mori-Yoshimura, Madoka; Yamashita, Satoshi; Nakano, Satoshi; Murata, Ken-Ya; Inamori, Yukie; Matsui, Naoko; Kimura, En; Kusaka, Hirofumi; Kondo, Tomoyoshi; Higuchi, Itsuro; Kaji, Ryuji; Tateyama, Maki; Izumi, Rumiko; Ono, Hiroya; Kato, Masaaki; Warita, Hitoshi; Takahashi, Toshiaki; Nishino, Ichizo; Aoki, Masashi