日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Elevated Serum Bile Acids Predict Poor Liver Outcomes in Children With Alagille Syndrome: Results From the GALA Study Group

血清胆汁酸水平升高预示阿拉吉勒综合征患儿肝脏预后不良:GALA研究组的结果

Perez, Carla Fiorella Murillo; Vandriel, Shannon M; Gonzales, Emmanuel M; Wang, Jian-She; Li, Li-Ting; She, Huiyu; Jankowska, Irena; Czubkowski, Piotr; Gliwicz-Miedzińska, Dorota; Jacquemin, Emmanuel; Bouligand, Jérôme; D'Antiga, Lorenzo; Nicastro, Emanuele; Fischler, Björn; Arnell, Henrik; Siew, Susan M; Stormon, Michael; Loomes, Kathleen M; Piccoli, David A; Rand, Elizabeth B; Squires, James E; Karpen, Saul J; Romero, Rene; Kasahara, Mureo; Önal, Zerrin; Sokal, Étienne; Demaret, Tanguy; Wiecek, Sabina; Lacaille, Florence; Debray, Dominique; Hardikar, Winita; Shankar, Sahana; Valentino, Pamela L; Sundaram, Shikha S; Ebel, Noelle H; Feinstein, Jeffrey A; Waisbourd-Zinman, Orith; Lin, Henry C; Rock, Nathalie; Verkade, Henkjan J; Jensen, M Kyle; Jaramillo, Catalina; Kim, Kyung Mo; Oh, Seak Hee; Brecemiclj, Jernej; Alam, Seema; Indolfi, Giuseppe; Blondet, Niviann; Fawaz, Rima; Nastasio, Silvia; Calvo, Pier Luigi; Nebbia, Gabriella; Arikan, Cigdem; Larson-Nath, Catherine; Zizzo, Andréanne N; Sandahl, Thomas Damgaard; Tzivinikos, Christos; El-Koofy, Nehal M; Elmonem, Mohamed A; Aqul, Amal A; Karnsakul, Wikrom; Bulut, Pinar; Kerkar, Nanda; Wolters, Victorien M; Roberts, Amin J; Evans, Helen M; Sanchez, Maria Camila; Cavalieri, Maria Lorena; Kelly, Deirdre A; Hartley, Jane; Lee, Way Seah; Hajinicolaou, Christina; Lertudomphonwanit, Chatmanee; Fischer, Ryan T; Bernabeu, Jesus Quintero; Quiros-Tejeira, Ruben E; Ferreira, Cristina Targa; Carvalho, Elisa; Eshun, John; Zellos, Aglaia; Dezsőfi, Antal; Pinto, Raquel Borges; Schwarz, Kathleen; Rogalidou, Maria; Garcia, Jennifer; Tamara, María Legarda; Beretta, Marisa; Mujawar, Quais; Santos-Silva, Ermelinda; Busoms, Cristina Molera; Lurz, Eberhard; Gonçalves, Cristina; Jimenez-Rivera, Carolina; Banales, Jesus M; Thompson, Richard J; Hansen, Bettina E; Kamath, Binita M

Biliary atresia: insights into mechanisms using a toxic model of the disease including Wnt and Hippo signaling pathways and microtubules

胆道闭锁:利用包括 Wnt 和 Hippo 信号通路和微管在内的毒性疾病模型深入了解其机制

Sophia Fried, Adi Har-Zahav, Yara Hamudi, Sarah Mahameed, Rasha Mansur, Miri Dotan, Tal Cozacov, Raanan Shamir, Rebecca G Wells, Orith Waisbourd-Zinman

Early angiography improves postoperative clinical outcomes compared to delayed angiography among patients with vascular pathologies following partial nephrectomy

对于部分肾切除术后合并血管病变的患者,早期血管造影比延迟血管造影能改善术后临床结果。

Lasmanovich, Rinat; Mahmud, Husny; Khaitovich, Boris; Zilberman, Dorit E; Rosenzweig, Barak; Laufer, Menachem; Portnoy, Orith; Epstein, Avi; Irony, Avinoah; Dotan, Zohar A

Robotic partial nephrectomy is associated with a lower incidence of urine leakage following nephron-sparing surgery for kidney tumors compared to open and laparoscopic approaches

与开放手术和腹腔镜手术相比,机器人辅助部分肾切除术在肾肿瘤肾单位保留手术后发生尿漏的概率较低。

Mahmud, Husny; Erlich, Tomer; Zilberman, Dorit E; Rosenzweig, Barak; Portnoy, Orith; Dotan, Zohar A

Long-term laboratory follow-up is essential in pediatric patients with celiac

对患有乳糜泻的儿科患者而言,长期实验室随访至关重要。

Krauthammer, Alexander; Guz-Mark, Anat; Zevit, Noam; Waisbourd-Zinman, Orith; Mozer-Glassberg, Yael; Friedler, Vered Nachmias; Rozenfeld Bar Lev, Michal; Matar, Manar; Shouval, Dror; Shamir, Raanan

Primary antibiotic prophylaxis in biliary atresia did not demonstrate decreased infection rate: Multi-centre retrospective study

胆道闭锁患者的一级抗生素预防并未降低感染率:多中心回顾性研究

Brody, Yael; Slae, Mordechai; Amir, Achiya Z; Mozer-Glassberg, Yael; Bar-Lev, Michal; Shteyer, Eyal; Waisbourd-Zinman, Orith

Event-free survival of maralixibat-treated patients with Alagille syndrome compared to a real-world cohort from GALA

与来自 GALA 的真实世界队列相比,接受 maralixibat 治疗的 Alagille 综合征患者的无事件生存期

Hansen, Bettina E; Vandriel, Shannon M; Vig, Pamela; Garner, Will; Mogul, Douglas B; Loomes, Kathleen M; Piccoli, David A; Rand, Elizabeth B; Jankowska, Irena; Czubkowski, Piotr; Gliwicz-Miedzińska, Dorota; Gonzales, Emmanuel M; Jacquemin, Emmanuel; Bouligand, Jérôme; D'Antiga, Lorenzo; Nicastro, Emanuele; Arnell, Henrik; Fischler, Björn; Sokal, Étienne; Demaret, Tanguy; Siew, Susan; Stormon, Michael; Karpen, Saul J; Romero, Rene; Ebel, Noelle H; Feinstein, Jeffrey A; Roberts, Amin J; Evans, Helen M; Sundaram, Shikha S; Chaidez, Alexander; Hardikar, Winita; Shankar, Sahana; Fischer, Ryan T; Lacaille, Florence; Debray, Dominique; Lin, Henry C; Jensen, M Kyle; Jaramillo, Catalina; Karthikeyan, Palaniswamy; Indolfi, Giuseppe; Verkade, Henkjan J; Larson-Nath, Catherine; Quiros-Tejeira, Ruben E; Valentino, Pamela L; Rogalidou, Maria; Dezsőfi, Antal; Squires, James E; Schwarz, Kathleen; Calvo, Pier Luigi; Bernabeu, Jesus Quintero; Zizzo, Andréanne N; Nebbia, Gabriella; Bulut, Pinar; Santos-Silva, Ermelinda; Fawaz, Rima; Nastasio, Silvia; Karnsakul, Wikrom; Tamara, María Legarda; Busoms, Cristina Molera; Kelly, Deirdre A; Sandahl, Thomas Damgaard; Jimenez-Rivera, Carolina; Banales, Jesus M; Mujawar, Quais; Li, Li-Ting; She, Huiyu; Wang, Jian-She; Kim, Kyung Mo; Oh, Seak Hee; Sanchez, Maria Camila; Cavalieri, Maria Lorena; Lee, Way Seah; Hajinicolaou, Christina; Lertudomphonwanit, Chatmanee; Waisbourd-Zinman, Orith; Arikan, Cigdem; Alam, Seema; Carvalho, Elisa; Melere, Melina; Eshun, John; Önal, Zerrin; Desai, Dev M; Wiecek, Sabina; Pinto, Raquel Borges; Wolters, Victorien M; Garcia, Jennifer; Beretta, Marisa; Kerkar, Nanda; Brecelj, Jernej; Rock, Nathalie; Lurz, Eberhard; Blondet, Niviann; Shah, Uzma; Thompson, Richard J; Kamath, Binita M

Oral N-acetylcysteine ameliorates liver fibrosis and enhances regenerative responses in Mdr2 knockout mice

口服 N-乙酰半胱氨酸可改善 Mdr2 基因敲除小鼠的肝纤维化并增强其再生反应

Adi Har-Zahav, Ana Tobar, Sophia Fried, Rachel Sivan, Benjamin J Wilkins, Pierre Russo, Raanan Shamir, Rebecca G Wells, Michael Gurevich, Orith Waisbourd-Zinman

Robotic partial nephrectomy is associated with a significantly decreased rate of postoperative pseudoaneurysm compared to open and laparoscopic partial nephrectomy

与开放式和腹腔镜部分肾切除术相比,机器人辅助部分肾切除术可显著降低术后假性动脉瘤的发生率。

Mahmud, Husny; Haitovic, Boris; Zilberman, Dorit E; Rosenzweig, Barak; Laufer, Menachem; Portnoy, Orith; Fridman, Eddie; Dotan, Zohar A

Low-dose biliatresone treatment of pregnant mice causes subclinical biliary disease in their offspring: Evidence for a spectrum of neonatal injury

低剂量双甲酰亚胺治疗怀孕小鼠会导致其后代出现亚临床胆道疾病:一系列新生儿损伤的证据

Kapish Gupta, Jimmy P Xu, Tamir Diamond, Iris E M de Jong, Andrew Glass, Jessica Llewellyn, Neil D Theise, Orith Waisbourd-Zinman, Jeffrey D Winkler, Edward M Behrens, Clementina Mesaros, Rebecca G Wells