日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Fast and slow strains of misfolded mutant superoxide dismutase 1 in familial amyotrophic lateral sclerosis

家族性肌萎缩侧索硬化症中错误折叠突变超氧化物歧化酶 1 的快慢两种菌株

Xu, Guilian; Dillon, Kristy; Lopez, Amanda; Brkic, Selma; Fromholt, Susan; Ostrow, Lyle W; Glass, Jonathan D; Chakrabarty, Paramita; Ayers, Jacob I; Borchelt, David R

Clinical assessment and interpretation of dysarthria in ALS using attention based deep learning AI models

利用基于注意力机制的深度学习人工智能模型对ALS患者的构音障碍进行临床评估和解读

Merler, Michele; Agurto, Carla; Peller, Julian; Roitberg, Esteban; Taitz, Alan; Trevisan, Marcos A; Navar, Indu; Berry, James D; Fraenkel, Ernest; Ostrow, Lyle W; Cecchi, Guillermo A; Norel, Raquel

Listener effort measures clinically meaningful change of dysarthria in amyotrophic lateral sclerosis

听觉努力程度可衡量肌萎缩侧索硬化症患者构音障碍的临床意义变化

Bingham, Indu Navar; Norel, Raquel; Roitberg, Esteban G; Peller, Julián; Trevisan, Marcos A; Agurto, Carla; Merler, Michele; Shalom, Diego E; Aguirre, Felipe; Embon, Iair; Taitz, Alan; Harris, Donna; Wright, Amy; Seaver, Katie; Sullivan, Stacey; Green, Jordan R; Ostrow, Lyle W; Fraenkel, Ernest; Berry, James D

Immune-related encephalitis after immune checkpoint inhibitor therapy

免疫检查点抑制剂治疗后发生的免疫相关性脑炎

Buckley, Monica W; Balaji Warner, Aanika; Brahmer, Julie; Cappelli, Laura C; Sharfman, William H; Fuchs, Ephraim; Kang, Hyunseok; Forde, Patrick M; Gladstone, Douglas E; Ambinder, Richard; Kelly, Ronan J; Lipson, Evan J; Gojo, Ivana; Lee, Edward J; Johnson, Tory P; Saidha, Shiv; Llinas, Rafael; Ostrow, Lyle W; Naidoo, Jarushka; Probasco, John C

Reliable monitoring of respiratory function with home spirometry in people living with amyotrophic lateral sclerosis

利用家用肺活量计对肌萎缩侧索硬化症患者的呼吸功能进行可靠监测

Peller, Julián; Trevisan, Marcos A; Bujia, Gaston; Aguirre, Felipe; Shalom, Diego E; Taitz, Alan; Henze, Stephanie; Bastola, Silviya; Osik, Jason; Shewcraft, Ryan A; Jiang, Peng; Schwartz, Joel; Heiman-Patterson, Terry; Sherman, Michael E; Wipperman, Matthew F; Levy, Oren; Shou, Guofa; Sillay, Karl A; Ostrow, Lyle W; Fraenkel, Ernest; Berry, James D; Navar Bingham, Indu; Roitberg, Esteban G

Biomarker Qualification for Neurofilament Light Chain in Amyotrophic Lateral Sclerosis: Theory and Practice

肌萎缩侧索硬化症中神经丝轻链生物标志物的鉴定:理论与实践

Benatar, Michael; Ostrow, Lyle W; Lewcock, Joseph W; Bennett, Frank; Shefner, Jeremy; Bowser, Robert; Larkin, Paul; Bruijn, Lucie; Wuu, Joanne

Listener effort quantifies clinically meaningful progression of dysarthria in people living with amyotrophic lateral sclerosis

听者努力程度可量化肌萎缩侧索硬化症患者构音障碍的临床意义进展

Bingham, Indu Navar; Norel, Raquel; Roitberg, Esteban G; Peller, Julián; Trevisan, Marcos A; Agurto, Carla; Shalom, Diego E; Aguirre, Felipe; Embon, Iair; Taitz, Alan; Harris, Donna; Wright, Amy; Seaver, Katie; Sullivan, Stacey; Green, Jordan R; Ostrow, Lyle W; Fraenkel, Ernest; Berry, James D

Distinct transcriptomic profile of satellite cells contributes to preservation of neuromuscular junctions in extraocular muscles of ALS mice

卫星细胞独特的转录组特征有助于ALS小鼠眼外肌中神经肌肉接头的维持。

Li, Ang; Yi, Jianxun; Li, Xuejun; Dong, Li; Ostrow, Lyle W; Ma, Jianjie; Zhou, Jingsong

Somatic Mosaicism in Amyotrophic Lateral Sclerosis and Frontotemporal Dementia Reveals Widespread Degeneration from Focal Mutations

肌萎缩侧索硬化症和额颞叶痴呆症中的体细胞嵌合现象揭示了局灶性突变导致的广泛退化

Zhou, Zinan; Kim, Junho; Huang, August Yue; Nolan, Matthew; Park, Junseok; Doan, Ryan; Shin, Taehwan; Miller, Michael B; Chhouk, Brian; Morillo, Katherine; Yeh, Rebecca C; Kenny, Connor; Neil, Jennifer E; Lee, Chao-Zong; Ohkubo, Takuya; Ravits, John; Ansorge, Olaf; Ostrow, Lyle W; Lagier-Tourenne, Clotilde; Lee, Eunjung Alice; Walsh, Christopher A

Author Correction: Clonally expanded CD8 T cells characterize amyotrophic lateral sclerosis-4

作者更正:克隆扩增的 CD8 T 细胞是肌萎缩侧索硬化症-4 的特征。

Campisi, Laura; Chizari, Shahab; Ho, Jessica S Y; Gromova, Anastasia; Arnold, Frederick J; Mosca, Lorena; Mei, Xueyan; Fstkchyan, Yesai; Torre, Denis; Beharry, Cindy; Garcia-Forn, Marta; Jiménez-Alcázar, Miguel; Korobeynikov, Vladislav A; Prazich, Jack; Fayad, Zahi A; Seldin, Marcus M; De Rubeis, Silvia; Bennett, Craig L; Ostrow, Lyle W; Lunetta, Christian; Squatrito, Massimo; Byun, Minji; Shneider, Neil A; Jiang, Ning; La Spada, Albert R; Marazzi, Ivan