日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Mucociliary and cough clearance in primary ciliary dyskinesia as affected by mutations in RSPH1 or DNAH5

RSPH1 或 DNAH5 基因突变影响原发性纤毛运动障碍的粘液纤毛清除和咳嗽功能

Ostrowski, Lawrence E; Abu-Nasser, Sara; Zeman, Kirby L; Leigh, Margaret W; Zariwala, Maimoona A; Olivier, Kenneth N; Ferkol, Thomas W; Taylor, Corinne N; Ceppe, Agathe S; Knowles, Michael R; Bennett, William D

STAT3-Dependent Regulation of CFTR and Ciliogenesis Is Essential for Mucociliary Clearance and Innate Airway Defense in Hyper-IgE Syndrome

STAT3依赖的CFTR和纤毛发生调控对于高IgE综合征中的黏液纤毛清除和先天性气道防御至关重要

Sun, Ling; Walls, Samantha A; Dang, Hong; Quinney, Nancy L; Sears, Patrick R; Sadritabrizi, Taraneh; Hasegawa, Koichi; Okuda, Kenichi; Asakura, Takanori; Chang, Xiuya; Zheng, Meiqi; Mikami, Yu; Dizmond, Felicia U; Danilova, Daniela; Zhou, Lynn; Deshmukh, Anshulika; Cholon, Deborah M; Radicioni, Giorgia; Rogers, Troy D; Kissner, William J; Markovetz, Matthew R; Guhr Lee, Tara N; Gutay, Mark I; Esther, Charles R Jr; Chua, Michael; Grubb, Barbara R; Ehre, Camille; Kesimer, Mehmet; Hill, David B; Ostrowski, Lawrence E; Button, Brian; Gentzsch, Martina; Robinson, Chevalia; Olivier, Kenneth N; Freeman, Alexandra F; Randell, Scott H; Vladar, Eszter; O'Neal, Wanda K; Boucher, Richard C; Chen, Gang

ODAD4-Related Primary Ciliary Dyskinesia: Report of Five Cases and a Founder Variant in Quebec

ODAD4相关原发性纤毛运动障碍:魁北克省五例病例及一个创始变异体的报告

Bourassa, Marie-Hélène; Sillon, Guillaume; Ding, Shuizi; Chioccioli, Maurizio; Lek, Monkol; Ma, Kaiyue; Mejia-Garcia, Alejandro; Gravel, Simon; Vinh, Donald C; Knowles, Michael R; Leigh, Margaret W; Davis, Stephanie D; Ferkol, Thomas; Olivier, Kenneth N; Schecterman, Elizabeth N; Yin, Weining; Sears, Patrick R; Gentzsch, Martina; Boyles, Susan E; Bennett, William D; Zeman, Kirby L; Ostrowski, Lawrence E; Zariwala, Maimoona A; Shapiro, Adam J

Lipid nanoparticle-encapsulated Dnai1 mRNA rescues ciliary activity in primary ciliary dyskinesia mouse cell models

脂质纳米颗粒包裹的Dnai1 mRNA可挽救原发性纤毛运动障碍小鼠细胞模型中的纤毛活动。

Smith, Amanda J; Sears, Patrick R; Hennig, Mirko; Bhattacharjee, Rumpa B; Yin, Weining; Golliher, Hannah; Ishimaru, Daniella; Lombana, T Noelle; Lockhart, David J; Wustman, Brandon A; Ostrowski, Lawrence E

Promoter Deletion Leading to Allele Specific Expression in a Genetically Unsolved Case of Primary Ciliary Dyskinesia

启动子缺失导致原发性纤毛运动障碍病例中等位基因特异性表达,该病例的遗传病因尚未明确

Beaman, M Makenzie; Yin, Weining; Smith, Amanda J; Sears, Patrick R; Leigh, Margaret W; Ferkol, Thomas W; Kearney, Brendan; Olivier, Kenneth N; Kimple, Adam J; Clarke, Shannon; Huggins, Erin; Nading, Erica; Jung, Seung-Hye; Iyengar, Apoorva K; Zou, Xue; Dang, Hong; Barrera, Alejandro; Majoros, William H; Rehder, Catherine W; Reddy, Timothy E; Ostrowski, Lawrence E; Allen, Andrew S; Knowles, Michael R; Zariwala, Maimoona A; Crawford, Gregory E

Recessively Inherited Deficiency of Secreted WFDC2 (HE4) Causes Nasal Polyposis and Bronchiectasis

隐性遗传的分泌型WFDC2(HE4)缺乏症会导致鼻息肉和支气管扩张

Dougherty, Gerard W; Ostrowski, Lawrence E; Nöthe-Menchen, Tabea; Raidt, Johanna; Schramm, Andre; Olbrich, Heike; Yin, Weining; Sears, Patrick R; Dang, Hong; Smith, Amanda J; Beule, Achim G; Hjeij, Rim; Rutjes, Niels; Haarman, Eric G; Maas, Saskia M; Ferkol, Thomas W; Noone, Peadar G; Olivier, Kenneth N; Bracht, Diana C; Barbry, Pascal; Zaragosi, Laure-Emmanuelle; Fierville, Morgane; Kliesch, Sabine; Wohlgemuth, Kai; König, Julia; George, Sebastian; Loges, Niki T; Ceppe, Agathe; Markovetz, Matthew R; Luo, Hong; Guo, Ting; Rizk, Hoda; Eldesoky, Tarek; Dahlke, Katrin; Boldt, Karsten; Ueffing, Marius; Hill, David B; Pang, Yuan-Ping; Knowles, Michael R; Zariwala, Maimoona A; Omran, Heymut

Development of an inhalable contrast agent targeting the respiratory tract mucus layer for pulmonary ultrasonic imaging

开发一种可吸入的、靶向呼吸道黏液层的造影剂,用于肺部超声成像

Tsuruta, James K; Sears, Patrick R; Rebuli, Meghan E; Weitz, Andrew S; Durham, Phillip G; Clapp, Phillip W; Hill, David B; Ostrowski, Lawrence E; Dayton, Paul A; Caughey, Melissa C

Mucociliary Transport Device Construction and Application to Study Mucociliary Clearance

粘液纤毛清除装置的构建及其在粘液纤毛清除研究中的应用

Sears, Patrick R; Ostrowski, Lawrence E

Mucolytic treatment of chronic rhinosinusitis in a murine model of primary ciliary dyskinesia

在原发性纤毛运动障碍小鼠模型中,黏液溶解剂治疗慢性鼻窦炎

Yin, Weining; Golliher, Hannah L; Ferguson, Amy J; Kimbell, Julia S; Livraghi-Butrico, Alessandra; Rogers, Troy D; Grubb, Barbara R; Kimple, Adam J; Ostrowski, Lawrence E

The role of SPAG1 in the assembly of axonemal dyneins in human airway epithelia

SPAG1在人呼吸道上皮细胞轴丝动力蛋白组装中的作用

Smith, Amanda J; Bustamante-Marin, Ximena M; Yin, Weining; Sears, Patrick R; Herring, Laura E; Dicheva, Nedyalka N; López-Giráldez, Francesc; Mane, Shrikant; Tarran, Robert; Leigh, Margaret W; Knowles, Michael R; Zariwala, Maimoona A; Ostrowski, Lawrence E