日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

New Validated Staging System for Light Chain (AL) Amyloidosis With Stage IIIC Defining Ultra-Poor Risk: AL International Staging System

新的经验证的轻链(AL)淀粉样变性分期系统,其中IIIC期定义了超高危:AL国际分期系统

Khwaja, Jahanzaib; Kirkwood, Amy A; Milani, Paolo; Yohannan, Binoy; Theodorakakou, Foteini; Weverling, Flores; Di Simone, Valeria; Ravichandran, Sriram; Kumar, Shaji; Petropoulos, Ioannis; Mussinelli, Roberta; Cohen, Oliver; Oerlemans, Marish I F J; Muchtar, Eli; Stamatelopoulos, Kimon; Lachmann, Helen J; Gillmore, Julian D; Briasoulis, Alexandros; Gertz, Morie; Whelan, Carol; Venneri, Lucia; Fontana, Marianna; Mahmood, Shameem; Schwotzer, Rahel; Minnema, Monique C; Dispenzieri, Angela; Palladini, Giovanni; Kastritis, Efstathios; Wechalekar, Ashutosh

Eligibility criteria for clinical trials in AL amyloidosis result in exclusion of nearly half of real-world patients

AL淀粉样变性临床试验的入组标准导致近一半的真实世界患者被排除在外。

Bellofiore, Claudia; Basset, Marco; Nuvolone, Mario; Nanci, Martina; Sanna, Giuseppe D; Di Simone, Valeria A; Fogliani, Alessandro; Di Cecca, Monica; Mussinelli, Roberta; Foli, Andrea; Ghazi Esfahani, Matin; Sadrzadeh, Mohammadjavad; Perlini, Stefano; De Luca, Leonardo; Clavreul, Solène; Merlini, Giampaolo; Palladini, Giovanni; Milani, Paolo

Reply: Refining Free Light Chain Ratio in Systemic Amyloidosis

回复:优化系统性淀粉样变性中的游离轻链比例

Milani, Paolo; Sanna, Giuseppe Damiano; Nuvolone, Mario; Merlini, Giampaolo; Palladini, Giovanni

Complex I Modulator BI4500 Reduces MASH by Limiting Oxidative Stress and Reprogramming Lipid Metabolism via AMPK in MCD Rats

复合物 I 调节剂 BI4500 通过限制氧化应激和通过 AMPK 重编程脂质代谢来降低 MCD 大鼠的 MASH 水平

Di Pasqua, Laura Giuseppina; Lotti, Sofia; Trucchi, Michelangelo; Palladini, Giuseppina; Croce, Anna Cleta; Protopapa, Francesca; Feletti, Fausto; Kauschke, Stefan G; Sun, Peng; Vairetti, Mariapia; Ferrigno, Andrea

Left ventriculo-arterial coupling in a contemporary cohort of patients with wild-type transthyretin cardiac amyloidosis treated with tafamidis

在接受他法米地治疗的当代野生型转甲状腺素蛋白心脏淀粉样变性患者队列中,左心室-动脉耦合情况

Sanna, Giuseppe Damiano; Di Simone, Valeria Anna; Milani, Paolo; Fogliani, Alessandro; Mussinelli, Roberta; Guida, Gianluigi; Attanasio, Andrea; Obici, Laura; Basset, Marco; Nanci, Martina; Foli, Andrea; Casu, Gavino; De Luca, Leonardo; Nuvolone, Mario; Merlini, Giampaolo; Perlini, Stefano; Palladini, Giovanni

Daratumumab-based regimens versus CyBorD in newly diagnosed patients with AL amyloidosis and IIIb cardiac stage: A matched case-control study

达雷妥尤单抗联合方案与环磷酰胺、双膦酸盐和地塞米松联合方案治疗新诊断的AL淀粉样变性伴IIIb期心脏疾病患者的比较:一项匹配病例对照研究

Bellofiore, Claudia; Basset, Marco; Sanna, Giuseppe Damiano; Foli, Andrea; Mussinelli, Roberta; Nanci, Martina; Fogliani, Alessandro; Ciardo, Martina; Nuvolone, Mario; Merlini, Giampaolo; Palladini, Giovanni; Milani, Paolo

Kinetics of hematologic response in AL amyloidosis: Insights from clinical and cytogenetic subgroup analysis in the daratumumab era

AL淀粉样变性血液学反应动力学:达雷妥尤单抗时代临床和细胞遗传学亚组分析的启示

Bazarbachi, Abdul-Hamid; Zanwar, Saurabh; Hegenbart, Ute; Trajanova, Despina; Bhutani, Divaya; Gertz, Morie A; Dispenzieri, Angela; Kumar, Shaji; D'Souza, Anita; Patwari, Anannya; Cowan, Andrew; Chen, GuiZhen; Milani, Paolo; Palladini, Giovanni; Sanchorawala, Vaishali; Bodanapu, Geethika; Mohty, Mohamad; Lentzsch, Suzanne; Schönland, Stefan O; Muchtar, Eli; Chakraborty, Rajshekhar

Diagnostic Performance of the New Free Light Chain Ratio in Systemic Amyloidosis

新的游离轻链比值在系统性淀粉样变性诊断中的性能

Milani, Paolo; Sanna, Giuseppe Damiano; Bellofiore, Claudia; Nuvolone, Mario; Basset, Marco; Mussinelli, Roberta; Mazzini, Giulia; Nanci, Martina; Ciardo, Martina; Caminito, Serena; Ghazi Esfahani, Matin; Sadrzadeh, Mohammadjavad; Fogliani, Alessandro; Benigna, Francesca; Guida, Gianluigi; Salinaro, Francesco; Bosoni, Tiziana; Barassi, Alessandra; Foli, Andrea; Albertini, Riccardo; Perlini, Stefano; Merlini, Giampaolo; Palladini, Giovanni

Clinical phenotype and prognosis of real-world patients with wild-type transthyretin amyloid cardiomyopathy treated with tafamidis

接受他法米地治疗的野生型转甲状腺素蛋白淀粉样变性心肌病患者的真实世界临床表型和预后

Porcari, Aldostefano; Milani, Paolo; Longhi, Simone; Cappelli, Francesco; Vagnarelli, Fabio; Aimo, Alberto; Cipriani, Alberto; Gardini, Elisa; Marazia, Stefania; Monda, Emanuele; Tini, Giacomo; Musumeci, Beatrice; Serenelli, Matteo; Cantone, Anna; Lofiego, Carla; Marini, Marco; Vergaro, Giuseppe; Foti, Grazia; Musca, Francesco; Tomasoni, Daniela; Bonacchi, Giacomo; Colio, Federica; Sinigiani, Giulio; De Michieli, Laura; Sturdà, Francesca; Pozzan, Marco; Gentile, Piero; Carigi, Samuela; Bartolotti, Michela; Sena, Giuseppe; Ruotolo, Irene; Sanna, Giuseppe Damiano; Zanoletti, Margherita; Canepa, Marco; Di Marco, Massimo; D'Elia, Emilia; Di Bella, Gianluca; Driussi, Mauro; Imazio, Massimo; Perfetto, Federico; Biagini, Elena; Limongelli, Giuseppe; Metra, Marco; Emdin, Michele; Merlini, Giampaolo; Perlini, Stefano; Merlo, Marco; Palladini, Giovanni; Sinagra, Gianfranco

Feasibility of a Biomarker-Based Screening for Pre-Symptomatic AL Amyloidosis in Patients With Intermediate/High-Risk MGUS

生物标志物筛查中/高危MGUS患者无症状AL淀粉样变性的可行性研究

Mangiacavalli, Silvia; Milani, Paolo; Cartia, Claudio Salvatore; Varettoni, Marzia; Palumbo, Michele; Basset, Marco; Masoni, Valeria; Nuvolone, Mario; Foli, Andrea; Ferretti, Virginia Valeria; Merlini, Giampaolo; Arcaini, Luca; Palladini, Giovanni