日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Excitotoxicity in amyotrophic lateral sclerosis: a key pathogenic mechanism

肌萎缩侧索硬化症中的兴奋性毒性:一种关键的致病机制

Silva-Hucha, Silvia; Hernández, Rosendo G; Baena-López, Diego; Fernández de Sevilla, María Estrella; Paradas, Carmen; Morcuende, Sara

Clinical Heterogeneity and Candidate Biomarkers in POLG-Related Mitochondrial Disease

POLG相关线粒体疾病的临床异质性和候选生物标志物

Bermejo-Guerrero, Laura; Restrepo-Vera, Juan Luis; Martin-Jimenez, Paloma; Navarro-Riquelme, Maria; Garrido-Moraga, Rocío; Ochoa, Luz Edith; González-Quintana, Adrián; Hernandez-Lain, Aurelio; Castillo-Villalba, Jessica; Morís, Germán; Muelas, Nuria; García-Arumí, Elena; González, Victoria; Martínez-Sáez, Elena; Vesperinas, Ana; Llansó, Laura; Juntas-Morales, Raul; Paradas, Carmen; Kapetanovic, Solange; Blázquez, Alberto; Martí, Ramon; Arenas, Joaquín; Martín, Miguel A; Domínguez-González, Cristina

Altered mitochondria-associated ER membrane (MAM) function shifts mitochondrial metabolism in amyotrophic lateral sclerosis (ALS)

线粒体相关内质网膜 (MAM) 功能改变导致肌萎缩侧索硬化症 (ALS) 中的线粒体代谢发生改变

Delfina Larrea #, Kirstin A Tamucci, Khushbu Kabra, Kevin R Velasco, Taekyung D Yun, Marta Pera, Jorge Montesinos, Rishi R Agrawal, Carmen Paradas, John W Smerdon, Emily R Lowry, Anna Stepanova, Belem Yoval-Sanchez, Alexander Galkin, Hynek Wichterle, Estela Area-Gomez #1

HMGCS1 variants cause rigid spine syndrome amenable to mevalonic acid treatment in an animal model.

HMGCS1 变异体可导致脊柱僵硬综合征,在动物模型中可通过甲羟戊酸治疗治愈

Dofash Lein N H, Miles Lee B, Saito Yoshihiko, Rivas Eloy, Calcinotto Vanessa, Oveissi Sara, Serrano Rita J, Templin Rachel, Ramm Georg, Rodger Alison, Haywood Joel, Ingley Evan, Clayton Joshua S, Taylor Rhonda L, Folland Chiara L, Groth David, Hock Daniella H, Stroud David A, Gorokhova Svetlana, Donkervoort Sandra, Bönnemann Carsten G, Sud Malika, VanNoy Grace E, Mangilog Brian E, Pais Lynn, O'Donnell-Luria Anne, Madruga-Garrido Marcos, Scala Marcello, Fiorillo Chiara, Baratto Serena, Traverso Monica, Malfatti Edoardo, Bruno Claudio, Zara Federico, Paradas Carmen, Ogata Katsuhisa, Nishino Ichizo, Laing Nigel G, Bryson-Richardson Robert J, Cabrera-Serrano Macarena, Ravenscroft Gianina

High-Density Lipoprotein-Associated Cholesterol Abnormalities in a Clinical Outcomes Study of Dysferlin-Deficient Limb-Girdle Muscular Dystrophy Type R2

肌营养不良蛋白缺乏型肢带型肌营养不良症R2型临床结局研究中高密度脂蛋白相关胆固醇异常

White, Zoe; Rufibach, Laura; Dressman, Heather Gordish; Hilsden, Heather; Cox, Dan; Spuler, Simone; Day, John W; Jones, Kristi J; Bharucha-Goebel, Diana X; Salort-Campana, Emmanuelle; Pestronk, Alan; Walter, Maggie C; Paradas, Carmen; Stojkovic, Tanya; Mori-Yoshimura, Madoka; Bravver, Elena; Diaz-Manera, Jordi; Pegoraro, Elena; Mendell, Jerry R; Straub, Volker; Bernatchez, Pascal

Interleukin-11 promotes lung adenocarcinoma tumourigenesis and immune evasion

白细胞介素-11促进肺腺癌的肿瘤发生和免疫逃逸

Cristina Cirauqui ,Laura Ojeda ,Itziar Otano ,Irene Pazos ,Alba Santos ,Eva M Garrido-Martín ,Patricia Yagüe ,Javier Ramos-Paradas ,Sonia Molina-Pinelo ,Giovanna Roncador ,José Luis Solórzano ,M Teresa Muñoz ,Patricia Cozar ,Patricia Plaza ,Rocío Suárez ,Marta Jiménez ,Roberto Moreno ,Arantxa Rosado ,Pablo Gámez ,Ricardo García-Luján ,Jon Zugazagoitia ,E Alejandro Sweet-Cordero ,Mariano Barbacid ,Amancio Carnero ,Irene Ferrer ,Luis Paz-Ares

Corrigendum: Microbiota-derived extracellular vesicles: current knowledge, gaps, and challenges in precision nutrition

更正:微生物群来源的细胞外囊泡:精准营养领域的现有知识、空白和挑战

Marquez-Paradas, Elvira; Torrecillas-Lopez, Maria; Barrera-Chamorro, Luna; Del Rio-Vazquez, Jose L; Gonzalez-de la Rosa, Teresa; Montserrat-de la Paz, Sergio

Microbiota-derived extracellular vesicles: current knowledge, gaps, and challenges in precision nutrition

微生物群来源的细胞外囊泡:精准营养领域的现状、空白与挑战

Marquez-Paradas, Elvira; Torrecillas-Lopez, Maria; Barrera-Chamorro, Luna; Del Rio-Vazquez, Jose L; Gonzalez-de la Rosa, Teresa; Montserrat-de la Paz, Sergio

Olive Leaf Protein Hydrolysate as a Novel Source of Antimicrobial Peptides: Peptidomic Characterization and In Silico Evaluation

橄榄叶蛋白水解物作为一种新型抗菌肽来源:肽组学表征和计算机模拟评价

Gonzalez-de la Rosa, Teresa; Herreros-Isidro, Alonso; Marquez-Paradas, Elvira; Barrera-Chamorro, Luna; Leon, Maria J; Montserrat-de la Paz, Sergio

Features of the First Case of Foodborne Botulism Caused by Dual-Toxin Clostridium parabotulinum Subtype A1(B5) in Spain

西班牙首例由双毒素副肉毒梭菌A1(B5)亚型引起的食源性肉毒中毒病例的特征

Valdezate, Sylvia; Valiente, Mónica; Carrasco, Gema; Medina-Pascual, María J; Hurtado, María Isabel; de Pipaón, Maite Ruiz; Garrido, Noelia; Paradas, Carmen; Hernández-Bello, José Ramón; Villalón, Pilar