日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

In vivo bioreactor matures iPSC-CMs for MLP disease modeling.

体内生物反应器使 iPSC-CMs 成熟,用于 MLP 疾病建模

Murphy Sean A, Cho Gunsik, Limphong Pattraranee, Lee Dong I, Kwon Chulan

Hepatocyte-specific activity of TSC22D4 triggers progressive NAFLD by impairing mitochondrial function

TSC22D4在肝细胞中的特异性活性通过损害线粒体功能引发进行性非酒精性脂肪性肝病。

Gretchen Wolff ,Minako Sakurai ,Amit Mhamane ,Maria Troullinaki ,Adriano Maida ,Ioannis K Deligiannis ,Kelvin Yin ,Peter Weber ,Jakob Morgenstern ,Annika Wieder ,Yun Kwon ,Revathi Sekar ,Anja Zeigerer ,Michael Roden ,Matthias Blüher ,Nadine Volk ,Tanja Poth ,Thilo Hackert ,Lena Wiedmann ,Francesca De Angelis Rigotti ,Juan Rodriguez-Vita ,Andreas Fischer ,Rajesh Mukthavaram ,Pattraranee Limphong ,Kiyoshi Tachikawa ,Priya Karmali ,Joseph Payne ,Padmanabh Chivukula ,Bilgen Ekim-Üstünel ,Celia P Martinez-Jimenez ,Julia Szendrödi ,Peter Nawroth ,Stephan Herzig

A Precision Medicine Approach to the Rescue of Function on Malignant Calmodulinopathic Long-QT Syndrome

精准医学方法在恶性钙调蛋白病性长QT间期综合征功能恢复中的应用

Limpitikul, Worawan B; Dick, Ivy E; Tester, David J; Boczek, Nicole J; Limphong, Pattraranee; Yang, Wanjun; Choi, Myoung Hyun; Babich, Jennifer; DiSilvestre, Deborah; Kanter, Ronald J; Tomaselli, Gordon F; Ackerman, Michael J; Yue, David T

Systemic delivery of factor IX messenger RNA for protein replacement therapy

IX 因子信使 RNA 的系统递送用于蛋白质替代疗法

Suvasini Ramaswamy, Nina Tonnu, Kiyoshi Tachikawa, Pattraranee Limphong, Jerel B Vega, Priya P Karmali, Pad Chivukula, Inder M Verma

The Human 343delT HSPB5 Chaperone Associated with Early-onset Skeletal Myopathy Causes Defects in Protein Solubility

与早发性骨骼肌病相关的人类 343delT HSPB5 伴侣导致蛋白质溶解度缺陷

Katie A Mitzelfelt, Pattraranee Limphong, Melinda J Choi, Frances D L Kondrat, Shuping Lai, Kurt D Kolander, Wai-Meng Kwok, Qiang Dai, Michael N Grzybowski, Huali Zhang, Graydon M Taylor, Qiang Lui, Mai T Thao, Judith A Hudson, Rita Barresi, Kate Bushby, Heinz Jungbluth, Elizabeth Wraige, Aron M Geu

Modeling human protein aggregation cardiomyopathy using murine induced pluripotent stem cells

利用小鼠诱导多能干细胞模拟人类蛋白聚集性心肌病

Limphong, Pattraranee; Zhang, Huali; Christians, Elisabeth; Liu, Qiang; Riedel, Michael; Ivey, Kathryn; Cheng, Paul; Mitzelfelt, Katie; Taylor, Graydon; Winge, Dennis; Srivastava, Deepak; Benjamin, Ivor

Glutathione-dependent reductive stress triggers mitochondrial oxidation and cytotoxicity

谷胱甘肽依赖性还原应激引发线粒体氧化和细胞毒性

Huali Zhang, Pattraranee Limphong, Joel Pieper, Qiang Liu, Christopher K Rodesch, Elisabeth Christians, Ivor J Benjamin

Arabidopsis thaliana GLX2-1 contains a dinuclear metal binding site, but is not a glyoxalase 2

拟南芥 GLX2-1 含有双核金属结合位点,但并非乙二醛酶 2

Limphong, Pattraranee; Crowder, Michael W; Bennett, Brian; Makaroff, Christopher A