日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

20-αHydroxycholesterol, an oxysterol in human breast milk, reverses mouse neonatal white matter injury through Gli-dependent oligodendrogenesis

20-α羟基胆固醇是人类母乳中的一种氧固醇,它通过Gli依赖性的少突胶质细胞发生逆转小鼠新生儿白质损伤

Agnes S Chao, Pavle Matak, Kelly Pegram, James Powers, Collin Hutson, Rebecca Jo, Laura Dubois, J Will Thompson, P Brian Smith, Vaibhav Jain, Chunlei Liu, Noelle E Younge, Blaire Rikard, Estefany Y Reyes, Mari L Shinohara, Simon G Gregory, Ronald N Goldberg, Eric J Benner

Severe Iron Metabolism Defects in Mice With Double Knockout of the Multicopper Ferroxidases Hephaestin and Ceruloplasmin

多铜氧化铁酶 Hephaestin 和铜蓝蛋白双敲除小鼠出现严重铁代谢缺陷

Brie K Fuqua, Yan Lu, David M Frazer, Deepak Darshan, Sarah J Wilkins, Linda Dunn, Alex V Loguinov, Scott C Kogan, Pavle Matak, Huijun Chen, Joshua L Dunaief, Chris D Vulpe, Gregory J Anderson

Mutations in TMEM260 Cause a Pediatric Neurodevelopmental, Cardiac, and Renal Syndrome

TMEM260 突变导致儿童神经发育、心脏和肾脏综合征

Asaf Ta-Shma, Tahir N Khan, Asaf Vivante, Jason R Willer, Pavle Matak, Chaim Jalas, Ben Pode-Shakked, Yishay Salem, Yair Anikster, Friedhelm Hildebrandt, Nicholas Katsanis, Orly Elpeleg, Erica E Davis

Temperature-activated ion channels in neural crest cells confer maternal fever-associated birth defects

神经嵴细胞中温度激活离子通道导致孕妇发热相关出生缺陷

Mary R Hutson, Anna L Keyte, Miriam Hernández-Morales, Eric Gibbs, Zachary A Kupchinsky, Ioannis Argyridis, Kyle N Erwin, Kelly Pegram, Margaret Kneifel, Paul B Rosenberg, Pavle Matak, Luke Xie, Jörg Grandl, Erica E Davis, Nicholas Katsanis, Chunlei Liu, Eric J Benner

Disrupted iron homeostasis causes dopaminergic neurodegeneration in mice

铁稳态破坏导致小鼠多巴胺能神经变性

Pavle Matak, Andrija Matak, Sarah Moustafa, Dipendra K Aryal, Eric J Benner, William Wetsel, Nancy C Andrews

Copper deficiency leads to anemia, duodenal hypoxia, upregulation of HIF-2α and altered expression of iron absorption genes in mice

铜缺乏导致小鼠贫血、十二指肠缺氧、HIF-2α上调和铁吸收基因表达改变

Pavle Matak, Sara Zumerle, Maria Mastrogiannaki, Souleiman El Balkhi, Stephanie Delga, Jacques R R Mathieu, François Canonne-Hergaux, Joel Poupon, Paul A Sharp, Sophie Vaulont, Carole Peyssonnaux

HIF-2alpha, but not HIF-1alpha, promotes iron absorption in mice

HIF-2alpha 可促进小鼠铁的吸收,但 HIF-1alpha 则不然

Maria Mastrogiannaki, Pavle Matak, Brian Keith, M Celeste Simon, Sophie Vaulont, Carole Peyssonnaux

Activated macrophages induce hepcidin expression in HuH7 hepatoma cells

活化的巨噬细胞诱导 HuH7 肝癌细胞中铁调素的表达

Pavle Matak, Timothy B Chaston, Bomee Chung, Surjit Kaila Srai, Andrew T McKie, Paul A Sharp