日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Structural and molecular homogeneity of ATTRv-T60A amyloid fibrils across patients and organs

ATTRv-T60A淀粉样蛋白原纤维在不同患者和器官中的结构和分子同质性

Fernandez-Ramirez, Maria Del Carmen; Nguyen, Binh A; Afrin, Shumaila; Singh, Virender; Evers, Bret; Shelton, John M; Escobar, Christian Lopez; Bassett, Parker; Wang, Lanie; Pękała, Maja; Ahmed, Yasmin; Cabrera Hernandez, Luis O; Pedretti, Rose; Singh, Preeti; Canepa, Jacob; Wosztyl, Aleksandra; Li, Yang; Boyer, David R; Cao, Qin; Saelices, Lorena

Mechanism of inhibition of acid-mediated transthyretin aggregation by designed peptides

设计肽抑制酸介导的转甲状腺素蛋白聚集的机制

Sun, Xun; Pedretti, Rose; Dyson, H Jane; Saelices, Lorena; Wright, Peter E

Biomarkers in Subclinical Transthyretin Cardiac Amyloidosis

亚临床转甲状腺素蛋白心脏淀粉样变性的生物标志物

Gulati, Jaskeerat S; Pedretti, Rose; Hendren, Nicholas; Kozlitina, Julia; Saelices, Lorena; Roth, Lori R; Grodin, Justin L

A Shared Amyloid Architecture in Cardiac Fibrils from Three Neuropathy-Associated ATTR Variants

三种与神经病变相关的ATTR变异体心脏纤维中共享的淀粉样蛋白结构

Fernandez-Ramirez, Maria Del Carmen; Afrin, Shumaila; An Nguyen, Binh; Singh, Virender; Pekala, Maja; Singh, Preeti; Ahmed, Yasmin; Pedretti, Rose; Lemoff, Andrew; Kluve-Beckerman, Barbara; Chhapra, Farzeen; Eisenberg, David; Saelices, Lorena

A Rare Unusually Aggressive Form of Hereditary Transthyretin Amyloidosis

一种罕见的、异常凶险的遗传性转甲状腺素蛋白淀粉样变性

Zhang, Jingwen; Roth, Lori R; Wees, Isabel; Phillips, Lauren; Pedretti, Rose; Nguyen, Pauline; Saelices, Lorena; Grodin, Justin L

Detection of Circulating Transthyretin Amyloid Aggregates in Plasma: A Novel Biomarker for Transthyretin Amyloidosis

血浆中循环转甲状腺素蛋白淀粉样蛋白聚集体的检测:转甲状腺素蛋白淀粉样变性的新型生物标志物

Pedretti, Rose; Wang, Lanie; Hanna, Mazen; Benson, Merrill D; Grodin, Justin L; Tang, W H Wilson; Masri, Ahmad; Saelices, Lorena

Structural polymorphism of amyloid fibrils in ATTR amyloidosis revealed by cryo-electron microscopy

冷冻电镜揭示ATTR淀粉样变性中淀粉样原纤维的结构多态性

Nguyen, Binh An; Singh, Virender; Afrin, Shumaila; Yakubovska, Anna; Wang, Lanie; Ahmed, Yasmin; Pedretti, Rose; Fernandez-Ramirez, Maria Del Carmen; Singh, Preeti; Pękała, Maja; Cabrera Hernandez, Luis O; Kumar, Siddharth; Lemoff, Andrew; Gonzalez-Prieto, Roman; Sawaya, Michael R; Eisenberg, David S; Benson, Merrill Douglas; Saelices, Lorena

Author Correction: O-GlcNAc forces an α-synuclein amyloid strain with notably diminished seeding and pathology

作者更正:O-GlcNAc 可诱导 α-突触核蛋白淀粉样变性,显著降低其种子形成和病理特征。

Balana, Aaron T; Mahul-Mellier, Anne-Laure; Nguyen, Binh A; Horvath, Mian; Javed, Afraah; Hard, Eldon R; Jasiqi, Yllza; Singh, Preeti; Afrin, Shumaila; Pedretti, Rose; Singh, Virender; Lee, Virginia M-Y; Luk, Kelvin C; Saelices, Lorena; Lashuel, Hilal A; Pratt, Matthew R

Detection of ATTR aggregates in the plasma of polyneuropathic patients with ATTR-V30M amyloidosis

在患有 ATTR-V30M 淀粉样变性的多发性神经病患者血浆中检测 ATTR 聚集体

Pedretti, Rose; Wang, Lanie; Grodin, Justin L; Masri, Ahmad; Kelly, Jeffery; Saelices, Lorena

ATTRv-V30M amyloid fibrils from heart and nerves exhibit structural homogeneity.

来自心脏和神经的 ATTRv-V30M 淀粉样蛋白原纤维表现出结构同质性

Nguyen Binh An, Afrin Shumaila, Yakubovska Anna, Singh Virender, Pedretti Rose, Bassett Parker, Pekala Maja, Alicea Jaime Vaquer, Kunach Peter, Wang Lanie, Lemoff Andrew, Kluve-Beckerman Barbara, Saelices Lorena