日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

A Shared Amyloid Architecture in Cardiac Fibrils from Three Neuropathy-Associated ATTR Variants

三种与神经病变相关的ATTR变异体心脏纤维中共享的淀粉样蛋白结构

Fernandez-Ramirez, Maria Del Carmen; Afrin, Shumaila; An Nguyen, Binh; Singh, Virender; Pekala, Maja; Singh, Preeti; Ahmed, Yasmin; Pedretti, Rose; Lemoff, Andrew; Kluve-Beckerman, Barbara; Chhapra, Farzeen; Eisenberg, David; Saelices, Lorena

Structural polymorphism of ex-vivo ALECT2 amyloid fibrils revealed by cryo-EM.

冷冻电镜揭示体外ALECT2淀粉样蛋白原纤维的结构多态性

Afrin Shumaila, Nguyen Binh An, Singh Virender, Singh Preeti, Bassett Parker, Pekala Maja, Evers Bret, Lopez Christian, Ahmed Yasmin, Li Li, Kallem Raja Reddy, Lemoff Andrew, Argyropoulos Christos, Kluve-Beckerman Barbara, Saelices Lorena

ATTRv-V30M amyloid fibrils from heart and nerves exhibit structural homogeneity.

来自心脏和神经的 ATTRv-V30M 淀粉样蛋白原纤维表现出结构同质性

Nguyen Binh An, Afrin Shumaila, Yakubovska Anna, Singh Virender, Pedretti Rose, Bassett Parker, Pekala Maja, Alicea Jaime Vaquer, Kunach Peter, Wang Lanie, Lemoff Andrew, Kluve-Beckerman Barbara, Saelices Lorena

Amyloid fibril polymorphism in the heart of an ATTR amyloidosis patient with polyneuropathy attributed to the V122Δ variant

ATTR淀粉样变性患者心脏中淀粉样原纤维多态性,伴有多发性神经病变,归因于V122Δ变异体

Ahmed, Yasmin; Nguyen, Binh An; Afrin, Shumaila; Singh, Virender; Evers, Bret; Singh, Preeti; Pedretti, Rose; Wang, Lanie; Bassett, Parker; Del Carmen Fernandez-Ramirez, Maria; Pekala, Maja; Kluve-Beckerman, Barbara; Saelices, Lorena

ATTRv-V30M Type A amyloid fibrils from heart and nerves exhibit structural homogeneity

来自心脏和神经的ATTRv-V30M A型淀粉样蛋白原纤维表现出结构同质性

Nguyen, Binh An; Afrin, Shumaila; Yakubovska, Anna; Singh, Virender; Alicea, Jaime Vaquer; Kunach, Peter; Singh, Preeti; Pekala, Maja; Ahmed, Yasmin; Fernandez-Ramirez, Maria Del Carmen; Hernandez, Luis O Cabrera; Pedretti, Rose; Bassett, Parker; Wang, Lanie; Lemoff, Andrew; Villalon, Layla; Kluve-Beckerman, Barbara; Saelices, Lorena