Inhibition of iduronic acid biosynthesis by ebselen reduces glycosaminoglycan accumulation in mucopolysaccharidosis type I fibroblasts.
依布硒啉抑制艾杜糖醛酸生物合成,从而减少粘多糖贮积症 I 型成纤维细胞中糖胺聚糖的积累
期刊:Glycobiology
影响因子:3.3
doi:10.1093/glycob/cwab066
Maccarana Marco, Tykesson Emil, Pera Edgar M, Gouignard Nadège, Fang Jianping, Malmström Anders, Ghiselli Giancarlo, Li Jin-Ping