日期 影响因子
日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:
–

BPM31510 Increases the CoQ Pool in Chemically Induced CoQ-Deficient Cells, CoQ-Deficient Patient Fibroblasts, and in Metabolically Active Murine Tissues

BPM31510 可增加化学诱导的辅酶Q缺乏细胞、辅酶Q缺乏患者的成纤维细胞以及代谢活跃的小鼠组织中的辅酶Q池。

期刊:FASEB Journal
影响因子:4.2
doi:10.1096/fj.202503629RR
Aristizabal-Henao, Juan J; Wessel, Sarah R; Stopka, Sylwia A; Karmacharya, Srada; Van Cura, Devon; Pesini, Alba; Nickerson, Kelsey R; Grover, Kashni; Zavidij, Oksana; Ravi, Archna; Mota, Andressa L; Rosen, Kenneth M; Nastke, Maria-Dorothea; Cox, Megan K; Narain, Niven R; Modur, Vijay; Quinzii, Catarina M; Gesta, Stephane; Kiebish, Michael A
成纤维细胞
细胞生物学
代谢
发表日期：2026
文献求助 收藏

Spatial mapping of CoQ10 repletion by BPM31510 in a genetic mouse model (Coq4(F147C)) of coenzyme Q deficiency

利用BPM31510在辅酶Q缺乏症的基因小鼠模型（Coq4(F147C)）中对辅酶Q10补充进行空间定位

期刊:Journal of Lipid Research
影响因子:4.1
doi:10.1016/j.jlr.2026.100987
Barriocanal-Casado, Eliana; Stopka, Sylwia A; Pesini, Alba; Aristizabal-Henao, Juan J; Karmacharya, Srada; Van Cura, Devon; Zhang, Ryan; Nickerson, Kelsey R; Grover, Kashni; Zavidij, Oksana; Wessel, Sarah R; Narain, Niven R; Modur, Vijay; Gesta, Stephane; Kiebish, Michael A; Quinzii, Catarina M
发表日期：2026
文献求助 收藏

Guanylate Kinase 1 Deficiency: A Novel and Potentially Treatable Mitochondrial DNA Depletion/Deletions Disease.

鸟苷酸激酶 1 缺乏症：一种新型且可能可治疗的线粒体 DNA 耗竭/缺失疾病

期刊:Annals of Neurology
影响因子:7.7
doi:10.1002/ana.27071
Hidalgo-Gutierrez Agustin, Shintaku Jonathan, Ramon Javier, Barriocanal-Casado Eliana, Pesini Alba, Saneto Russell P, Garrabou Gloria, Milisenda Jose Cesar, Matas-Garcia Ana, Gort Laura, Ugarteburu Olatz, Gu Yue, Koganti Lahari, Wang Tian, Tadesse Saba, Meneri Megi, Sciacco Monica, Wang Shuang, Tanji Kurenai, Horwitz Marshall S, Dorschner Michael O, Mansukhani Mahesh, Comi Giacomo Pietro, Ronchi Dario, Marti Ramon, Ribes Antonia, Tort Frederic, Hirano Michio
免疫/内分泌
线粒体
发表日期：2024
文献求助 收藏

Mechanisms and Therapeutic Effects of Benzoquinone Ring Analogs in Primary CoQ Deficiencies

苯醌环类似物在原发性辅酶Q缺乏症中的作用机制及治疗效果

期刊:Antioxidants
影响因子:6.6
doi:10.3390/antiox11040665
Pesini, Alba; Hidalgo-Gutierrez, Agustin; Quinzii, Catarina M
发表日期：2022
文献求助 收藏

Uridine Prevents Negative Effects of OXPHOS Xenobiotics on Dopaminergic Neuronal Differentiation

尿苷可预防氧化磷酸化异生物质对多巴胺能神经元分化的负面影响

期刊:Cells
影响因子:5.2
doi:10.3390/cells8111407
Iglesias, Eldris; Bayona-Bafaluy, M Pilar; Pesini, Alba; Garrido-Pérez, Nuria; Meade, Patricia; Gaudó, Paula; Jiménez-Salvador, Irene; Montoya, Julio; Ruiz-Pesini, Eduardo
信号转导
磷酸化
神经科学
发表日期：2019
文献求助 收藏