Reduced elastogenesis: a clue to the arteriosclerosis and emphysematous changes in Schimke immuno-osseous dysplasia?
弹性纤维生成减少:是 Schimke 免疫骨发育不良中动脉硬化和肺气肿改变的线索吗?
期刊:Orphanet Journal of Rare Diseases
影响因子:3.4
doi:10.1186/1750-1172-7-70
Marie Morimoto, Zhongxin Yu, Peter Stenzel, J Marietta Clewing, Behzad Najafian, Christy Mayfield, Glenda Hendson, Justin G Weinkauf, Andrew K Gormley, David M Parham, Umakumaran Ponniah, Jean-Luc André, Yumi Asakura, Mitra Basiratnia, Radovan Bogdanović, Arend Bokenkamp, Dominique Bonneau, Anna Buc