日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Improved functional JAG1 and NOTCH2 variant testing in patients with clinical or suspected Alagille syndrome using new low-Notch activity cells

利用新型低Notch活性细胞,改进对临床诊断或疑似阿拉吉尔综合征患者的JAG1和NOTCH2功能变异检测。

Buhl, Nicole; Pfister, Eva-Doreen; Oliveira, Daniel V; Turetti, Fabio; Lurz, Eberhard; Baumann, Ulrich; Di Donato, Nataliya; Illig, Thomas; Skawran, Britta; Andersson, Emma R; Mašek, Jan; Stalke, Amelie

Endoscopic bile duct stenting as preliminary treatment of complicated choledochal malformation before definitive surgery

内镜下胆管支架置入术作为复杂胆总管畸形根治性手术前的初步治疗。

Weidner, Johannes; Kuebler, Joachim Friedrich; Schneider, Andrea; Dingemann, Jens; Baumann, Ulrich; Pfister, Eva-Doreen; Schukfeh, Nagoud

A farnesoid X receptor T296I variant disrupts ligand-induced FXR activation and thus bile acid transport in progressive familial intrahepatic cholestasis.

法尼醇 X 受体 T296I 变体破坏配体诱导的 FXR 激活,从而破坏进行性家族性肝内胆汁淤积症中的胆汁酸转运。

Behrendt Annika, Bastianelli Alex, Stindt Jan, Pfister Eva-Doreen, Sgodda Malte, Cantz Tobias, Hook Sebastian, Gopalswamy Mohanraj, Grau Kathrin, Brands Stefanie, Dröge Carola, Stalke Amelie, Bonus Michele, Franke Sabine, Baumann Ulrich, Keitel Verena, Gohlke Holger

Crosstalk of injured podocytes with parietal epithelial cells through Wnt4/β-Catenin signaling.

受损足细胞与壁层上皮细胞通过 Wnt4/β-catenin 信号通路发生相互作用

Schwartze Eike, Pfister Eva, Endlich Nicole, Endlich Tim, Amann Kerstin, Büttner-Herold Maike, Pippin Jeff, Shankland Stuart J, Daniel Christoph

Rectal budesonide: A potential game changer after Kasai hepatoportoenterostomy

直肠布地奈德:葛西氏肝门空肠吻合术后的潜在变革者

Langreen, Stefanie; Pauer, Nathalie; Pfister, Eva D; Junge, Norman; Baumann, Ulrich; Madadi-Sanjani, Omid; Petersen, Claus; Dingemann, Jens; Schukfeh, Nagoud

Clinical Outcomes of Percutaneous Transhepatic Biliary Drainage in Pediatric Patients following Liver Transplantation

儿童肝移植术后经皮经肝胆道引流的临床结果

Pape, Thorben; Baumann, Ulrich; Pfister, Eva-Doreen; Vondran, Florian W R; Richter, Nicolas; Dingemann, Jens; Hunkemöller, Anna M; von Garrel, Tabea; Wedemeyer, Heiner; Schneider, Andrea; Lenzen, Henrike; Stahl, Klaus

Native liver survival in bile salt export pump deficiency: results of a retrospective cohort study

胆汁酸输出泵功能不全患者的自体肝脏存活率:一项回顾性队列研究的结果

Pfister, Eva-Doreen; Jaeger, Veronika K; Karch, André; Shay, Denys; Schukfeh, Nagoud; Ohlendorf, Johanna; Junge, Norman; Goldschmidt, Imeke; Stalke, Amelie; Keitel-Anselmino, Verena; Baumann, Ulrich

The Impact of Thrombophilic Factors on Disease Progression in Children with Biliary Atresia-A Single-Centre Cohort Study

血栓形成倾向因素对胆道闭锁患儿疾病进展的影响——一项单中心队列研究

Ohlendorf, Johanna; Kiene, Hella; Wiegandt, Jessica; Karch, André; Jaeger, Veronika K; Laue, Tobias; Junge, Norman; Mutschler, Frauke; Goldschmidt, Imeke; Pfister, Eva-Doreen; Leiskau, Christoph; Petersen, Claus; Madadi-Sanjani, Omid; Kuebler, Joachim Friedrich; Götz, Juliane Katharina; Baumann, Ulrich

Long-Term Outcome Following Liver Transplantation for Primary Hepatic Tumors-A Single Centre Observational Study over 40 Years

原发性肝肿瘤肝移植术后的长期疗效——一项为期40年的单中心观察性研究

Leiskau, Christoph; Junge, Norman; Mutschler, Frauke E; Laue, Tobias; Ohlendorf, Johanna; Richter, Nicolas; Vondran, Florian W R; Pfister, Eva-Doreen; Baumann, Ulrich

Mild Crigler-Najjar Syndrome with Progressive Liver Disease-A Multicenter Retrospective Cohort Study

轻型克里格勒-纳贾尔综合征伴进行性肝病——一项多中心回顾性队列研究

Junge, Norman; Hentschel, Hanna; Krebs-Schmitt, Dorothee; Stalke, Amelie; Pfister, Eva-Doreen; Hartleben, Björn; Claßen, Martin; Querfurt, Alexander; Münch, Veronika; Bufler, Philip; Oh, Jun; Grabhorn, Enke