Dystrophin's central domain forms a complex filament that becomes disorganized by in-frame deletions
肌营养不良蛋白的中心结构域形成复杂的丝状结构,而框内缺失会导致该结构紊乱。
期刊:Journal of Biological Chemistry
影响因子:3.9
doi:10.1074/jbc.M117.809798
Delalande, Olivier; Molza, Anne-Elisabeth; Dos Santos Morais, Raphael; Chéron, Angélique; Pollet, Émeline; Raguenes-Nicol, Céline; Tascon, Christophe; Giudice, Emmanuel; Guilbaud, Marine; Nicolas, Aurélie; Bondon, Arnaud; Leturcq, France; Férey, Nicolas; Baaden, Marc; Perez, Javier; Roblin, Pierre; Piétri-Rouxel, France; Hubert, Jean-François; Czjzek, Mirjam; Le Rumeur, Elisabeth