日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Increased intervals in enzyme replacement therapy for stable type 1 Gaucher disease: A non-inferiority sequential trial emulation

延长酶替代疗法治疗稳定型1型戈谢病的间隔时间:一项非劣效性序贯试验模拟研究

Beydon, Maxime; Stirnemann, Jérôme; Yousfi, Karima; Zebiche, Samira; Hamroun, Dalil; Brassier, Anaïs; Pichard, Samia; Swiader, Laure; de Villemeur, Thierry Billette; Héron, Bénédicte; Dalbies, Florence; Cador, Bérengère; Guemann, Anne-Sophie; Gaches, Francis; Hivert, Bénédicte; Leguy-Seguin, Vanessa; Masseau, Agathe; Pers, Yves-Marie; Pettazzoni, Magali; Bekri, Soumeya; Caillaud, Catherine; Guillou, Edouard Le; Szymanowski, Marie; Astudillo, Leonardo; Mauhin, Wladimir; Nadjar, Yann; Serratrice, Christine; Berger, Marc G; Camou, Fabrice; Belmatoug, Nadia; Nguyen, Yann

Relationship between preoperative supine radiographs and intraoperative coronal spinal alignment in thoracic adolescent idiopathic scoliosis

胸椎青少年特发性脊柱侧弯术前仰卧位X线片与术中冠状位脊柱排列的关系

Luc, François; Pichard, David; Mainard, Nicolas; Simon, Anne-Laure; Saghbiny, Elie; Ould-Slimane, Mourad; Ilharreborde, Brice

Expert-Designed Fact Sheets and AI-Based Analysis of Patient Symptoms to Combat Diagnostic Delays in Inherited Metabolic Diseases

专家设计的情况说明书和基于人工智能的患者症状分析,旨在解决遗传代谢疾病诊断延误问题

Cano, Aline; Chen, Xiaoyi; Khemiri, Azza; Brassier, Anais; Jean-Baptiste, Arnoux; Froissart, Roseline; Bouchereau, Juliette; Hoebeke, Célia; Mazodier, Karin; Héron, Bénédicte; Labrune, Philippe; Caillaud, Catherine; Cheillan, David; Nadjar, Yann; Pichard, Samia; Imbard, Apolline; Pettazzoni, Magali; Douillard, Claire; Nadia, Belmatoug; Calatayud, Anna-Line; Zerguini, Mounira; Garcelon, Nicolas; Benoist, Jean-François; Acquaviva, Cécile; De Lonlay, Pascale

Use of a three-dimensional ultrasound device for noninvasive urine bladder volume measurement in dogs and cats

使用三维超声设备对犬猫进行无创膀胱尿液容量测量

Kaufmann, Hugo; Pichard, Diane; Canonne, Aude-Morgane; Desquilbet, Loïc; Maurey, Christelle

Should PNPO Deficiency Be Treated In Utero? Clinical Findings From Prenatal Pyridoxine Therapy

PNPO缺乏症是否应在子宫内治疗?产前吡哆醇治疗的临床发现

de Puyraimond, Chloé; Pichard, Samia; Girard, Muriel; Delanne, Julian; Faivre, Laurence; Imbard, Apolline; Baurand, Amandine; Benoist, Jean-François; Mills, Philippa B; Clayton, Peter T; Schiff, Manuel

Treatment of Cutaneous Neurofibromas in Neurofibromatosis Type 1 With MEK Inhibitor Selumetinib: A Nonrandomized Clinical Trial

使用MEK抑制剂Selumetinib治疗1型神经纤维瘤病合并皮肤神经纤维瘤:一项非随机临床试验

Gross, Andrea M; Reid, Olivia H; Baldwin, Lauren A; Cannon, Ashley; Choo-Wosoba, Hyoyoung; Steinberg, Seth M; Lobbous, Mina; Wolters, Pamela L; Pichard, Dominique C; Tibery, Cecilia M; Dombi, Eva; Derdak, Joanne; Widemann, Brigitte C; Korf, Bruce R

Towards optimised nutrition therapy after critical illness: a position statement and research framework by the global research initiative on post-intensive care nutrition (GRIP) consortium

优化重症疾病后营养治疗:全球重症监护后营养研究倡议(GRIP)联盟的立场声明和研究框架

Rosseel, Zenzi; Overwater, Noortje M P; Aerts, Maridi; Chapple, Lee-Anne S; Chen, Dechang; Haines, Krista L; Liu, Jiao; Kouw, Imre W K; Ke, Lu; Pichard, Claude; Ridley, Emma J; Singer, Pierre; Waitzberg, Dan L; Li, Weiqin; Wischmeyer, Paul E; An, Youzhong; van Zanten, Arthur R H; Waele, Elisabeth De

Cystic fibrosis liver disease progression in the era of elexacaftor-tezacaftor-ivacaftor

囊性纤维化肝病在依来卡托-替扎卡托-伊伐卡托时代的进展

Mouliade, Charlotte; Parlati, Lucia; Tzedakis, Stylianos; Collier, Mathis; Bouam, Samir; Vallet-Pichard, Anais; D'Halluin-Venier, Valérie; Kanaan, Reem; Pol, Stanislas; Sogni, Philippe; Burgel, Pierre-Régis; Mallet, Vincent

Optimised nanobody-based quenchbodies for enhanced protein detection

优化的基于纳米抗体的淬灭体可增强蛋白质检测

Jordan H Cater ,Nehad S El Salamouni # ,Ghada H Mansour # ,Sebastian Hutchinson # ,Conall Mc Guinness ,Stefan H Mueller ,Richard R Spinks ,Nirukshan Shanmugam ,Adeline Pichard-Kostuch ,Viktor Zahoransky ,Harshad Ghodke ,Marco Ribezzi-Crivellari ,Haibo Yu ,Antoine M van Oijen ,Andrew D Griffiths ,Lisanne M Spenkelink

Immune-driven gene expression loss following intramuscular AAV delivery to non-human primates is only transient.

对非人灵长类动物进行肌肉注射 AAV 后,免疫驱动的基因表达丧失只是暂时的

Journou Malo, Devaux Marie, Jaulin Nicolas, Pichard Virginie, Segovia Mercedes, Moreau Aurélie, Le Duff Johanne, Cuturi Maria Cristina, Guilbaud Mickaël, Adjali Oumeya