日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Overexpression of bank vole PrP(I109) in mice induces a spontaneous atypical prion disease with sex-dependent onset, early NfL elevation, and universal prion strain permissiveness

小鼠体内田鼠 PrP(I109) 的过表达可诱发一种自发性非典型朊病毒病,该病具有性别依赖性发病、早期 NfL 水平升高以及对普遍朊病毒株的易感性。

Eraña, Hasier; Vidal, Enric; Fernández-Borges, Natalia; Charco, Jorge M; Díaz-Domínguez, Carlos M; Sampedro-Torres-Quevedo, Cristina; San-Juan-Ansoleaga, Maitena; Fernández-Muñoz, Eva; Galarza-Ahumada, Josu; Pérez-Castro, Miguel Ángel; Gonçalves-Anjo, Nuno; Piñeiro, Patricia; Pirisinu, Laura; Di Bari, Michele Angelo; Giler, Samanta; Raimondi, Ilaria; Espinosa, Juan Carlos; Vanni, Ilaria; D'Agostino, Claudia; Rodríguez-Cuesta, Juan; Pasetto, Laura; Bonetto, Valentina; González-Martín, Nora; Teijeira, Susana; Zou, Wen-Quan; Geijo, Mariví; Torres, Juan María; Chiesa, Roberto; Sánchez-Martín, Manuel A; Nonno, Romolo; Requena, Jesús R; Castilla, Joaquín

Prions in Muscles of Cervids with Chronic Wasting Disease, Norway

挪威慢性消耗性疾病鹿科动物肌肉中的朊病毒

Vuong, Tram T; Cazzaniga, Federico A; Tran, Linh; Våge, Jørn; Di Bari, Michele; Pirisinu, Laura; D'Agostino, Claudia; Nonno, Romolo; Moda, Fabio; Benestad, Sylvie L

Strain-Dependent Morphology of Reactive Astrocytes in Human- and Animal-Vole-Adapted Prions

人类和动物-田鼠适应性朊病毒中反应性星形胶质细胞的菌株依赖性形态

Bruno, Rosalia; Riccardi, Geraldina; Iacobone, Floriana; Chiarotti, Flavia; Pirisinu, Laura; Vanni, Ilaria; Marcon, Stefano; D'Agostino, Claudia; Giovannelli, Matteo; Parchi, Piero; Agrimi, Umberto; Nonno, Romolo; Di Bari, Michele Angelo

An optimized Western blot assay provides a comprehensive assessment of the physiological endoproteolytic processing of the prion protein.

优化的蛋白质印迹分析可对朊病毒蛋白的生理性内蛋白水解加工进行全面评估

Vanni Ilaria, Iacobone Floriana, D'Agostino Claudia, Giovannelli Matteo, Pirisinu Laura, Altmeppen Hermann Clemens, Castilla Joaquin, Torres Juan Maria, Agrimi Umberto, Nonno Romolo

Characterization of the First Case of Classical Scrapie in a Sheep in Tunisia

突尼斯首例绵羊典型羊瘙痒症病例的特征描述

Amara, Abdelkader; Elmehatli, Kéfia; Di Bari, Michele Angelo; Pirisinu, Laura; Andolsi, Rihab; Gachout, Souhir; Smida, Boubaker Ben; Handous, Meriem; Ammar, Heni Haj; Khorchani, Roukaya; Zrelli, Malek; Iulini, Barbara; Florio, Caterina Lucia; Caramelli, Maria; Casalone, Cristina; De Antoniis, Laura; Riccardi, Geraldina; Esposito, Elena; Giovannelli, Matteo; D'Agostino, Claudia; Chiappini, Barbara; Nonno, Romolo; Agrimi, Umberto; Vaccari, Gabriele

A single amino acid residue in bank vole prion protein drives permissiveness to Nor98/atypical scrapie and the emergence of multiple strain variants

田鼠朊病毒蛋白中单个氨基酸残基导致对Nor98/非典型羊瘙痒症的易感性以及多种毒株变异的出现。

Pirisinu, Laura; Di Bari, Michele Angelo; D'Agostino, Claudia; Vanni, Ilaria; Riccardi, Geraldina; Marcon, Stefano; Vaccari, Gabriele; Chiappini, Barbara; Benestad, Sylvie L; Agrimi, Umberto; Nonno, Romolo

Gerstmann-Sträussler-Scheinker Disease with F198S Mutation Induces Independent Tau and Prion Protein Pathologies in Bank Voles

具有 F198S 突变的 Gerstmann-Sträussler-Scheinker 病在田鼠中诱导独立的 Tau 和朊病毒蛋白病理学

Bruno, Rosalia; Pirisinu, Laura; Riccardi, Geraldina; D'Agostino, Claudia; De Cecco, Elena; Legname, Giuseppe; Cardone, Franco; Gambetti, Pierluigi; Nonno, Romolo; Agrimi, Umberto; Di Bari, Michele Angelo

Chronic wasting disease in Europe: new strains on the horizon

欧洲慢性消耗性疾病:新菌株即将出现

Tranulis, Michael Andreas; Gavier-Widén, Dolores; Våge, Jørn; Nöremark, Maria; Korpenfelt, Sirkka-Liisa; Hautaniemi, Maria; Pirisinu, Laura; Nonno, Romolo; Benestad, Sylvie Lafond

Studies in bank voles reveal strain differences between chronic wasting disease prions from Norway and North America

对田鼠的研究揭示了来自挪威和北美的慢性消耗性疾病朊病毒的毒株差异

Nonno, Romolo; Di Bari, Michele A; Pirisinu, Laura; D'Agostino, Claudia; Vanni, Ilaria; Chiappini, Barbara; Marcon, Stefano; Riccardi, Geraldina; Tran, Linh; Vikøren, Turid; Våge, Jørn; Madslien, Knut; Mitchell, Gordon; Telling, Glenn C; Benestad, Sylvie L; Agrimi, Umberto

Characterization of goat prions demonstrates geographical variation of scrapie strains in Europe and reveals the composite nature of prion strains

对山羊朊病毒的特征分析表明,欧洲羊瘙痒病毒株存在地理差异,并揭示了朊病毒毒株的复合性质。

Nonno, Romolo; Marin-Moreno, Alba; Carlos Espinosa, Juan; Fast, Christine; Van Keulen, Lucien; Spiropoulos, John; Lantier, Isabelle; Andreoletti, Olivier; Pirisinu, Laura; Di Bari, Michele A; Aguilar-Calvo, Patricia; Sklaviadis, Theodoros; Papasavva-Stylianou, Penelope; Acutis, Pier Luigi; Acin, Cristina; Bossers, Alex; Jacobs, Jorge G; Vaccari, Gabriele; D'Agostino, Claudia; Chiappini, Barbara; Lantier, Frederic; Groschup, Martin H; Agrimi, Umberto; Maria Torres, Juan; Langeveld, Jan P M