日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Obscurin deficiency leads to compensated dilated cardiomyopathy and increased arrhythmias.

Obscurin 缺乏会导致代偿性扩张型心肌病和心律失常增加

Pioner Josè Manuel, Pierantozzi Enrico, Coppini Raffaele, Rubino Egidio Maria, Biasci Valentina, Vitale Giulia, Laurino Annunziatina, Santini Lorenzo, Scardigli Marina, Randazzo Davide, Olianti Camilla, Serano Matteo, Rossi Daniela, Tesi Chiara, Cerbai Elisabetta, Lange Stephan, Reggiani Carlo, Sacconi Leonardo, Poggesi Corrado, Ferrantini Cecilia, Sorrentino Vincenzo

Probing relaxed myosin states in hypertrophic cardiomyopathy by second harmonic-generation microscopy

利用二次谐波显微镜探测肥厚型心肌病中松弛的肌球蛋白状态

Arecchi, Giulia; Dente, Marica; Ma, Weikang; Scellini, Beatrice; Piroddi, Nicoletta; Scardigli, Marina; Yu, Jingyuan; Zhao, Jing; Cicchi, Riccardo; Kinegawa, Ryo; Muellenbroich, Caroline; Poggesi, Corrado; Ferrantini, Cecilia; Irving, Thomas C; Regnier, Michael; Sacconi, Leonardo; Tesi, Chiara

A Personalized Approach to Vitamin D Supplementation in Cardiovascular Health Beyond the Bone: An Expert Consensus by the Italian National Institute for Cardiovascular Research

维生素D补充在心血管健康中的个性化应用(超越骨骼层面):意大利国家心血管研究所专家共识

Mattioli, Anna Vittoria; Coppi, Francesca; Severino, Paolo; Penna, Claudia; Pagliaro, Pasquale; Dei Cas, Alessandra; Bucciarelli, Valentina; Madonna, Rosalinda; Tarperi, Cantor; Schena, Federico; Cetrullo, Silvia; Angelone, Tommaso; Rocca, Carmine; Parenti, Astrid; Palazzuoli, Alberto; Margonato, Alberto; Paolillo, Stefania; Perrone Filardi, Pasquale; Barillà, Francesco; Lombardi, Carlo; Pinti, Marcello; Molinari, Claudio; Cevese, Antonio; Novo, Giuseppina; Pizzi, Carmine; Porto, Italo; Poggesi, Corrado; Gallina, Sabina; Ambrosio, Giuseppe; Fedele, Francesco; On Behalf Of The Italian National Institute For Cardiovascular Research Inrc

Myosin Isoform-Dependent Effect of Omecamtiv Mecarbil on the Regulation of Force Generation in Human Cardiac Muscle

奥美卡替夫美卡比对人类心肌收缩力调节的肌球蛋白同工型依赖性效应

Scellini, Beatrice; Piroddi, Nicoletta; Dente, Marica; Pioner, J Manuel; Ferrantini, Cecilia; Poggesi, Corrado; Tesi, Chiara

MYBPC3-c.772G>A mutation results in haploinsufficiency and altered myosin cycling kinetics in a patient induced stem cell derived cardiomyocyte model of hypertrophic cardiomyopathy

MYBPC3-c.772G>A 突变导致肥厚型心肌病患者诱导干细胞衍生心肌细胞模型中单倍体功能不全和肌球蛋白循环动力学改变。

Steczina, Sonette; Mohran, Saffie; Bailey, Logan R J; McMillen, Timothy S; Kooiker, Kristina B; Wood, Neil B; Davis, Jennifer; Previs, Michael J; Olivotto, Iacopo; Pioner, Josè Manuel; Geeves, Michael A; Poggesi, Corrado; Regnier, Michael

Slower Calcium Handling Balances Faster Cross-Bridge Cycling in Human MYBPC3 HCM

较慢的钙处理速度平衡了人类 MYBPC3 HCM 中较快的横桥循环

Pioner, Josè Manuel; Vitale, Giulia; Steczina, Sonette; Langione, Marianna; Margara, Francesca; Santini, Lorenzo; Giardini, Francesco; Lazzeri, Erica; Piroddi, Nicoletta; Scellini, Beatrice; Palandri, Chiara; Schuldt, Maike; Spinelli, Valentina; Girolami, Francesca; Mazzarotto, Francesco; van der Velden, Jolanda; Cerbai, Elisabetta; Tesi, Chiara; Olivotto, Iacopo; Bueno-Orovio, Alfonso; Sacconi, Leonardo; Coppini, Raffaele; Ferrantini, Cecilia; Regnier, Michael; Poggesi, Corrado

Corrigendum: Calcium handling maturation and adaptation to increased substrate stiffness in human iPSC-derived cardiomyocytes: the impact of full-length dystrophin deficiency

更正:人诱导多能干细胞来源的心肌细胞中钙离子处理成熟及对底物刚度增加的适应:全长肌营养不良蛋白缺乏的影响

Pioner, Josè Manuel; Santini, Lorenzo; Palandri, Chiara; Langione, Marianna; Grandinetti, Bruno; Querceto, Silvia; Martella, Daniele; Mazzantini, Costanza; Scellini, Beatrice; Giammarino, Lucrezia; Lupi, Flavia; Mazzarotto, Francesco; Gowran, Aoife; Rovina, Davide; Santoro, Rosaria; Pompilio, Giulio; Tesi, Chiara; Parmeggiani, Camilla; Regnier, Michael; Cerbai, Elisabetta; Mack, David L; Poggesi, Corrado; Ferrantini, Cecilia; Coppini, Raffaele

Lifetime Clinical Course of Hypertrophic Cardiomyopathy: Outcome of the Historical Florence Cohort Over 5 Decades

肥厚型心肌病终生临床病程:佛罗伦萨历史队列50余年随访结果

Maurizi, Niccolò; Olivotto, Iacopo; Maron, Martin S; Bonacchi, Giacomo; Antiochos, Panagiotis; Tomberli, Benedetta; Fumagalli, Carlo; Poggesi, Corrado; Berteotti, Martina; Girolami, Francesca; Cecchi, Franco; Maron, Barry J

The harder the climb the better the view: The impact of substrate stiffness on cardiomyocyte fate

攀登越艰难,风景越美:基质硬度对心肌细胞命运的影响

Querceto, Silvia; Santoro, Rosaria; Gowran, Aoife; Grandinetti, Bruno; Pompilio, Giulio; Regnier, Michael; Tesi, Chiara; Poggesi, Corrado; Ferrantini, Cecilia; Pioner, Josè Manuel

Genotype-Driven Pathogenesis of Atrial Fibrillation in Hypertrophic Cardiomyopathy: The Case of Different TNNT2 Mutations

肥厚型心肌病中房颤的基因型驱动发病机制:不同TNNT2突变的案例

Pioner, Josè Manuel; Vitale, Giulia; Gentile, Francesca; Scellini, Beatrice; Piroddi, Nicoletta; Cerbai, Elisabetta; Olivotto, Iacopo; Tardiff, Jil; Coppini, Raffaele; Tesi, Chiara; Poggesi, Corrado; Ferrantini, Cecilia