日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Blocking RAN translation without altering repeat RNAs rescues C9ORF72-related ALS and FTD phenotypes

阻断 RAN 翻译而不改变重复 RNA 可挽救 C9ORF72 相关 ALS 和 FTD 表型

Jiang, Xin; Schaeffer, Laure; Patni, Divya; Russo, Tommaso; Lee, Chao-Zong; Aguilar, Corey; Marques, Christine; Jansen-West, Karen; Hruska-Plochan, Marian; Ray-Soni, Ananya; Lim, Su Min; Held, Aaron; Yue, Mei; Castellanos Otero, Paula; Aryal, Sandeep; Beaussant, Hortense D A M; Basu, Himanish; Takakuwa, Hiro; Daughrity, Lillian M; Ramesh, Nandini; Da Costa, Paulo; A A Quadros, Ana Rita; Nolan, Matthew; Reyes, Charles Jourdan F; Wheeler, Hayden; Moran, Laura C; Griesman, Grant; Wymann, Benjamin; Trombetta, Bianca A; Lopez-De-Silanes, Emma Sofia; Canori, Michael; Krishnan, Gopinath; Vieira Souza Da Silva, Yasmim; Eriani, Gilbert; Albers, Mark W; Arnold, Steven E; Song, Yuyu; Jain, Ankur; Chiu, Isaac M; Zhang, Yong-Jie; Gao, Fen-Biao; Wainger, Brian J; Polymenidou, Magdalini; Petrucelli, Leonard; Martin, Franck; Lagier-Tourenne, Clotilde

Lysosomal escape and TMEM106B fibrillar core determine TDP-43 seeding outcomes.

溶酶体逃逸和 TMEM106B 纤维核心决定 TDP-43 播种结果。

Zhong Weijia, Scialò Carlo, Gatta Beatrice, Häfliger Manon, Leu Noemi, Lurati Flavio, Peter Martina, Ramesh Nandini, Roschitzki Bernd, Jagannath Somanath, Manglunia Ruchi, de Cecco Elena, Lim Su Min, Wilkins Oscar G, Aguzzi Adriano, Ward Michael, Fratta Pietro, Petrucelli Leonard, Lagier-Tourenne Clotilde, Polymenidou Magdalini

Antimicrobial activity of iron-depriving pyoverdines against human opportunistic pathogens.

缺铁绿脓菌素对人类机会性病原体的抗菌活性

Vollenweider Vera, Rehm Karoline, Chepkirui Clara, Pérez-Berlanga Manuela, Polymenidou Magdalini, Piel Jörn, Bigler Laurent, Kümmerli Rolf

Association between markers of brain pathology and verbal memory binding in autosomal dominant Alzheimer’s disease

常染色体显性遗传阿尔茨海默病中脑部病理标志物与言语记忆结合之间的关联

Cordts, Isabell; Wachinger, Annika; Scialo, Carlo; Lingor, Paul; Polymenidou, Magdalini; Buratti, Emanuele; Feneberg, Emily; Parra‐Rodriguez, Mario A; Baena, Ana Y; Munera, Diana; Badillo‐Cabrera, Alex L; Félix, Nikole A Bonillas; Lopera, Francisco; Quiroz, Yakeel T

Comprehensive evaluation of human-derived anti-poly-GA antibodies in cellular and animal models of C9orf72 disease

在C9orf72疾病的细胞和动物模型中对人源抗poly-GA抗体进行全面评估

Jambeau, Melanie; Meyer, Kevin D; Hruska-Plochan, Marian; Tabet, Ricardos; Lee, Chao-Zong; Ray-Soni, Ananya; Aguilar, Corey; Savage, Kitty; Mishra, Nibha; Cavegn, Nicole; Borter, Petra; Lin, Chun-Chia; Jansen-West, Karen R; Jiang, Jie; Freyermuth, Fernande; Li, Nan; De Rossi, Pierre; Pérez-Berlanga, Manuela; Jiang, Xin; Daughrity, Lilian M; Pereira, João; Narayanan, Sarav; Gu, Yuanzheng; Dhokai, Shekhar; Dalkilic-Liddle, Isin; Maniecka, Zuzanna; Weber, Julien; Workman, Michael; McAlonis-Downes, Melissa; Berezovski, Eugene; Zhang, Yong-Jie; Berry, James; Wainger, Brian J; Kankel, Mark W; Rushe, Mia; Hock, Christoph; Nitsch, Roger M; Cleveland, Don W; Petrucelli, Leonard; Gendron, Tania F; Montrasio, Fabio; Grimm, Jan; Polymenidou, Magdalini; Lagier-Tourenne, Clotilde

Protein Phase Separation: A New Phase in Cell Biology

蛋白质相分离:细胞生物学的新阶段

Boeynaems, Steven; Alberti, Simon; Fawzi, Nicolas L; Mittag, Tanja; Polymenidou, Magdalini; Rousseau, Frederic; Schymkowitz, Joost; Shorter, James; Wolozin, Benjamin; Van Den Bosch, Ludo; Tompa, Peter; Fuxreiter, Monika

Disease-modifying effects of metabolic perturbations in ALS/FTLD

代谢紊乱对肌萎缩侧索硬化症/额颞叶痴呆症的疾病修饰作用

Jawaid, Ali; Khan, Romesa; Polymenidou, Magdalini; Schulz, Paul E

Biological Spectrum of Amyotrophic Lateral Sclerosis Prions

肌萎缩侧索硬化症朊病毒的生物学谱

Polymenidou, Magdalini; Cleveland, Don W

Protease resistance of infectious prions is suppressed by removal of a single atom in the cellular prion protein

通过去除细胞朊病毒蛋白中的单个原子,可以抑制传染性朊病毒的蛋白酶抗性。

Leske, Henning; Hornemann, Simone; Herrmann, Uli Simon; Zhu, Caihong; Dametto, Paolo; Li, Bei; Laferriere, Florent; Polymenidou, Magdalini; Pelczar, Pawel; Reimann, Regina Rose; Schwarz, Petra; Rushing, Elisabeth Jane; Wüthrich, Kurt; Aguzzi, Adriano

Prion-like propagation as a pathogenic principle in frontotemporal dementia

朊病毒样传播是额颞叶痴呆症的致病机制

Hock, Eva-Maria; Polymenidou, Magdalini