日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Decreasing TfR1 expression reverses anemia and hepcidin suppression in β-thalassemic mice

降低 TfR1 表达可逆转 β-地中海贫血小鼠的贫血和铁调素抑制。

Li, Huihui; Choesang, Tenzin; Bao, Weili; Chen, Huiyong; Feola, Maria; Garcia-Santos, Daniel; Li, Jie; Sun, Shuming; Follenzi, Antonia; Pham, Petra; Liu, Jing; Zhang, Jinghua; Ponka, Prem; An, Xiuli; Mohandas, Narla; Fleming, Robert E; Rivella, Stefano; Li, Guiyuan; Ginzburg, Yelena Z

Extracellular glycine is necessary for optimal hemoglobinization of erythroid cells

细胞外甘氨酸对于红细胞的最佳血红蛋白化是必需的。

Garcia-Santos, Daniel; Schranzhofer, Matthias; Bergeron, Richard; Sheftel, Alex D; Ponka, Prem

Response to: Dietary and pharmacological factors affecting iron absorption in mice and man

回复:影响小鼠和人类铁吸收的饮食和药物因素

Fillebeen, Carine; Gkouvatsos, Konstantinos; Fragoso, Gabriela; Calvé, Annie; Garcia-Santos, Daniel; Buffler, Marzell; Becker, Christiane; Schümann, Klaus; Ponka, Prem; Santos, Manuela M; Pantopoulos, Kostas

Mice are poor heme absorbers and do not require intestinal Hmox1 for dietary heme iron assimilation

小鼠对血红素的吸收能力较差,不需要肠道Hmox1来吸收膳食中的血红素铁。

Fillebeen, Carine; Gkouvatsos, Konstantinos; Fragoso, Gabriela; Calvé, Annie; Garcia-Santos, Daniel; Buffler, Marzell; Becker, Christiane; Schümann, Klaus; Ponka, Prem; Santos, Manuela M; Pantopoulos, Kostas

Hepcidin bound to α2-macroglobulin reduces ferroportin-1 expression and enhances its activity at reducing serum iron levels.

铁调素与α2-巨球蛋白结合,可降低铁转运蛋白-1的表达,并增强其降低血清铁水平的活性

Huang Michael Li-Hsuan, Austin Christopher J D, Sari Marie-Agnès, Suryo Rahmanto Yohan, Ponka Prem, Vyoral Daniel, Richardson Des R

The long history of iron in the Universe and in health and disease

铁在宇宙、健康和疾病中的悠久历史

Sheftel, Alex D; Mason, Anne B; Ponka, Prem

Nramp1 promotes efficient macrophage recycling of iron following erythrophagocytosis in vivo

Nramp1促进巨噬细胞在体内吞噬红细胞后有效回收铁。

Soe-Lin, Shan; Apte, Sameer S; Andriopoulos, Billy Jr; Andrews, Marc C; Schranzhofer, Matthias; Kahawita, Tanya; Garcia-Santos, Daniel; Ponka, Prem

Dysregulation of iron homeostasis in the CNS contributes to disease progression in a mouse model of amyotrophic lateral sclerosis

中枢神经系统铁稳态失调会导致肌萎缩侧索硬化症小鼠模型疾病进展。

Jeong, Suh Young; Rathore, Khizr I; Schulz, Katrin; Ponka, Prem; Arosio, Paolo; David, Samuel

Ceruloplasmin protects injured spinal cord from iron-mediated oxidative damage

铜蓝蛋白可保护受损脊髓免受铁介导的氧化损伤。

Rathore, Khizr I; Kerr, Bradley J; Redensek, Adriana; López-Vales, Rubèn; Jeong, Suh Young; Ponka, Prem; David, Samuel

Use of Nramp2-transfected Chinese hamster ovary cells and reticulocytes from mk/mk mice to study iron transport mechanisms

利用转染了Nramp2的中国仓鼠卵巢细胞和mk/mk小鼠的网织红细胞研究铁转运机制

Zhang, An-Sheng; Canonne-Hergaux, Francois; Gruenheid, Samantha; Gros, Philippe; Ponka, Prem