Synapse alterations precede neuronal damage and storage pathology in a human cerebral organoid model of CLN3-juvenile neuronal ceroid lipofuscinosis
在 CLN3-青少年神经元蜡样脂褐素沉积症的人类脑器官模型中,突触改变先于神经元损伤和储存病理
期刊:Acta Neuropathologica Communications
影响因子:6.2
doi:10.1186/s40478-019-0871-7
Gemma Gomez-Giro, Jonathan Arias-Fuenzalida, Javier Jarazo, Dagmar Zeuschner, Muhammad Ali, Nina Possemis, Silvia Bolognin, Rashi Halder, Christian Jäger, Willemijn F E Kuper, Peter M van Hasselt, Holm Zaehres, Antonio Del Sol, Herman van der Putten, Hans R Schöler, Jens C Schwamborn