日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Readthrough-induced misincorporated amino acid ratios guide mutant-specific therapeutic approaches for two CFTR nonsense mutations

通读诱导的错误氨基酸比例可指导针对两种 CFTR 无义突变的突变体特异性治疗方法

Aiswarya Premchandar, Ruiji Ming, Abed Baiad, Dillon F Da Fonte, Haijin Xu, Denis Faubert, Guido Veit, Gergely L Lukacs

Folding correctors can restore CFTR posttranslational folding landscape by allosteric domain-domain coupling

折叠校正器可以通过变构域-域耦合恢复 CFTR 翻译后折叠景观

Naoto Soya, Haijin Xu, Ariel Roldan, Zhengrong Yang, Haoxin Ye, Fan Jiang, Aiswarya Premchandar, Guido Veit, Susan P C Cole, John Kappes, Tamás Hegedüs, Gergely L Lukacs

A PI3Kγ mimetic peptide triggers CFTR gating, bronchodilation, and reduced inflammation in obstructive airway diseases

PI3Kγ模拟肽可触发CFTR门控、支气管扩张并减轻阻塞性气道疾病中的炎症

Ghigo, Alessandra; Murabito, Alessandra; Sala, Valentina; Pisano, Anna Rita; Bertolini, Serena; Gianotti, Ambra; Caci, Emanuela; Montresor, Alessio; Premchandar, Aiswarya; Pirozzi, Flora; Ren, Kai; Della Sala, Angela; Mergiotti, Marco; Richter, Wito; de Poel, Eyleen; Matthey, Michaela; Caldrer, Sara; Cardone, Rosa A; Civiletti, Federica; Costamagna, Andrea; Quinney, Nancy L; Butnarasu, Cosmin; Visentin, Sonja; Ruggiero, Maria Rosaria; Baroni, Simona; Crich, Simonetta Geninatti; Ramel, Damien; Laffargue, Muriel; Tocchetti, Carlo G; Levi, Renzo; Conti, Marco; Lu, Xiao-Yun; Melotti, Paola; Sorio, Claudio; De Rose, Virginia; Facchinetti, Fabrizio; Fanelli, Vito; Wenzel, Daniela; Fleischmann, Bernd K; Mall, Marcus A; Beekman, Jeffrey; Laudanna, Carlo; Gentzsch, Martina; Lukacs, Gergely L; Pedemonte, Nicoletta; Hirsch, Emilio

Keratin 8 is a scaffolding and regulatory protein of ERAD complexes

角蛋白 8 是 ERAD 复合物的支架和调节蛋白

Iwona Maria Pranke, Benoit Chevalier #, Aiswarya Premchandar #, Nesrine Baatallah, Kamil F Tomaszewski, Sara Bitam, Danielle Tondelier, Anita Golec, Jan Stolk, Gergely L Lukacs, Pieter S Hiemstra, Michal Dadlez, David A Lomas, James A Irving, Agnes Delaunay-Moisan, Eelco van Anken, Alexandre Hinzpet

Outcomes of liver transplantation in recipients with previous coronavirus disease 2019 infection

既往感染过2019冠状病毒病的患者接受肝移植的预后

Rajakumar, Akila; Paulin, Susan; Velusamy, Premchandar; Devarajan, Vidya; Jothimani, Dinesh; Rajalingam, Rajesh; Rammohan, Ashwin; Rela, Mohamed

Mutation-specific dual potentiators maximize rescue of CFTR gating mutants

突变特异性双重增强剂可最大限度地挽救 CFTR 门控突变体

Veit, Guido; Da Fonte, Dillon F; Avramescu, Radu G; Premchandar, Aiswarya; Bagdany, Miklos; Xu, Haijin; Bensinger, Dennis; Stubba, Daniel; Schmidt, Boris; Matouk, Elias; Lukacs, Gergely L

Phosphorylation-dependent modulation of CFTR macromolecular signalling complex activity by cigarette smoke condensate in airway epithelia

香烟烟雾冷凝物在呼吸道上皮中对 CFTR 大分子信号复合物活性的磷酸化依赖性调节

Andrea Schnúr, Aiswarya Premchandar, Miklos Bagdany, Gergely L Lukacs

New insights into interactions between the nucleotide-binding domain of CFTR and keratin 8

对 CFTR 核苷酸结合域与角蛋白 8 之间相互作用的新见解

Aiswarya Premchandar, Anna Kupniewska, Arkadiusz Bonna, Grazyna Faure, Tomasz Fraczyk, Ariel Roldan, Brice Hoffmann, Mélanie Faria da Cunha, Harald Herrmann, Gergely L Lukacs, Aleksander Edelman, Michał Dadlez

Common source but a rare cause for intraoperative breathing circuit leak: Every anaesthesiologist should be aware of

术中呼吸回路漏气的常见来源,但却是罕见原因:每位麻醉医师都应该了解

Govindarajulu, Dhanabagyam; Vijayakumar, Vinodhadevi; Velusamy, Premchandar