日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

How to Manage Venous Thromboembolism Risk during Pregnancy in Patients with Inherited Antithrombin Deficiency?

妊娠期遗传性抗凝血酶缺乏症患者如何管理静脉血栓栓塞风险?

Mauge, Laetitia; Madar, Hugo; Carré, Julie; Fiore, Mathieu; Gendron, Nicolas; Mouton, Christine; Proulle, Valérie; Suchon, Pierre; Trillot, Nathalie; Lechat, Thomas; Sentilhes, Loïc; Macchi, Laurent

Increased RhoA pathway activation downstream of αIIbβ3/SRC contributes to heterozygous Bernard Soulier syndrome

αIIbβ3/SRC下游RhoA通路激活增强是导致杂合子Bernard Soulier综合征的原因之一。

Lordier, Larissa; Di Buduo, Christian A; Kauskot, Alexandre; Balayn, Nathalie; Lavenu-Bombled, Cécile; Baschieri, Francesco; Proulle, Valérie; Oyarzun, Cecilia P Marin; Careddu, Francesca; Biunno, Ida; Manoliu, Tudor; Rameau, Philippe; Plo, Isabelle; Papadopoulos, Nicolas; Constantinescu, Stefan; Vainchenker, William; Nguyen, Guillaume Nam; Ballerini, Paola; Favier, Remi; Balduini, Alessandra; Raslova, Hana

The IgG-degrading enzyme, Imlifidase, restores the therapeutic activity of FVIII in inhibitor-positive hemophilia A mice

IgG降解酶Imlifidase可恢复抑制剂阳性A型血友病小鼠体内FVIII的治疗活性。

Bou-Jaoudeh, Melissa; Delignat, Sandrine; Daventure, Victoria; Astermark, Jan; Lévesque, Hervé; Dimitrov, Jordan D; Deligne, Claire; Proulle, Valérie; Lacroix-Desmazes, Sébastien

A thrombopoietin receptor agonist to rescue an unusual platelet transfusion-induced reaction in a p.V1316M-associated von Willebrand disease type 2B patient

血小板生成素受体激动剂用于挽救一名携带p.V1316M突变的2B型血管性血友病患者发生的异常血小板输注诱发反应

Casari, Caterina; Favier, Remi; Legendre, Paulette; Kauskot, Alexandre; Adam, Frederic; Picard, Veronique; Lenting, Peter T; Denis, Cecile V; Proulle, Valerie

Monoclonal gammopathy of clinical significance: in vivo demonstration of the anti-thrombotic effect of an acquired anti-thrombin antibody

具有临床意义的单克隆丙种球蛋白病:获得性抗凝血酶抗体的抗血栓作用的体内证实

Schell, Berenice; Desconclois, Celine; Mariette, Xavier; Goujard, Cecile; Lenting, Peter J; Denis, Cecile V; Proulle, Valerie

Piezo1-xerocytosis red cell metabolome shows impaired glycolysis and increased hemoglobin oxygen affinity

Piezo1-干血症红细胞代谢组显示糖酵解受损和血红蛋白氧亲和力增加

Kiger, Laurent; Oliveira, Lydie; Guitton, Corinne; Bendélac, Laurence; Ghazal, Kaldoun; Proulle, Valérie; Galacteros, Frédéric; Junot, Christophe; Fenaille, François; Roméo, Paul-Henri; Garçon, Loic; Picard, Véronique

Effectiveness and safety of hFVIII/VWF concentrate (Voncento(®)) in patients with inherited von Willebrand disease requiring surgical procedures: the OPALE multicentre observational study

hFVIII/VWF浓缩物(Voncento®)治疗需要手术的遗传性血管性血友病患者的有效性和安全性:OPALE多中心观察性研究

Rugeri, Lucia; d'Oiron, Roseline; Harroche, Annie; Proulle, Valérie; Mourey, Guillaume; De Raucourt, Emmanuelle; Desprez, Dominique; Baikian, Nathalie Itzhar; Petesch, Brigitte Pan; Borel-Derlon, Annie; Combe, Sophie; Frotscher, Birgit; Hassoun, Abel; Catovic, Hasan; Bracquart, Diane; Trossaërt, Marc

Rapid Gardos Hereditary Xerocytosis Diagnosis in 8 Families Using Reticulocyte Indices

利用网织红细胞指数对8个家族进行Gardos遗传性干红细胞症的快速诊断

Picard, Véronique; Guitton, Corinne; Mansour-Hendili, Lamisse; Jondeau, Bernard; Bendélac, Laurence; Denguir, Maha; Demagny, Julien; Proulle, Valérie; Galactéros, Frédéric; Garçon, Loic

Clinical and biological features in PIEZO1-hereditary xerocytosis and Gardos channelopathy: a retrospective series of 126 patients

PIEZO1 遗传性口干症和 Gardos 通道病患者的临床和生物学特征:一项回顾性研究分析了 126 例患者

Picard, Véronique; Guitton, Corinne; Thuret, Isabelle; Rose, Christian; Bendelac, Laurence; Ghazal, Kaldoun; Aguilar-Martinez, Patricia; Badens, Catherine; Barro, Claire; Bénéteau, Claire; Berger, Claire; Cathébras, Pascal; Deconinck, Eric; Delaunay, Jacques; Durand, Jean-Marc; Firah, Nadia; Galactéros, Frédéric; Godeau, Bertrand; Jaïs, Xavier; de Jaureguiberry, Jean-Pierre; Le Stradic, Camille; Lifermann, François; Maffre, Robert; Morin, Gilles; Perrin, Julien; Proulle, Valérie; Ruivard, Marc; Toutain, Fabienne; Lahary, Agnès; Garçon, Loïc

Relevance of platelet desialylation and thrombocytopenia in type 2B von Willebrand disease: preclinical and clinical evidence

血小板去唾液酸化和血小板减少症在 2B 型血管性血友病中的相关性:临床前和临床证据

Dupont, Annabelle; Soukaseum, Christelle; Cheptou, Mathilde; Adam, Frédéric; Nipoti, Thomas; Lourenco-Rodrigues, Marc-Damien; Legendre, Paulette; Proulle, Valérie; Rauch, Antoine; Kawecki, Charlotte; Bryckaert, Marijke; Rosa, Jean-Philippe; Paris, Camille; Ternisien, Catherine; Boisseau, Pierre; Goudemand, Jenny; Borgel, Delphine; Lasne, Dominique; Maurice, Pascal; Lenting, Peter J; Denis, Cécile V; Susen, Sophie; Kauskot, Alexandre