日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Distinct neuronal alterations distinguish two subtypes of sporadic Creutzfeldt-Jakob disease with shared dysfunctional pathways.

散发性克雅氏病的两个亚型具有不同的神经元改变,但它们都存在共同的功能障碍通路。

Williams Katie, Groveman Bradley R, Foliaki Simote T, Race Brent, Hay Arielle, Walters Ryan O, Thomas Tina, Zanusso Gianluigi, Carroll James A, Haigh Cathryn L

Prion-induced ferroptosis is facilitated by RAC3.

RAC3 促进朊病毒诱导的铁死亡

Peng Hao, Pfeiffer Susanne, Varynskyi Borys, Qiu Marina, Srinark Chanikarn, Jin Xiang, Zhang Xin, Williams Katie, Groveman Bradley R, Foliaki Simote T, Race Brent, Thomas Tina, Chen Chengxuan, Müller Constanze, Kovács Krisztina, Arzberger Thomas, Momma Stefan, Haigh Cathryn L, Schick Joel A

Evidence against efficient spontaneous disassembly of prions into small oligomers.

有证据表明朊病毒无法有效地自发解离成小寡聚体

Shoup Daniel, Hughson Andrew G, Race Brent, Alam Parvez, Dulebohn Daniel, Priola Suzette A, Caughey Byron

Cryo-EM structure of a natural prion: chronic wasting disease fibrils from deer

天然朊病毒的冷冻电镜结构:鹿源慢性消耗性疾病原纤维

Alam, Parvez; Hoyt, Forrest; Artikis, Efrosini; Soukup, Jakub; Hughson, Andrew G; Schwartz, Cindi L; Barbian, Kent; Miller, Michael W; Race, Brent; Caughey, Byron

Sensitive detection of pathological seeds of α-synuclein, tau and prion protein on solid surfaces

对固体表面上α-突触核蛋白、tau蛋白和朊病毒蛋白的病理种子进行灵敏检测

Orrú, Christina D; Groveman, Bradley R; Hughson, Andrew G; Barrio, Tomás; Isiofia, Kachi; Race, Brent; Ferreira, Natalia C; Gambetti, Pierluigi; Schneider, David A; Masujin, Kentaro; Miyazawa, Kohtaro; Ghetti, Bernardino; Zanusso, Gianluigi; Caughey, Byron

The PINK1/Parkin pathway of mitophagy exerts a protective effect during prion disease

PINK1/Parkin通路介导的线粒体自噬在朊病毒病中发挥保护作用。

Ward, Anne; Jessop, Forrest; Faris, Robert; Hollister, Jason; Shoup, Daniel; Race, Brent; Bosio, Catharine M; Priola, Suzette A

Sodium hypochlorite inactivation of human CJD prions

次氯酸钠对人类克雅氏病朊病毒的灭活作用

Groveman, Bradley R; Race, Brent; Hughson, Andrew G; Haigh, Cathryn L

Sporadic Creutzfeldt-Jakob disease infected human cerebral organoids retain the original human brain subtype features following transmission to humanized transgenic mice

散发型克雅氏病感染的人类脑类器官在传播至人源化转基因小鼠后,仍保留了原始人类脑亚型的特征。

Groveman, Bradley R; Race, Brent; Foliaki, Simote T; Williams, Katie; Hughson, Andrew G; Baune, Chase; Zanusso, Gianluigi; Haigh, Cathryn L

Efficacy of Wex-cide 128 disinfectant against multiple prion strains

Wex-cide 128 消毒剂对多种朊病毒株的功效

Baune, Chase; Groveman, Bradley R; Hughson, Andrew G; Thomas, Tina; Twardoski, Barry; Priola, Suzette; Chesebro, Bruce; Race, Brent

CD11c is not required by microglia to convey neuroprotection after prion infection

CD11c并非小胶质细胞在朊病毒感染后发挥神经保护作用所必需的。

Carroll, James A; Striebel, James F; Baune, Chase; Chesebro, Bruce; Race, Brent