日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Females experience a more severe disease course in Batten disease

女性患巴顿病时病情通常更为严重。

Cialone, Jennifer; Adams, Heather; Augustine, Erika F; Marshall, Frederick J; Kwon, Jennifer M; Newhouse, Nicole; Vierhile, Amy; Levy, Erika; Dure, Leon S; Rose, Katherine R; Ramirez-Montealegre, Denia; de Blieck, Elisabeth A; Mink, Jonathan W

Quantifying physical decline in juvenile neuronal ceroid lipofuscinosis (Batten disease)

量化青少年神经元蜡样脂褐质沉积症(巴顿病)的生理衰退

Kwon, J M; Adams, H; Rothberg, P G; Augustine, E F; Marshall, F J; Deblieck, E A; Vierhile, A; Beck, C A; Newhouse, N J; Cialone, J; Levy, E; Ramirez-Montealegre, D; Dure, L S; Rose, K R; Mink, J W

Immunosuppression alters disease severity in juvenile Batten disease mice

免疫抑制会改变幼年巴顿病小鼠的疾病严重程度。

Seehafer, Sabrina S; Ramirez-Montealegre, Denia; Wong, Andrew Ms; Chan, Chun-Hung; Castaneda, Julian; Horak, Michael; Ahmadi, Sarah M; Lim, Ming J; Cooper, Jonathan D; Pearce, David A

Alterations in striatal dopamine catabolism precede loss of substantia nigra neurons in a mouse model of juvenile neuronal ceroid lipofuscinosis

在幼年神经元蜡样脂褐质沉积症小鼠模型中,纹状体多巴胺代谢的改变先于黑质神经元的丢失。

Weimer, Jill M; Benedict, Jared W; Elshatory, Yasser M; Short, Douglas W; Ramirez-Montealegre, Denia; Ryan, Deborah A; Alexander, Noreen A; Federoff, Howard J; Cooper, Jonathan D; Pearce, David A