Bone marrow failure in Fanconi anemia is triggered by an exacerbated p53/p21 DNA damage response that impairs hematopoietic stem and progenitor cells
范康尼贫血症中的骨髓衰竭是由加剧的 p53/p21 DNA 损伤反应引发的,这种反应会损害造血干细胞和祖细胞
期刊:Cell Stem Cell
影响因子:19.8
doi:10.1016/j.stem.2012.05.013
Raphael Ceccaldi, Kalindi Parmar, Enguerran Mouly, Marc Delord, Jung Min Kim, Marie Regairaz, Marika Pla, Nadia Vasquez, Qing-Shuo Zhang, Corinne Pondarre, Régis Peffault de Latour, Eliane Gluckman, Marina Cavazzana-Calvo, Thierry Leblanc, Jérôme Larghero, Markus Grompe, Gérard Socié, Alan D D'Andre