日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

The interleukin-33 receptor (ST2) is a novel therapeutic target to attenuate the progression of hemophilic arthropathy

白细胞介素-33受体(ST2)是减缓血友病性关节病进展的新型治疗靶点。

Hawerkamp, Heike C; Yeow, Aoife; Byrne, Ciara M; Chevalier, Anne; Matarazzo, Laura; Lawrence, Alexander; Ivers, Daniel; Murangi, Tatenda; O'Dowd, Niamh; Hulshof, Anne-Marije; Atiq, Ferdows; O'Sullivan, Jamie M; Kelly, Vincent P; Finlay, Conor M; McSorley, Henry J; Gangadharan, Bagirath; Reipert, Birgit M; O'Donnell, James S; Turecek, Peter L; Fallon, Padraic G

A giant virus infecting the amoeboflagellate Naegleria

感染变形虫纳格里虫的巨型病毒

Patrick Arthofer, Florian Panhölzl, Vincent Delafont, Alban Hay, Siegfried Reipert, Norbert Cyran, Stefanie Wienkoop, Anouk Willemsen, Ines Sifaoui, Iñigo Arberas-Jiménez, Frederik Schulz, Jacob Lorenzo-Morales, Matthias Horn

Immunogenicity profile of rurioctocog alfa pegol in previously treated patients with severe congenital hemophilia A

rurioctocog alfa pegol 在既往接受过治疗的重型先天性血友病 A 患者中的免疫原性特征

Horling, Frank M; Reipert, Birgit M; Allacher, Peter; Engl, Werner; Pan, Luying; Tangada, Srilatha

Targets of autoantibodies in acquired hemophilia A are not restricted to factor VIII: data from the GTH-AH 01/2010 study

获得性血友病A中自身抗体的靶点并不局限于因子VIII:来自GTH-AH 01/2010研究的数据

Oleshko, Olga; Werwitzke, Sonja; Klingberg, Annika; Witte, Torsten; Eichler, Hermann; Klamroth, Robert; Holstein, Katharina; Hart, Christina; Pfrepper, Christian; Knöbl, Paul; Greil, Richard; Neumeister, Peter; Reipert, Birgit M; Tiede, Andreas

Prospective Hemophilia Inhibitor PUP Study reveals distinct antibody signatures during FVIII inhibitor eradication

前瞻性血友病抑制剂 PUP 研究揭示了 FVIII 抑制剂清除过程中独特的抗体特征

Paul, Helmut; Berg, Verena; Gangadharan, Bagirath; Bowen, Joel; LeBeau, Petra; Blatný, Jan; Male, Christoph; Radulescu, Vlad C; Diaz, Rosa; Mancuso, Maria Elisa; Brown, Deborah L; Reipert, Birgit M

Freeze Substitution Accelerated via Agitation: New Prospects for Ultrastructural Studies of Lichen Symbionts and Their Extracellular Matrix

搅拌加速冷冻替代:地衣共生体及其细胞外基质超微结构研究的新前景

Reipert, Siegfried; Gruber, Daniela; Cyran, Norbert; Schmidt, Brigitte; de la Torre Noetzel, Rosa; Sancho, Leopoldo G; Goga, Michal; Bačkor, Martin; Schmidt, Katy

Extracellular Vesicles and Particles Modulate Proton Secretion in a Model of Human Parietal Cells

细胞外囊泡和颗粒调节人类壁细胞模型中的质子分泌

Agnes Mistlberger-Reiner, Sonja Sterneder, Siegfried Reipert, Sara Wolske, Veronika Somoza

Qualification of Hemophilia Treatment Centers to Enable Multi-Center Studies of Gene Expression Signatures in Blood Cells from Pediatric Patients

血友病治疗中心的资质认证,使儿科患者血细胞基因表达特征的多中心研究成为可能

Birgit M Reipert, Christoph J Hofbauer, Bagirath Gangadharan, Verena Berg, Elizabeth Donnachie, Shannon Meeks, Maria Elisa Mancuso, Joel Bowen, Deborah L Brown

Immune tolerance against infused FVIII in hemophilia A is mediated by PD-L1+ Tregs

血友病 A 对输注 FVIII 的免疫耐受由 PD-L1+ Tregs 介导

Janine Becker-Gotot, Mirjam Meissner, Vadim Kotov, Blanca Jurado-Mestre, Andrea Maione, Andreas Pannek, Thilo Albert, Chrystel Flores, Frank A Schildberg, Paul A Gleeson, Birgit M Reipert, Johannes Oldenburg, Christian Kurts

Bi-allelic LETM1 variants perturb mitochondrial ion homeostasis leading to a clinical spectrum with predominant nervous system involvement

LETM1双等位基因变异会扰乱线粒体离子稳态,导致一系列临床表现,其中以神经系统受累为主。

Kaiyrzhanov, Rauan; Mohammed, Sami E M; Maroofian, Reza; Husain, Ralf A; Catania, Alessia; Torraco, Alessandra; Alahmad, Ahmad; Dutra-Clarke, Marina; Grønborg, Sabine; Sudarsanam, Annapurna; Vogt, Julie; Arrigoni, Filippo; Baptista, Julia; Haider, Shahzad; Feichtinger, René G; Bernardi, Paolo; Zulian, Alessandra; Gusic, Mirjana; Efthymiou, Stephanie; Bai, Renkui; Bibi, Farah; Horga, Alejandro; Martinez-Agosto, Julian A; Lam, Amanda; Manole, Andreea; Rodriguez, Diego-Perez; Durigon, Romina; Pyle, Angela; Albash, Buthaina; Dionisi-Vici, Carlo; Murphy, David; Martinelli, Diego; Bugiardini, Enrico; Allis, Katrina; Lamperti, Costanza; Reipert, Siegfried; Risom, Lotte; Laugwitz, Lucia; Di Nottia, Michela; McFarland, Robert; Vilarinho, Laura; Hanna, Michael; Prokisch, Holger; Mayr, Johannes A; Bertini, Enrico Silvio; Ghezzi, Daniele; Østergaard, Elsebet; Wortmann, Saskia B; Carrozzo, Rosalba; Haack, Tobias B; Taylor, Robert W; Spinazzola, Antonella; Nowikovsky, Karin; Houlden, Henry