日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Molecular Investigation in Early-Onset Interstitial Lung Disease: Results From 699 Unrelated Patients

早期间质性肺疾病的分子检测:来自 699 例无关患者的结果

Louvrier, Camille; Nathan, Nadia; Cottin, Vincent; Desroziers, Tifenn; Nau, Valérie; Soreze, Yohan; Dastot-Le Moal, Florence; Reix, Philippe; Bouvry, Diane; Thumerelle, Caroline; Reynaud-Gaubert, Martine; Hadchouel, Alice; Prévot, Grégoire; Manali, Effrosyni; Kannengiesser, Caroline; Ba, Ibrahima; Amselem, Serge; Houdouin, Véronique; Borie, Raphaël; Legendre, Marie

Beyond the Lung. Impact of Elexacaftor/Tezacaftor/Ivacaftor on Sinonasal Disease in Children With Cystic Fibrosis

肺部以外的影响:Elexacaftor/Tezacaftor/Ivacaftor 对囊性纤维化患儿鼻窦疾病的影响

Petitjean, Margaux; Letierce, Alexia; Bonnel, Anne-Sophie; Reix, Philippe; Deneuville, Eric; Stremler, Nathalie; Luscan, Romain; Couloigner, Vincent; Mely, Laurent; Bessaci, Katia; Labbe, Guillaume; Marguet, Christophe; Kelly-Aubert, Mairead; Hassani, Fatiha; Sermet-Gaudelus, Isabelle; Simon, François

Beyond Trikafta: new models to assess tissue dependent rescue of N1303K-CFTR

Trikafta 之外:评估 N1303K-CFTR 组织依赖性拯救的新模型

Pranke, Iwona; Capurro, Valeria; Chevalier, Benoit; Pesce, Emanuela; Tomati, Valeria; Pastorino, Cristina; Kelly-Aubert, Mairead; Hatton, Aurelie; Dreano, Elise; Lena, Mariateresa; Bocciardi, Renata; Zara, Federico; Pantano, Stefano; Terlizzi, Vito; Lucanto, Cristina; Costa, Stefano; Claut, Laura; Daccò, Valeria; Poli, Piercarlo; Maschio, Massimo; Fabrizzi, Benedetta; Caporelli, Nicole; Cipolli, Marco; Volpi, Sonia; Chedevergne, Frederique; Cosson, Laure; Macey, Julie; Ramel, Sophie; Weiss, Laurence; Grenet, Dominique; Le Clainche-Viala, Laurence; Douvry, Benoit; Ravoninjatovo, Bruno; Audousset, Camille; Tatopoulos, Aurélie; Richaud-Thiriez, Bénédicte; Baravalle, Melissa; Thouvenin, Guillaume; Labbé, Guillaume; Mittaine, Marie; Reix, Philippe; Durieu, Isabelle; Mankikian, Julie; Bui, Stéphanie; Nguyen-Khoa, Thao; Khoukh, Karim; Martin, Clémence; Da Silva, Jennifer; De Carli, Paola; Castellani, Carlo; Cresta, Federico; Galietta, Luis; Guillemaut, Anne; Girodon, Emmanuelle; Remus, Natacha; Bulcaen, Mathis; Ensinck, Marjolein; Zajac, Miroslaw; Carlon, Marianne; LeBihan, Jean; Burgel, Pierre-Régis; Sermet-Gaudelus, Isabelle; Hinzpeter, Alexandre; Pedemonte, Nicoletta

Persistent tachypnoea of infancy and neuroendocrine cell hyperplasia of infancy: from systematic review to future directions

婴儿持续性呼吸急促和婴儿神经内分泌细胞增生:从系统综述到未来方向

Nathan, Nadia; Grochowska, Magdalena; Krenke, Katarzyna; Epaud, Ralph; Reix, Philippe; Griese, Matthias; Louvrier, Camille; Soreze, Yohan; Mulard, Cécile; Donnet, Barbara; Ducou le Pointe, Hubert; Dufour-Barba, Clémence; Coulomb l'Herminé, Aurore; Dubus, Jean-Christophe; Marczak, Honorata

International consensus statement on routine blood testing in primary ciliary dyskinesia

关于原发性纤毛运动障碍常规血液检测的国际共识声明

Altaraihi, Sarah; Marthin, June K; Anagnostopoulou, Pinelopi; Boon, Mieke; Carr, Siobhan B; Castillo-Corullón, Silvia; Dehlink, Eleonora; Destouches, Damien M S; Duckers, Jamie; Haarman, Eric G; Karadag, Bülent; Kavouridou, Christina; Loebinger, Michael R; Maitre, Bernard; Mazurek, Henryk; Morgan, Lucy; Omran, Heymut; Ozcelik, Ugur; Peckam, Daniel; Pifferi, Massimo; Pohunek, Petr; Qvist, Tavs; Raidt, Johanna; Reix, Phillipe; Ringshausen, Felix C; Robinson, Phil; Robson, Evie; Röhmel, Jobst; Santamaria, Francesca; Schlegtendal, Anne; Ullmann, Nicola; Walker, Woolf; Yiallouros, Panayiotis; Thouvenin, Guillaume; Crowley, Suzanne; Nielsen, Kim G

Elexacaftor/Tezacaftor/Ivacaftor Population Pharmacokinetics in Pediatric Patients With Cystic Fibrosis

艾来卡托/替扎卡托/伊伐卡托在囊性纤维化患儿中的群体药代动力学

Truong, Ngoc Hoa; Benaboud, Sihem; Bouazza, Naïm; Barboura, Mahassen; Bardin, Emmanuelle; Miralles, Michel; Lui, Gabrielle; Froelicher-Bournaud, Léo; Rouillon, Steeve; Bihouee, Tiphaine; Bui, Stéphanie; Reix, Philippe; Dalphin, Marie-Laure; Laurans, Muriel; Languepin, Jeanne; Corvol, Harriet; Troussier, Françoise; Weiss, Laurence; Cinthia, Rames; Tatopoulos, Aurélie; Deneuville, Eric; Chiron, Raphael; Stremler, Nathalie; Llerena, Cathy; Ramel, Sophie; Perisson, Caroline; Houdoin, Véronique; Mittaine, Marie; Treluyer, Jean-Marc; Sermet-Gaudelus, Isabelle; Foissac, Frantz

Newborn Screening for Cystic Fibrosis Is Associated With the Lowest Healthcare Costs: A 10-Year Observational Follow-Up Study in France

法国一项为期10年的观察性随访研究表明,新生儿囊性纤维化筛查与最低的医疗保健成本相关。

Guyot, Erika; Deygas, Floriane; Belhassen, Manon; Berard, Marjorie; Van Ganse, Eric; Sermet-Gaudelus, Isabelle; Tiaiba, Sabrine; Dubus, Jean-Christophe; Durieu, Isabelle; Reix, Philippe

Efficacy and tolerance of intravenous methylprednisolone pulses in children with severe bronchopulmonary dysplasia requiring respiratory support

静脉注射甲泼尼龙冲击疗法治疗需要呼吸支持的重度支气管肺发育不良患儿的疗效和耐受性

Reynaud, Josseline; Dreyfus, Lélia; Coutier, Laurianne; Butin, Marine; Godbert, Isabelle; Baudin, Florent; Horvat, Côme; Reix, Philippe

Factors of late respiratory support or oxygen weaning in infants with bronchopulmonary dysplasia

支气管肺发育不良患儿后期呼吸支持或氧气撤离的因素

Garcia-Anton, Alma; Dreyfus, Lélia; Portefaix, Aurélie; Baudin, Florent; Plaisant, Franck; Loppinet, Thomas; Reix, Philippe; Butin, Marine; Coutier, Laurianne

Effects of Elexacaftor-Tezacaftor-Ivacaftor on Nasal and Sinus Symptoms in Children With Cystic Fibrosis

Elexacaftor-Tezacaftor-Ivacaftor 对囊性纤维化患儿鼻部和鼻窦症状的影响

Petit, Guillaume; Coudert, Aurélie; Hermann, Ruben; Truy, Eric; Bonjour, Maxime; Reix, Philippe; Ayari, Sonia