日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Granulocyte-Macrophage Colony Stimulating Factor Receptor Contributes to Plexiform Neurofibroma Initiation.

粒细胞-巨噬细胞集落刺激因子受体促进丛状神经纤维瘤的发生

Pundavela Jay, Hall Ashley, Dinglasan Samantha Anne, Choi Kwangmin, Rizvi Tilat A, Trapnell Bruce C, Wu Jianqiang, Ratner Nancy

Genetic activation of ERK2 recapitulates core neurodevelopmental features of Rasopathy syndromes in mice

ERK2基因激活可在小鼠中重现Rasopathy综合征的核心神经发育特征。

Grover, Kassidy E; Cappel, Zoe R; Volz, Avery; Cotella, Evelin M; Smallwood, Kelly; Berryhill, Christine A; Raje, Kimaya R; Fisher, Austen A; Casper, Mary Claire T; Nardini, Diana; Rizvi, Tilat A; Salazar, Rosa M; Wooten, Ashley; Williams, Michael T; Vorhees, Charles V; Romick, Lindsey E; Greis, Kenneth D; Hu, Yueh-Chiang; Miles, Linde A; Angus, Steven P; Ratner, Nancy; Prada, Carlos E; Weaver, K Nicole; Waclaw, Ronald R; Robinson, J Elliott

Angiotensin receptor signaling in sickle cell anemia has a reno-protective effect on urine concentrating ability but results in sickle glomerulopathy

镰状细胞贫血中的血管紧张素受体信号传导对尿液浓缩能力具有肾脏保护作用,但会导致镰状细胞肾小球病。

Roy, Swarnava; Rai, Parul; Eiymo Mwa Mpollo, Marthe-Sandrine; Chang, Kyung-Hee; Rizvi, Tilat; Shanmukhappa, Shiva Kumar; VandenHeuvel, Katherine; Aronow, Bruce; Inagami, Tadashi; Cancelas, Jose A; Malik, Punam

Oligodendrocyte Nf1 Controls Aberrant Notch Activation and Regulates Myelin Structure and Behavior

少突胶质细胞 Nf1 控制异常的 Notch 激活并调节髓鞘结构和行为

López-Juárez, Alejandro; Titus, Haley E; Silbak, Sadiq H; Pressler, Joshua W; Rizvi, Tilat A; Bogard, Madeleine; Bennett, Michael R; Ciraolo, Georgianne; Williams, Michael T; Vorhees, Charles V; Ratner, Nancy

Placenta growth factor augments airway hyperresponsiveness via leukotrienes and IL-13

胎盘生长因子通过白三烯和IL-13增强气道高反应性

Eiymo Mwa Mpollo, Marthe-Sandrine; Brandt, Eric B; Shanmukhappa, Shiva Kumar; Arumugam, Paritha I; Tiwari, Swati; Loberg, Anastacia; Pillis, Devin; Rizvi, Tilat; Lindsey, Mark; Jonck, Bart; Carmeliet, Peter; Kalra, Vijay K; Le Cras, Timothy D; Ratner, Nancy; Wills-Karp, Marsha; Hershey, Gurjit K Khurana; Malik, Punam

Genetic diminution of circulating prothrombin ameliorates multiorgan pathologies in sickle cell disease mice.

基因手段降低循环凝血酶原水平可改善镰状细胞病小鼠的多器官病变

Arumugam Paritha I, Mullins Eric S, Shanmukhappa Shiva Kumar, Monia Brett P, Loberg Anastacia, Shaw Maureen A, Rizvi Tilat, Wansapura Janaka, Degen Jay L, Malik Punam

Preclinical assessments of the MEK inhibitor PD-0325901 in a mouse model of Neurofibromatosis type 1

在1型神经纤维瘤病小鼠模型中对MEK抑制剂PD-0325901进行临床前评估

Jousma, Edwin; Rizvi, Tilat A; Wu, Jianqiang; Janhofer, David; Dombi, Eva; Dunn, Richard S; Kim, Mi-Ok; Masters, Andrea R; Jones, David R; Cripe, Timothy P; Ratner, Nancy

Neurofibroma-associated macrophages play roles in tumor growth and response to pharmacological inhibition

神经纤维瘤相关巨噬细胞在肿瘤生长和对药物抑制的反应中发挥作用

Prada, Carlos E; Jousma, Edwin; Rizvi, Tilat A; Wu, Jianqiang; Dunn, R Scott; Mayes, Debra A; Cancelas, Jose A; Dombi, Eva; Kim, Mi-Ok; West, Brian L; Bollag, Gideon; Ratner, Nancy

Ectopic myelinating oligodendrocytes in the dorsal spinal cord as a consequence of altered semaphorin 6D signaling inhibit synapse formation

由于信号通路改变,背侧脊髓中异位髓鞘形成少突胶质细胞会抑制突触形成。

Leslie, Jennifer R; Imai, Fumiyasu; Fukuhara, Kaori; Takegahara, Noriko; Rizvi, Tilat A; Friedel, Roland H; Wang, Fan; Kumanogoh, Atsushi; Yoshida, Yutaka

Plexiform and dermal neurofibromas and pigmentation are caused by Nf1 loss in desert hedgehog-expressing cells

丛状神经纤维瘤、真皮神经纤维瘤和色素沉着是由表达沙漠刺猬蛋白的细胞中Nf1缺失引起的。

Wu, Jianqiang; Williams, Jon P; Rizvi, Tilat A; Kordich, Jennifer J; Witte, David; Meijer, Dies; Stemmer-Rachamimov, Anat O; Cancelas, Jose A; Ratner, Nancy