日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

TGFβ links EBV to multisystem inflammatory syndrome in children.

TGFβ 将 EBV 与儿童多系统炎症综合征联系起来

Goetzke Carl Christoph, Massoud Mona, Frischbutter Stefan, Guerra Gabriela Maria, Ferreira-Gomes Marta, Heinrich Frederik, von Stuckrad Anne Sae Lim, Wisniewski Sebastian, Licha Jan Robin, Bondareva Marina, Ehlers Lisa, Khaldi-Plassart Samira, Javouhey Etienne, Pons Sylvie, Trouillet-Assant Sophie, Ozsurekci Yasemin, Zhang Yu, Poli Maria Cecilia, Discepolo Valentina, Lo Vecchio Andrea, Sahin Bengü, Verboom Murielle, Hallensleben Michael, Heuhsen Anja Isabelle, Astudillo Camila, Espinosa Yazmin, Vial Cox Maria Cecilia, Dobbs Kerry, Delmonte Ottavia M, Montealegre Sanchez Gina A, Magliocco Mary, Barron Karyl, Danielson Jeffrey, Petrov Lev, Unterwalder Nadine, Sawitzki Birgit, Matz Mareen, Lehmann Katrin, Gratopp Alexander, von Bernuth Horst, Burkhardt Lisa-Marie, Wiese Niklas, Peter Lena, Schmueck-Henneresse Michael, Amini Leila, Maurer Marcus, Roehmel Jobst Fridolin, Gewurz Benjamin E, Yonker Lael M, Witkowski Mario, Kruglov Andrey, Mall Marcus Alexander, Su Helen C, Ozen Seza, Radbruch Andreas, Belot Alexandre, Durek Pawel, Kallinich Tilmann, Mashreghi Mir-Farzin

Reduction of systemic inflammation by elexacaftor/tezacaftor/ivacaftor correlates with lung function improvement in cystic fibrosis

elexacaftor/tezacaftor/ivacaftor 降低全身炎症与囊性纤维化患者肺功能改善相关

Halle, Olga; Graeber, Simon Y; Kontsendorn, Julia; Kessemeier, Claudia; Falke, Jan-Niklas; Schwabe, Jannik; Schütz, Katharina; Pallenberg, Sophia T; Dalferth, Rebecca; Grychtol, Ruth; Ringshausen, Felix C; Stahl, Mirjam; Thee, Stephanie; Roehmel, Jobst F; Syunyaeva, Zulfiya; Duerr, Julia; Chung, Jaehi; Hirtz, Stephanie; Uselmann, Tatjana; Kühbandner, Iris; Rückes-Nilges, Claudia; Bagheri-Pothoff, Azadeh; Barth, Sandra; Schaub, Bianca; Brinkmann, Folke; Weber, Stefanie; van Koningsbruggen-Rietschel, Silke; Abdo, Mustafa; Weckmann, Markus; Widder, Stefanie; Hansen, Gesine; Tümmler, Burkhard; Sommerburg, Olaf; Naehrlich, Lutz; Mall, Marcus A; Dittrich, Anna-Maria

Multiple-breath washout is more sensitive than spirometry to detect lung function impairment in children and adults with bronchiectasis

与肺量计相比,多次呼吸冲洗法对检测支气管扩张患儿和成人的肺功能损害更为敏感。

Ziegahn, Niklas; Roehmel, Jobst F; Pioch, Charlotte O; Busack, Leonie M; Allomba, Christine; Fuhlrott, Bent R; Meinus, Carolin; Schnabel, Olaf; Yoosefi Moridani, Mehrak; Thee, Stephanie; Lau, Susanne; Mall, Marcus A; Stahl, Mirjam

The established chest MRI score for cystic fibrosis can be applied to contrast agent-free matrix pencil decomposition functional MRI: a multireader analysis

已建立的囊性纤维化胸部MRI评分可应用于无对比剂矩阵铅笔分解功能磁共振成像:一项多阅片者分析

Steinke, Eva; Bauman, Grzegorz; Steffen, Ingo G; Schobert, Isabel T; Thee, Stephanie; Syunyaeva, Zulfiya; Roehmel, Jobst; Posch, Helena; Fahlenkamp, Ute L; Scale, Carolin; Veldhoen, Simon; Bieri, Oliver; Wielpütz, Mark O; Mall, Marcus A; Stahl, Mirjam; Doellinger, Felix

Analyses of 1236 genotyped primary ciliary dyskinesia individuals identify regional clusters of distinct DNA variants and significant genotype-phenotype correlations

对 1236 名已进行基因分型的原发性纤毛运动障碍患者的分析,发现了不同 DNA 变异的区域性聚集以及显著的基因型-表型相关性。

Raidt, Johanna; Riepenhausen, Sarah; Pennekamp, Petra; Olbrich, Heike; Amirav, Israel; Athanazio, Rodrigo A; Aviram, Micha; Balinotti, Juan E; Bar-On, Ophir; Bode, Sebastian F N; Boon, Mieke; Borrelli, Melissa; Carr, Siobhan B; Crowley, Suzanne; Dehlink, Eleonora; Diepenhorst, Sandra; Durdik, Peter; Dworniczak, Bernd; Emiralioğlu, Nagehan; Erdem, Ela; Fonnesu, Rossella; Gracci, Serena; Große-Onnebrink, Jörg; Gwozdziewicz, Karolina; Haarman, Eric G; Hansen, Christine R; Hogg, Claire; Holgersen, Mathias G; Kerem, Eitan; Körner, Robert W; Kötz, Karsten; Kouis, Panayiotis; Loebinger, Michael R; Lorent, Natalie; Lucas, Jane S; Maj, Debora; Mall, Marcus A; Marthin, June K; Martinu, Vendula; Mazurek, Henryk; Mitchison, Hannah M; Nöthe-Menchen, Tabea; Özçelik, Ugur; Pifferi, Massimo; Pogorzelski, Andrzej; Ringshausen, Felix C; Roehmel, Jobst F; Rovira-Amigo, Sandra; Rumman, Nisreen; Schlegtendal, Anne; Shoemark, Amelia; Sperstad Kennelly, Synne; Staar, Ben O; Sutharsan, Sivagurunathan; Thomas, Simon; Ullmann, Nicola; Varghese, Julian; von Hardenberg, Sandra; Walker, Woolf T; Wetzke, Martin; Witt, Michal; Yiallouros, Panayiotis; Zschocke, Anna; Ziętkiewicz, Ewa; Nielsen, Kim G; Omran, Heymut

Association between upper and lower respiratory disease among patients with primary ciliary dyskinesia: an international study

原发性纤毛运动障碍患者上呼吸道和下呼吸道疾病的关联性:一项国际研究

Lam, Yin Ting; Papon, Jean-François; Alexandru, Mihaela; Anagiotos, Andreas; Armengot, Miguel; Boon, Mieke; Burgess, Andrea; Calmes, Doriane; Crowley, Suzanne; Dheyauldeen, Sinan Ahmed D; Emiralioglu, Nagehan; Erdem Eralp, Ela; van Gogh, Christine; Gokdemir, Yasemin; Haarman, Eric G; Harris, Amanda; Hayn, Isolde; Ismail-Koch, Hasnaa; Karadag, Bülent; Kempeneers, Céline; Kieninger, Elisabeth; Kim, Sookyung; Lorent, Natalie; Ozcelik, Ugur; Pioch, Charlotte; Raidt, Johanna; Reula, Ana; Roehmel, Jobst; Sperstad Kennelly, Synne; Yiallouros, Panayiotis; Goutaki, Myrofora

Contrast agent-free functional magnetic resonance imaging with matrix pencil decomposition to quantify abnormalities in lung perfusion and ventilation in patients with cystic fibrosis

采用无对比剂功能磁共振成像结合矩阵铅笔分解技术量化囊性纤维化患者肺灌注和通气异常

Doellinger, Felix; Bauman, Grzegorz; Roehmel, Jobst; Stahl, Mirjam; Posch, Helena; Steffen, Ingo G; Pusterla, Orso; Bieri, Oliver; Wielpütz, Mark O; Mall, Marcus A

Antigen specificity and cross-reactivity drive functionally diverse anti-Aspergillus fumigatus T cell responses in cystic fibrosis

抗原特异性和交叉反应性驱动囊性纤维化中功能多样的抗烟曲霉 T 细胞反应

Carsten Schwarz, Patience Eschenhagen, Henrijette Schmidt, Thordis Hohnstein, Christina Iwert, Claudia Grehn, Jobst Roehmel, Eva Steinke, Mirjam Stahl, Laura Lozza, Ekaterina Tikhonova, Elisa Rosati, Ulrik Stervbo, Nina Babel, Jochen G Mainz, Hilmar Wisplinghoff, Frank Ebel, Lei-Jie Jia, Matthew G B

Characteristics of Otologic Disease Among Patients With Primary Ciliary Dyskinesia

原发性纤毛运动障碍患者的耳科疾病特征

Goutaki, Myrofora; Lam, Yin Ting; Alexandru, Mihaela; Anagiotos, Andreas; Armengot, Miguel; Boon, Mieke; Burgess, Andrea; Caversaccio, Nathalie; Crowley, Suzanne; Dheyauldeen, Sinan Ahmed D; Emiralioglu, Nagehan; Erdem, Ela; van Gogh, Christine; Gunaydin, Onder; Haarman, Eric G; Harris, Amanda; Hayn, Isolde; Ismail-Koch, Hasnaa; Karadag, Bulent; Kempeneers, Céline; Kim, Sookyung; Lorent, Natalie; Ozcelik, Ugur; Pioch, Charlotte; Poirrier, Anne-Lise M L; Reula, Ana; Roehmel, Jobst; Yiallouros, Panayiotis; Yumusakhuylu, Ali Cemal; Papon, Jean-François

Effects of Lumacaftor/Ivacaftor on Cystic Fibrosis Disease Progression in Children 2 through 5 Years of Age Homozygous for F508del-CFTR: A Phase 2 Placebo-controlled Clinical Trial

Lumacaftor/Ivacaftor 对 2 至 5 岁 F508del-CFTR 纯合子儿童囊性纤维化疾病进展的影响:一项 II 期安慰剂对照临床试验

Stahl, Mirjam; Roehmel, Jobst; Eichinger, Monika; Doellinger, Felix; Naehrlich, Lutz; Kopp, Matthias V; Dittrich, Anna-Maria; Lee, Christopher; Sommerburg, Olaf; Tian, Simon; Xu, Tu; Wu, Pan; Joshi, Aniket; Ray, Partha; Duncan, Margaret E; Wielpütz, Mark O; Mall, Marcus A