日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

STAT3-Dependent Regulation of CFTR and Ciliogenesis Is Essential for Mucociliary Clearance and Innate Airway Defense in Hyper-IgE Syndrome

STAT3依赖的CFTR和纤毛发生调控对于高IgE综合征中的黏液纤毛清除和先天性气道防御至关重要

Sun, Ling; Walls, Samantha A; Dang, Hong; Quinney, Nancy L; Sears, Patrick R; Sadritabrizi, Taraneh; Hasegawa, Koichi; Okuda, Kenichi; Asakura, Takanori; Chang, Xiuya; Zheng, Meiqi; Mikami, Yu; Dizmond, Felicia U; Danilova, Daniela; Zhou, Lynn; Deshmukh, Anshulika; Cholon, Deborah M; Radicioni, Giorgia; Rogers, Troy D; Kissner, William J; Markovetz, Matthew R; Guhr Lee, Tara N; Gutay, Mark I; Esther, Charles R Jr; Chua, Michael; Grubb, Barbara R; Ehre, Camille; Kesimer, Mehmet; Hill, David B; Ostrowski, Lawrence E; Button, Brian; Gentzsch, Martina; Robinson, Chevalia; Olivier, Kenneth N; Freeman, Alexandra F; Randell, Scott H; Vladar, Eszter; O'Neal, Wanda K; Boucher, Richard C; Chen, Gang

Prolonged airway explant culture enables study of health, disease, and viral pathogenesis.

长期气道外植体培养能够研究健康、疾病和病毒发病机制

Lee-Ferris Rhianna E, Okuda Kenichi, Galiger Jacob R, Schworer Stephen A, Rogers Troy D, Dang Hong, Gilmore Rodney, Edwards Caitlin, Crisp Gillian, Nakano Satoko, Cawley Anne M, Pickles Raymond J, Gallant Samuel C, Crisci Elisa, Rivier Lauraine, Hagood James S, O'Neal Wanda K, Baric Ralph S, Grubb Barbara R, Boucher Richard C, Randell Scott H

Dysregulated Airway Host Defense in Hyper IgE Syndrome due to STAT3 Mutations

STAT3 突变导致高 IgE 综合征中气道宿主防御功能失调

Sun, Ling; Walls, Samantha A; Dang, Hong; Quinney, Nancy L; Sears, Patrick R; Sadritabrizi, Taraneh; Hasegawa, Koichi; Okuda, Kenichi; Asakura, Takanori; Chang, Xiuya; Zheng, Meiqi; Mikami, Yu; Dizmond, Felicia U; Danilova, Daniela; Zhou, Lynn; Deshmukh, Anshulika; Cholon, Deborah M; Radicioni, Giorgia; Rogers, Troy D; Kissner, William J; Markovetz, Matthew R; Guhr Lee, Tara N; Gutay, Mark I; Esther, Charles R; Chua, Michael; Grubb, Barbara R; Ehre, Camille; Kesimer, Mehmet; Hill, David B; Ostrowski, Lawrence E; Button, Brian; Gentzsch, Martina; Robinson, Chevalia; Olivier, Kenneth N; Freeman, Alexandra F; Randell, Scott H; O'Neal, Wanda K; Boucher, Richard C; Chen, Gang

Mucolytic treatment of chronic rhinosinusitis in a murine model of primary ciliary dyskinesia

在原发性纤毛运动障碍小鼠模型中,黏液溶解剂治疗慢性鼻窦炎

Yin, Weining; Golliher, Hannah L; Ferguson, Amy J; Kimbell, Julia S; Livraghi-Butrico, Alessandra; Rogers, Troy D; Grubb, Barbara R; Kimple, Adam J; Ostrowski, Lawrence E

BPIFB1 loss alters airway mucus properties and diminishes mucociliary clearance

BPIFB1 缺失会改变气道黏液的特性并降低黏液纤毛清除功能。

Donoghue, Lauren J; Markovetz, Matthew R; Morrison, Cameron B; Chen, Gang; McFadden, Kathryn M; Sadritabrizi, Taraneh; Gutay, Mark I; Kato, Takafumi; Rogers, Troy D; Snead, Jazmin Y; Livraghi-Butrico, Alessandra; Button, Brian; Ehre, Camille; Grubb, Barbara R; Hill, David B; Kelada, Samir N P

Regional Differences in Mucociliary Clearance in the Upper and Lower Airways

上下呼吸道黏液纤毛清除的区域差异

Rogers, Troy D; Button, Brian; Kelada, Samir N P; Ostrowski, Lawrence E; Livraghi-Butrico, Alessandra; Gutay, Mark I; Esther, Charles R Jr; Grubb, Barbara R

Mice with a Deletion of Rsph1 Exhibit a Low Level of Mucociliary Clearance and Develop a Primary Ciliary Dyskinesia Phenotype

Rsph1基因缺失的小鼠表现出黏液纤毛清除功能低下,并出现原发性纤毛运动障碍表型。

Yin, Weining; Livraghi-Butrico, Alessandra; Sears, Patrick R; Rogers, Troy D; Burns, Kimberlie A; Grubb, Barbara R; Ostrowski, Lawrence E

Loss of Cftr function exacerbates the phenotype of Na(+) hyperabsorption in murine airways

Cftr功能丧失会加剧小鼠气道中Na(+)过度吸收的表型

Livraghi-Butrico, Alessandra; Kelly, Elizabeth J; Wilkinson, Kristen J; Rogers, Troy D; Gilmore, Rodney C; Harkema, Jack R; Randell, Scott H; Boucher, Richard C; O'Neal, Wanda K; Grubb, Barbara R

Conditional deletion of dnaic1 in a murine model of primary ciliary dyskinesia causes chronic rhinosinusitis

在原发性纤毛运动障碍小鼠模型中条件性敲除dnaic1基因会导致慢性鼻窦炎

Ostrowski, Lawrence E; Yin, Weining; Rogers, Troy D; Busalacchi, Katie B; Chua, Michael; O'Neal, Wanda K; Grubb, Barbara R