日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

An early endothelial cell-specific requirement for Glut1 is revealed in Glut1 deficiency syndrome model mice

在 Glut1 缺乏综合征模型小鼠中揭示了内皮细胞对 Glut1 的早期特异性需求。

Tang, Maoxue; Park, Sarah H; Petri, Sabrina; Yu, Hang; Rueda, Carlos B; Abel, E Dale; Kim, Carla Y; Hillman, Elizabeth Mc; Li, Fanghua; Lee, Yeojin; Ding, Lei; Jagadish, Smitha; Frankel, Wayne N; De Vivo, Darryl C; Monani, Umrao R

Brain microvasculature defects and Glut1 deficiency syndrome averted by early repletion of the glucose transporter-1 protein.

早期补充葡萄糖转运蛋白-1 可预防脑微血管缺陷和 Glut1 缺乏症

Tang Maoxue, Gao Guangping, Rueda Carlos B, Yu Hang, Thibodeaux David N, Awano Tomoyuki, Engelstad Kristin M, Sanchez-Quintero Maria-Jose, Yang Hong, Li Fanghua, Li Huapeng, Su Qin, Shetler Kara E, Jones Lynne, Seo Ryan, McConathy Jonathan, Hillman Elizabeth M, Noebels Jeffrey L, De Vivo Darryl C, Monani Umrao R

Mitochondrial ATP-Mg/Pi carrier SCaMC-3/Slc25a23 counteracts PARP-1-dependent fall in mitochondrial ATP caused by excitotoxic insults in neurons

线粒体ATP-Mg/Pi载体SCaMC-3/Slc25a23可拮抗神经元兴奋性毒性损伤引起的PARP-1依赖性线粒体ATP下降。

Rueda, Carlos B; Traba, Javier; Amigo, Ignacio; Llorente-Folch, Irene; González-Sánchez, Paloma; Pardo, Beatriz; Esteban, José A; del Arco, Araceli; Satrústegui, Jorgina

Calcium-regulation of mitochondrial respiration maintains ATP homeostasis and requires ARALAR/AGC1-malate aspartate shuttle in intact cortical neurons

钙离子对线粒体呼吸的调节维持着ATP的稳态,而这需要完整皮层神经元中ARALAR/AGC1-苹果酸-天冬氨酸穿梭机制。

Llorente-Folch, Irene; Rueda, Carlos B; Amigo, Ignacio; del Arco, Araceli; Saheki, Takeyori; Pardo, Beatriz; Satrústegui, Jorgina

Glucagon regulation of oxidative phosphorylation requires an increase in matrix adenine nucleotide content through Ca2+ activation of the mitochondrial ATP-Mg/Pi carrier SCaMC-3

胰高血糖素对氧化磷酸化的调节需要通过Ca2+激活线粒体ATP-Mg/Pi载体SCaMC-3来增加线粒体基质腺嘌呤核苷酸含量。

Amigo, Ignacio; Traba, Javier; González-Barroso, M Mar; Rueda, Carlos B; Fernández, Margarita; Rial, Eduardo; Sánchez, Aránzazu; Satrústegui, Jorgina; Del Arco, Araceli