Fused in sarcoma (FUS) protein lacking nuclear localization signal (NLS) and major RNA binding motifs triggers proteinopathy and severe motor phenotype in transgenic mice.
融合肉瘤 (FUS) 蛋白缺乏核定位信号 (NLS) 和主要 RNA 结合基序,可引发转基因小鼠的蛋白质病变和严重的运动表型
期刊:Journal of Biological Chemistry
影响因子:3.9
doi:10.1074/jbc.M113.492017
Shelkovnikova Tatyana A, Peters Owen M, Deykin Alexey V, Connor-Robson Natalie, Robinson Hannah, Ustyugov Alexey A, Bachurin Sergey O, Ermolkevich Tatyana G, Goldman Igor L, Sadchikova Elena R, Kovrazhkina Elena A, Skvortsova Veronica I, Ling Shuo-Chien, Da Cruz Sandrine, Parone Philippe A, Buchman Vladimir L, Ninkina Natalia N