日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Lewy pathology formation in patient-derived GBA1 Parkinson's disease midbrain organoids.

患者来源的GBA1帕金森病中脑类器官中路易病理的形成

Frattini Emanuele, Faustini Gaia, Lopez Gianluca, Carsana Emma Veronica, Tosi Mattia, Trezzi Ilaria, Magni Manuela, Soldà Giulia, Straniero Letizia, Facchi Daniele, Samarani Maura, Martá-Ariza Mitchell, De Luca Chiara Maria Giulia, Vezzoli Elena, Pittaro Alessandra, Stepanyan Astghik, Silipigni Rosamaria, Rosety Isabel, Schwamborn Jens C, Sardi Sergio Pablo, Moda Fabio, Corti Stefania, Comi Giacomo P, Blandini Fabio, Tritsch Nicolas X, Bortolozzi Mario, Ferrero Stefano, Cribiù Fulvia Milena, Wisniewski Thomas, Asselta Rosanna, Aureli Massimo, Bellucci Arianna, Di Fonzo Alessio

Transcriptomic characterization of tissues from patients and subsequent pathway analyses reveal biological pathways that are implicated in spastic ataxia

对患者组织进行转录组学表征以及后续的通路分析,揭示了与痉挛性共济失调相关的生物学通路。

Kakouri, Andrea C; Votsi, Christina; Oulas, Anastasis; Nicolaou, Paschalis; Aureli, Massimo; Lunghi, Giulia; Samarani, Maura; Compagnoni, Giacomo M; Salani, Sabrina; Di Fonzo, Alessio; Christophides, Thalis; Tanteles, George A; Zamba-Papanicolaou, Eleni; Pantzaris, Marios; Spyrou, George M; Christodoulou, Kyproula

α-Synuclein fibrils subvert lysosome structure and function for the propagation of protein misfolding between cells through tunneling nanotubes

α-突触核蛋白原纤维通过隧道纳米管破坏溶酶体的结构和功能,从而在细胞间传播蛋白质错误折叠。

Dilsizoglu Senol, Aysegul; Samarani, Maura; Syan, Sylvie; Guardia, Carlos M; Nonaka, Takashi; Liv, Nalan; Latour-Lambert, Patricia; Hasegawa, Masato; Klumperman, Judith; Bonifacino, Juan S; Zurzolo, Chiara

Mitochondrial Dysregulation and Impaired Autophagy in iPSC-Derived Dopaminergic Neurons of Multiple System Atrophy.

多系统萎缩症中iPSC衍生多巴胺能神经元的线粒体功能失调和自噬受损

Monzio Compagnoni Giacomo, Kleiner Giulio, Samarani Maura, Aureli Massimo, Faustini Gaia, Bellucci Arianna, Ronchi Dario, Bordoni Andreina, Garbellini Manuela, Salani Sabrina, Fortunato Francesco, Frattini Emanuele, Abati Elena, Bergamini Christian, Fato Romana, Tabano Silvia, Miozzo Monica, Serratto Giulia, Passafaro Maria, Deleidi Michela, Silipigni Rosamaria, Nizzardo Monica, Bresolin Nereo, Comi Giacomo P, Corti Stefania, Quinzii Catarina M, Di Fonzo Alessio

Evidence for the Involvement of Lipid Rafts and Plasma Membrane Sphingolipid Hydrolases in Pseudomonas aeruginosa Infection of Cystic Fibrosis Bronchial Epithelial Cells

铜绿假单胞菌感染囊性纤维化支气管上皮细胞中脂筏和质膜鞘脂水解酶参与的证据

Schiumarini, Domitilla; Loberto, Nicoletta; Mancini, Giulia; Bassi, Rosaria; Giussani, Paola; Chiricozzi, Elena; Samarani, Maura; Munari, Silvia; Tamanini, Anna; Cabrini, Giulio; Lippi, Giuseppe; Dechecchi, Maria Cristina; Sonnino, Sandro; Aureli, Massimo

Novel positive allosteric modulators of sigma-1 receptor

新型σ-1受体正向变构调节剂

Saria, Alois; Prast, Janine; Schardl, Aurelia; Kummer, Kai; Vetrovoy, Oleg; Tyulkova, Ekaterina; Rybnikova, Elena; Otrokocsi, Lilla; Gölöncsér, Flóra; Sperlágh, Beáta; Kittel, Ágnes; Fedorovich, Sergei; Pekun, Tatyana; Hrynevich, Sviatlana; Waseem, Tatyana; Zhuravin, Igor; Dubrovskaya, Nadezhda; Vasilev, Dmitrii; Kozlova, Darya; Tumanova, Natalia; Turner, Anthony; Nalivaeva, Natalia; Popek, Mariusz; Frontczak-Baniewicz, Małgorzata; Zabłocka, Barbara; Albrecht, Jan; Zielińska, Magdalena; Taranukhin, Andrey; Saransaari, Pirjo; Oja, Simo; Samarani, Maura; Loberto, Nicoletta; Murdica, Valentina; Schiumarini, Domitilla; Prioni, Simona; Prinetti, Alessandro; Sonnino, Sandro; Bassi, Rosaria; Aureli, Massimo; Friedemann, Merlin; Helk, Eneken; Tiiman, Ann; Zovo, Kairit; Palumaa, Peep; Tõugu, Vello; Goloncser, Flora; Ando, Romeo; Zelena, Dora; Haller, Jozsef; Sperlagh, Beata; Horváth, Gergely; Otrokocsi, Lilla; Kittel, Ágnes; Baranyi, Mária; Sperlágh, Beáta; Link, Reet; Kopanchuk, Sergei; Rinken, Ago; Vavers, Edijs; Zvejniece, Liga; Veinberg, Grigory; Svalbe, Baiba; Domracheva, Ilona; Vilskersts, Reinis; Dambrova, Maija