Sustained oral spermidine supplementation rescues functional and structural defects in COL6-deficient myopathic mice
持续口服亚精胺补充剂可挽救 COL6 缺乏的肌病小鼠的功能和结构缺陷
期刊:Autophagy
影响因子:14.6
doi:10.1080/15548627.2023.2241125
Lisa Gambarotto, Samuele Metti, Matteo Corpetti, Martina Baraldo, Patrizia Sabatelli, Silvia Castagnaro, Matilde Cescon, Bert Blaauw, Paolo Bonaldo