日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Imbalanced TGFβ signalling and autophagy drive erythroid priming of hematopoietic stem cells in β-thalassemia

β-地中海贫血中TGFβ信号传导和自噬失衡驱动造血干细胞向红系分化。

Maria Rosa Lidonnici,Giulia Chianella,Nicole Mende,Hugo P Bastos,Matteo Barcella,Ivan Merelli,Mariangela Storto,Valentina Romeo,Francesca Tiboni,Samantha Scaramuzza,Claudia Rossi,Laura Raggi,Annamaria Aprile,Stefania Crippa,Deena Iskander,Irene Roberts,Anastasios Karamiditris,Julia Keith,Christophe Lechauve,Mitchell J Weiss,Nicola K Wilson,Berthold Göttgens,Maria Ester Bernardo ,Fabio Ciceri ,Alessandro Aiuti ,Sarah Marktel,Elisa Laurenti,Giuliana Ferrari

Imbalanced TGFβ signalling and autophagy drive erythroid priming of hematopoietic stem cells in β-thalassemia

β-地中海贫血中TGFβ信号传导和自噬失衡驱动造血干细胞向红系分化。

Maria Rosa Lidonnici ,Giulia Chianella ,Nicole Mende ,Hugo P Bastos ,Matteo Barcella ,Ivan Merelli ,Mariangela Storto ,Valentina Romeo ,Francesca Tiboni ,Samantha Scaramuzza ,Claudia Rossi ,Laura Raggi ,Annamaria Aprile ,Stefania Crippa ,Deena Iskander ,Irene Roberts ,Anastasios Karamiditris ,Julia Keith ,Christophe Lechauve ,Mitchell J Weiss ,Nicola K Wilson ,Berthold Göttgens ,Maria Ester Bernardo ,Fabio Ciceri ,Alessandro Aiuti ,Sarah Marktel ,Elisa Laurenti ,Giuliana Ferrari

Early bone marrow alterations in patients with adenosine deaminase 2 deficiency across disease phenotypes and severities

腺苷脱氨酶2缺乏症患者早期骨髓改变与疾病表型和严重程度的关系

Dimitri Bulté ,Federica Barzaghi ,Cristina Mesa-Nuñez ,Chiara Rigamonti ,Luca Basso-Ricci ,Camilla Visconti ,Stefania Crippa ,Emanuela Pettinato ,Diego Gilioli ,Raffaella Milani ,Pamela Quaranta ,Roberta Caorsi ,Alessia Cafaro ,Giuliana Cangemi ,Michela Lupia ,Francesca Schena ,Alice Grossi ,Giulia Di Colo ,Silvia Federici ,Antonella Insalaco ,Fabrizio De Benedetti ,Sarah Marktel ,Raffaella Di Micco ,Maria Ester Bernardo ,Serena Scala ,Maria Pia Cicalese ,Francesca Conti ,Maurizio Miano ,Marco Gattorno ,Carlo Dufour ,Alessandro Aiuti ,Alessandra Mortellaro

Early bone marrow alterations in patients with adenosine deaminase 2 deficiency across disease phenotypes and severities

腺苷脱氨酶2缺乏症患者早期骨髓改变与疾病表型和严重程度的关系

Dimitri Bulté,Federica Barzaghi,Cristina Mesa-Nuñez,Chiara Rigamonti,Luca Basso-Ricci,Camilla Visconti,Stefania Crippa,Emanuela Pettinato,Diego Gilioli,Raffaella Milani,Pamela Quaranta,Roberta Caorsi,Alessia Cafaro,Giuliana Cangemi,Michela Lupia,Francesca Schena,Alice Grossi,Giulia Di Colo,Silvia Federici,Antonella Insalaco,Fabrizio De Benedetti,Sarah Marktel,Raffaella Di Micco,Maria Ester Bernardo,Serena Scala,Maria Pia Cicalese,Francesca Conti,Maurizio Miano,Marco Gattorno,Carlo Dufour,Alessandro Aiuti,Alessandra Mortellaro

Cellular and transcriptional dynamics of human neutrophils at steady state and upon stress

人类中性粒细胞在稳定状态和应激状态下的细胞和转录动力学

Elisa Montaldo #, Eleonora Lusito #, Valentina Bianchessi #, Nicoletta Caronni #, Serena Scala, Luca Basso-Ricci, Carla Cantaffa, Alice Masserdotti, Mattia Barilaro, Simona Barresi, Marco Genua, Francesco Maria Vittoria, Giulia Barbiera, Dejan Lazarevic, Carlo Messina, Elisabetta Xue, Sarah Marktel,

Follicular helper T cell signature of replicative exhaustion, apoptosis, and senescence in common variable immunodeficiency

常见变异型免疫缺陷症中复制耗竭、凋亡和衰老的滤泡辅助 T 细胞特征

Giulia Milardi, Biagio Di Lorenzo, Jolanda Gerosa, Federica Barzaghi, Gigliola Di Matteo, Maryam Omrani, Tatiana Jofra, Ivan Merelli, Matteo Barcella, Matteo Filippini, Anastasia Conti, Francesca Ferrua, Francesco Pozzo Giuffrida, Francesca Dionisio, Patrizia Rovere-Querini, Sarah Marktel, Andrea As

Follicular helper T cell signature of replicative exhaustion, apoptosis, and senescence in common variable immunodeficiency

常见变异型免疫缺陷中滤泡辅助性T细胞的复制耗竭、凋亡和衰老特征

Giulia Milardi,Biagio Di Lorenzo,Jolanda Gerosa,Federica Barzaghi,Gigliola Di Matteo,Maryam Omrani,Tatiana Jofra,Ivan Merelli,Matteo Barcella,Matteo Filippini,Anastasia Conti,Francesca Ferrua,Francesco Pozzo Giuffrida,Francesca Dionisio,Patrizia Rovere-Querini,Sarah Marktel,Andrea Assanelli,Simona Piemontese,Immacolata Brigida,Matteo Zoccolillo,Emilia Cirillo,Giuliana Giardino,Maria Giovanna Danieli,Fernando Specchia,Lucia Pacillo,Silvia Di Cesare,Carmela Giancotta,Francesca Romano,Alessandro Matarese,Alfredo Antonio Chetta,Matteo Trimarchi,Andrea Laurenzi,Maurizio De Pellegrin,Silvia Darin,Davide Montin,Maddalena Marinoni,Rosa Maria Dellepiane,Valeria Sordi,Vassilios Lougaris,Angelo Vacca,Raffaella Melzi,Rita Nano,Chiara Azzari,Lucia Bongiovanni,Claudio Pignata,Caterina Cancrini,Alessandro Plebani,Lorenzo Piemonti,Constantinos Petrovas,Raffaella Di Micco,Maurilio Ponzoni,Alessandro Aiuti ,Maria Pia Cicalese,Georgia Fousteri

Bone marrow stromal cells from β-thalassemia patients have impaired hematopoietic supportive capacity

β-地中海贫血患者的骨髓基质细胞造血支持能力受损。

Stefania Crippa,Valeria Rossella,Annamaria Aprile,Laura Silvestri,Silvia Rivis,Samantha Scaramuzza,Stefania Pirroni,Maria Antonietta Avanzini,Luca Basso-Ricci,Raisa Jofra Hernandez,Marco Zecca,Sarah Marktel,Fabio Ciceri,Alessandro Aiuti ,Giuliana Ferrari,Maria Ester Bernardo

Bone marrow stromal cells from β-thalassemia patients have impaired hematopoietic supportive capacity

β-地中海贫血患者的骨髓基质细胞造血支持能力受损。

Stefania Crippa ,Valeria Rossella ,Annamaria Aprile ,Laura Silvestri ,Silvia Rivis ,Samantha Scaramuzza ,Stefania Pirroni ,Maria Antonietta Avanzini ,Luca Basso-Ricci ,Raisa Jofra Hernandez ,Marco Zecca ,Sarah Marktel ,Fabio Ciceri ,Alessandro Aiuti ,Giuliana Ferrari ,Maria Ester Bernardo

Interleukin-6 as Biomarker for Acute GvHD and Survival After Allogeneic Transplant With Post-transplant Cyclophosphamide

白细胞介素-6 作为急性移植物抗宿主病的生物标志物以及同种异体移植后使用环磷酰胺的存活率

Raffaella Greco, Francesca Lorentino, Rosamaria Nitti, Maria Teresa Lupo Stanghellini, Fabio Giglio, Daniela Clerici, Elisabetta Xue, Lorenzo Lazzari, Simona Piemontese, Sara Mastaglio, Andrea Assanelli, Sarah Marktel, Consuelo Corti, Massimo Bernardi, Fabio Ciceri, Jacopo Peccatori