日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Hepatorenal Tyrosinaemia: Impact of a Simplified Diet on Metabolic Control and Clinical Outcome

肝肾酪氨酸血症:简化饮食对代谢控制和临床结果的影响

Bärhold, Friederike; Meyer, Uta; Neugebauer, Anne-Kathrin; Thimm, Eva Maria; Lier, Dinah; Rosenbaum-Fabian, Stefanie; Och, Ulrike; Fekete, Anna; Möslinger, Dorothea; Rohde, Carmen; Beblo, Skadi; Hochuli, Michel; Bogovic, Nina; Korpel, Vanessa; Dahl, Stephan Vom; Mayorandan, Sebene; Fischer, Aleksandra; Freisinger, Peter; Dokoupil, Katharina; Heddrich-Ellerbrok, Margret; Jörg-Streller, Monika; van Teeffelen-Heithoff, Agnes; Lahl, Janina; Das, Anibh Martin

Activated L-Arginine/Nitric Oxide Pathway in Pediatric Cystic Fibrosis and Its Association with Pancreatic Insufficiency, Liver Involvement and Nourishment: An Overview and New Results

儿童囊性纤维化中激活的L-精氨酸/一氧化氮通路及其与胰腺功能不全、肝脏受累和营养状况的关系:概述和最新结果

Brinkmann, Folke; Hanusch, Beatrice; Ballmann, Manfred; Mayorandan, Sebene; Bollenbach, Alexander; Chobanyan-Jürgens, Kristine; Jansen, Kathrin; Schmidt-Choudhury, Anjona; Derichs, Nico; Tsikas, Dimitrios; Lücke, Thomas

Local and Systemic Alterations of the L-Arginine/Nitric Oxide Pathway in Sputum, Blood, and Urine of Pediatric Cystic Fibrosis Patients and Effects of Antibiotic Treatment

儿童囊性纤维化患者痰液、血液和尿液中L-精氨酸/一氧化氮通路局部和系统性改变及抗生素治疗的影响

Hanusch, Beatrice; Brinkmann, Folke; Mayorandan, Sebene; Chobanyan-Jürgens, Kristine; Wiemers, Anna; Jansen, Kathrin; Ballmann, Manfred; Schmidt-Choudhury, Anjona; Bollenbach, Alexander; Derichs, Nico; Tsikas, Dimitrios; Lücke, Thomas

Clinical course of 63 patients with neonatal onset urea cycle disorders in the years 2001-2013

2001-2013年间63例新生儿期起病的尿素循环障碍患者的临床病程

Unsinn, Caroline; Das, Anibh; Valayannopoulos, Vassili; Thimm, Eva; Beblo, Skadi; Burlina, Alberto; Konstantopoulou, Vassiliki; Mayorandan, Sebene; de Lonlay, Pascale; Rennecke, Jörg; Derbinski, Jens; Hoffmann, Georg F; Häberle, Johannes

Glycogen storage disease type III: modified Atkins diet improves myopathy

III型糖原贮积症:改良阿特金斯饮食可改善肌病

Mayorandan, Sebene; Meyer, Uta; Hartmann, Hans; Das, Anibh Martin

Cross-sectional study of 168 patients with hepatorenal tyrosinaemia and implications for clinical practice

一项针对168例肝肾酪氨酸血症患者的横断面研究及其对临床实践的意义

Mayorandan, Sebene; Meyer, Uta; Gokcay, Gülden; Segarra, Nuria Garcia; de Baulny, Hélène Ogier; van Spronsen, Francjan; Zeman, Jiri; de Laet, Corinne; Spiekerkoetter, Ute; Thimm, Eva; Maiorana, Arianna; Dionisi-Vici, Carlo; Moeslinger, Dorothea; Brunner-Krainz, Michaela; Lotz-Havla, Amelie Sophia; Cocho de Juan, José Angel; Couce Pico, Maria Luz; Santer, René; Scholl-Bürgi, Sabine; Mandel, Hanna; Bliksrud, Yngve Thomas; Freisinger, Peter; Aldamiz-Echevarria, Luis Jose; Hochuli, Michel; Gautschi, Matthias; Endig, Jessica; Jordan, Jens; McKiernan, Patrick; Ernst, Stefanie; Morlot, Susanne; Vogel, Arndt; Sander, Johannes; Das, Anibh Martin