日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Clonal CD8(+) T cells populate the leptomeninges and coordinate with immune cells in human degenerative brain diseases.

克隆 CD8(+) T 细胞存在于软脑膜中,并与人类退行性脑疾病中的免疫细胞协调作用。

Hobson Ryan, Levy Samuel H S, Singal Chitra Mohinder Singh, Flaherty Delaney, Xiao Harrison, Ciener Benjamin, Reddy Hasini, Zabinyakov Nick, Kim Christine Y, Teich Andrew F, Shneider Neil A, Bradshaw Elizabeth M, Elyaman Wassim

Amygdala TDP-43 pathology is associated with behavioural dysfunction and ferritin accumulation in amyotrophic lateral sclerosis.

杏仁核 TDP-43 病理与肌萎缩侧索硬化症中的行为功能障碍和铁蛋白积累有关。

Rifai Olivia M, Waldron Fergal M, O'Shaughnessy Judi, Read Fiona L, Gilodi Martina, Pastore Annalisa, Shneider Neil A, Tartaglia Gian Gaetano, Zacco Elsa, Spence Holly, Gregory Jenna M

Secondary prophylaxis of variceal hemorrhage in biliary atresia-Analysis of prospective multicenter studies

胆道闭锁患者静脉曲张出血的二级预防——前瞻性多中心研究分析

Bass, Lee M; Hawthorne, Kieran; Magee, John C; Shneider, Benjamin L

Twelve-Month Outcome of Nasolabial Fold Correction by a Novel Non-1,4-Butanediol Diglycidyl Ether, Click-Crosslinked, Long-Chain Hyaluronic Acid Product

一种新型非1,4-丁二醇二缩水甘油醚、点击交联的长链透明质酸产品治疗鼻唇沟的12个月疗效

Safir, Ari; Sattler, Sonja; Da Mota, Rodrigo; Kowalska-Olędzka, Elzbieta; Kedar, Daniel J; Gronovich, Yoav; Lotan, Adi Maisel; Shneider, Svetlana; Meunier, Stephane; Artzi, Ofir

A strategy to identify biliary atresia efficiently: A perspective from a Texas center

高效识别胆道闭锁的策略:来自德克萨斯州中心的视角

Harpavat, Sanjiv; Rabbani, Tebyan A; Upton, Ashley M; Devaraj, Sridevi; Hernandez, Jose A; Shneider, Benjamin L

Antisense oligonucleotide jacifusen for FUS-ALS: an investigator-initiated, multicentre, open-label case series

针对FUS-ALS的反义寡核苷酸jacifusen:一项研究者发起的多中心、开放标签病例系列研究

Shneider, Neil A; Harms, Matthew B; Korobeynikov, Vlad A; Rifai, Olivia M; Hoover, Benjamin N; Harrington, Elizabeth A; Aziz-Zaman, Sonya; Singleton, Jessica; Jamil, Arish; Madan, Vikram R; Lee, Ikjae; Andrews, Jinsy A; Smiley, Richard M; Alam, Mahabub M; Black, Lauren E; Shin, Minwook; Watts, Jonathan K; Walk, David; Newman, Daniel; Pascuzzi, Robert M; Weber, Markus; Neuwirth, Christoph; Da Cruz, Sandrine; Soriano, Armand; Lane, Roger; Henry, Scott; Mathews, Joel; Jafar-Nejad, Paymaan; Norris, Dan; Rigo, Frank; Brown, Robert H; Miller, Stephan; Crean, Rebecca; Bennett, C Frank

Prospective Analysis of Liver Stiffness Measurement by Vibration Controlled Transient Elastography as a Predictor of Outcomes in Biliary Atresia

前瞻性分析振动控制瞬时弹性成像测量的肝脏硬度作为胆道闭锁预后指标的价值

Molleston, Jean P; Goodrich, Nathan P; Ye, Wen; Leung, Daniel H; Sokol, Ronald J; Shneider, Benjamin L

TDP-43-dependent mis-splicing of KCNQ2 triggers intrinsic neuronal hyperexcitability in ALS/FTD.

TDP-43 依赖的 KCNQ2 错误剪接引发 ALS/FTD 中的内在神经元过度兴奋。

Joseph Brian J, Marshall Kelly A, Harley Peter, Mann Jacob R, Alessandrini Francesco, Vanoye Carlos G, Chi Wanhao, Prudencio Mercedes, Simkin Dina, Kao Tzu-Ting, Desai Reshma R, Keuss Matthew J, Barattucci Simone, Zanovello Matteo, Mehta Puja R, DeKeyser Jean-Marc, Limone Francesco, Lee Jonathan, Brown Anna-Leigh, Leyton-Jaimes Marcel F, Nash Leslie A, Juan Irune Guerra San, Aronica Eleonora, Wainger Brian J, Shah Mala, Goswami Anand, Shneider Neil A, Dickson Dennis W, Burrone Juan, Zhang Chaolin, Wichterle Hynek, Petrucelli Leonard, Watts Jonathan K, George Alfred L Jr, Fratta Pietro, Eggan Kevin, Kiskinis Evangelos

Multiplex neurodegeneration proteotoxicity platform reveals DNAJB6 promotes non-toxic FUS condensate gelation and inhibits neurotoxicity

多重神经退行性疾病蛋白毒性平台揭示DNAJB6促进无毒FUS凝聚物凝胶化并抑制神经毒性

Resnick, Samuel J; Qamar, Seema; Krishna, Pushya; Korobeynikov, Vladislav; Ausserwoger, Hannes; Miller, Alyssa; Esposito, Pietro; Varela, Juan A; Sheng, Jenny; Huang, Lei Haley; Nixon-Abell, Jonathon; Melore, Schuyler; Chung, Chyi Wei; Läubli, Nino F; Kapsiani, Sofia; Li, Xuecong; Wang, Jingshu; Zhang, Nancy; Alam, Mahabub Maraj; Burguete, Alondra S; Swayne, Theresa C; Chen, Yanyan; Liao, Ya-Cheng; Shneider, Neil A; Vendruscolo, Michele; Knowles, Tuomas P J; Kaminski, Clemens F; Ruggeri, Francesco Simone; Kaminski Schierle, Gabriele S; St George-Hyslop, Peter; Chavez, Alejandro

Amyloid fibril structures link CHCHD10 and CHCHD2 to neurodegeneration.

淀粉样原纤维结构将 CHCHD10 和 CHCHD2 与神经退行性疾病联系起来

Lv Guohua, Sayles Nicole M, Huang Yun, Mancinelli Chiara, McAvoy Kevin, Shneider Neil A, Manfredi Giovanni, Kawamata Hibiki, Eliezer David