日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

The Wolfram-like variant WFS1E864K destabilizes MAM and compromises autophagy and mitophagy in human and mice

Wolfram 样变体 WFS1E864K 会破坏 MAM 的稳定性,并损害人和小鼠的自噬和线粒体自噬。

Simone Patergnani ,Méghane S Bataillard ,Alberto Danese ,Stacy Alves ,Chantal Cazevieille ,René Valéro ,Lisbeth Tranebjærg ,Tangui Maurice ,Paolo Pinton ,Benjamin Delprat ,Elodie M Richard

Thonzonium bromide inhibits progression of malignant pleural mesothelioma through regulation of ERK1/2 and p38 pathways and mitochondrial uncoupling

溴化铊通过调节 ERK1/2 和 p38 通路以及线粒体解偶联抑制恶性胸膜间皮瘤进展

Irene Dell'Anno, Federica Morani, Simone Patergnani, Antonio Daga, Paolo Pinton, Carlotta Giorgi, Luciano Mutti, Federica Gemignani, Stefano Landi

ErbB2-NOTCH1 axis controls autophagy in cardiac cells

ErbB2-NOTCH1 轴控制心脏细胞自噬

Francesca Fortini, Francesco Vieceli Dalla Sega, Edoardo Lazzarini, Giorgio Aquila, Polina Sysa-Shah, Edoardo Bertero, Alessia Ascierto, Paolo Severi, Achille Wilfred Ouambo Talla, Alessio Schirone, Kathleen Gabrielson, Giampaolo Morciano, Simone Patergnani, Gaia Pedriali, Paolo Pinton, Roberto Ferr

1,3,8-Triazaspiro[4.5]decane Derivatives Inhibit Permeability Transition Pores through a FO-ATP Synthase c Subunit Glu119-Independent Mechanism That Prevents Oligomycin A-Related Side Effects

1,3,8-三氮杂螺[4.5]癸烷衍生物通过 FO-ATP 合酶 c 亚基 Glu119 非依赖性机制抑制通透性转换孔,从而预防寡霉素 A 相关副作用

Gaia Pedriali, Daniela Ramaccini, Esmaa Bouhamida, Alessio Branchini, Giulia Turrin, Elisabetta Tonet, Antonella Scala, Simone Patergnani, Mirko Pinotti, Claudio Trapella, Carlotta Giorgi, Elena Tremoli, Gianluca Campo, Giampaolo Morciano, Paolo Pinton

Activation of the sigma-1 receptor chaperone alleviates symptoms of Wolfram syndrome in preclinical models

sigma-1 受体伴侣的激活可缓解临床前模型中的 Wolfram 综合征症状

Lucie Crouzier, Alberto Danese, Yuko Yasui, Elodie M Richard, Jean-Charles Liévens, Simone Patergnani, Simon Couly, Camille Diez, Morgane Denus, Nicolas Cubedo, Mireille Rossel, Marc Thiry, Tsung-Ping Su, Paolo Pinton, Tangui Maurice, Benjamin Delprat

Pathological mitophagy disrupts mitochondrial homeostasis in Leber's hereditary optic neuropathy

病理性线粒体自噬破坏了莱伯氏遗传性视神经病变中的线粒体稳态

Alberto Danese, Simone Patergnani, Alessandra Maresca, Camille Peron, Andrea Raimondi, Leonardo Caporali, Saverio Marchi, Chiara La Morgia, Valentina Del Dotto, Claudia Zanna, Angelo Iannielli, Alice Segnali, Ivano Di Meo, Andrea Cavaliere, Magdalena Lebiedzinska-Arciszewska, Mariusz R Wieckowski, A

Metformin Induces Apoptosis and Inhibits Notch1 in Malignant Pleural Mesothelioma Cells

二甲双胍诱导恶性胸膜间皮瘤细胞凋亡并抑制 Notch1

Marika Rossini, Fernanda Martini, Elena Torreggiani, Francesca Fortini, Giorgio Aquila, Francesco Vieceli Dalla Sega, Simone Patergnani, Paolo Pinton, Pio Maniscalco, Giorgio Cavallesco, Paola Rizzo, Mauro Tognon

BAP1 forms a trimer with HMGB1 and HDAC1 that modulates gene × environment interaction with asbestos

BAP1 与 HMGB1 和 HDAC1 形成三聚体,调节基因×环境与石棉的相互作用

Flavia Novelli, Angela Bononi, Qian Wang, Fang Bai, Simone Patergnani, Franz Kricek, Ellinor Haglund, Joelle S Suarez, Mika Tanji, Ronghui Xu, Yasutaka Takanishi, Michael Minaai, Sandra Pastorino, Paul Morris, Greg Sakamoto, Harvey I Pass, Haithem Barbour, Giovanni Gaudino, Carlotta Giorgi, Paolo Pi

Hydroxylapatite-collagen hybrid scaffold induces human adipose-derived mesenchymal stem cells to osteogenic differentiation in vitro and bone regrowth in patients

羟基磷灰石-胶原混合支架诱导人类脂肪间充质干细胞体外成骨分化及患者骨再生

Elisa Mazzoni, Antonio D'Agostino, Maria Rosa Iaquinta, Ilaria Bononi, Lorenzo Trevisiol, John Charles Rotondo, Simone Patergnani, Carlotta Giorgi, Michael J Gunson, G William Arnett, Pier Francesco Nocini, Mauro Tognon, Fernanda Martini

Calcium mishandling in absence of primary mitochondrial dysfunction drives cellular pathology in Wolfram Syndrome

在没有原发性线粒体功能障碍的情况下,钙处理不当会导致 Wolfram 综合征的细胞病理

Chiara La Morgia #, Alessandra Maresca #, Giulia Amore, Laura Ludovica Gramegna, Michele Carbonelli, Emanuela Scimonelli, Alberto Danese, Simone Patergnani, Leonardo Caporali, Francesca Tagliavini, Valentina Del Dotto, Mariantonietta Capristo, Federico Sadun, Piero Barboni, Giacomo Savini, Stefania