日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Rps19 (R67∆) mutation creates a model of Diamond-Blackfan anemia and reveals downstream mediators of p53 pathway

Rps19 (R67∆) 突变构建了 Diamond-Blackfan 贫血模型,并揭示了 p53 通路的下游介质。

Kokavec, Juraj; Turková, Tereza; Schuster, Björn; Prochazka, Jan; Spoutil, František; Jamrichová, Kristína; Holečková, Markéta; Chalupský, Karel; Beck, Inken M; Ruberte, Jesús; Vale, Matilde; Čermák, Lukáš; Stopka, Tomáš; Sedlacek, Radislav

FAM83H Regulates Postnatal T Cell Development Through Thymic Stroma Organization

FAM83H通过胸腺基质组织调控出生后T细胞发育

Ogan, Betul Melike; Forstlova, Veronika; Dowling, Laura Jane; Simova, Michaela; Vicikova, Kristina; Novosadova, Vendula; Spoutil, Frantisek; Cervenkova, Sylvie; Procházková, Michaela; Tureckova, Jolana; Fedosieieva, Olha; Labaj, Juraj; Nickl, Petr; Krizova, Kamila; Prochazka, Jan; Sedlacek, Radislav; Balounova, Jana

Achondroplasia: aligning mouse model with human clinical studies shows crucial importance of immediate postnatal start of the therapy

软骨发育不全:小鼠模型与人类临床研究的对比表明,出生后立即开始治疗至关重要。

Rico-Llanos, Gustavo; Spoutil, Frantisek; Blahova, Eva; Koudelka, Adolf; Prochazkova, Michaela; Czyrek, Aleksandra; Fafilek, Bohumil; Prochazka, Jan; Gonzalez Lopez, Marcos; Krivanek, Jan; Sedlacek, Radislav; Krakow, Deborah; Nonaka, Yosuke; Nakamura, Yoshikazu; Krejci, Pavel

Skeletal dysmorphology and mineralization defects in Fgf20 KO mice

Fgf20 KO 小鼠的骨骼形态学和矿化缺陷

Sylvie Dlugosova, Frantisek Spoutil, Carlos Eduardo Madureira Trufen, Betul Melike Ogan, Michaela Prochazkova, Olha Fedosieieva, Petr Nickl, Goretti Aranaz Novaliches, Radislav Sedlacek, Jan Prochazka

Autoimmune amelogenesis imperfecta in patients with APS-1 and coeliac disease

患有 APS-1 和乳糜泻的患者的自身免疫性牙釉质形成不全症

Yael Gruper, Anette S B Wolff, Liad Glanz, Frantisek Spoutil, Mihaela Cuida Marthinussen, Adriana Osickova, Yonatan Herzig, Yael Goldfarb, Goretti Aranaz-Novaliches, Jan Dobeš, Noam Kadouri, Osher Ben-Nun, Amit Binyamin, Bar Lavi, Tal Givony, Razi Khalaila, Tom Gome, Tomáš Wald, Blanka Mrazkova, Car

Omega-3 PUFAs prevent bone impairment and bone marrow adiposity in mouse model of obesity

Omega-3 PUFA 可预防肥胖小鼠的骨质疏松和骨髓脂肪沉积

Andrea Benova, Michaela Ferencakova, Kristina Bardova, Jiri Funda, Jan Prochazka, Frantisek Spoutil, Tomas Cajka, Martina Dzubanova, Tim Balcaen, Greet Kerckhofs, Wouter Willekens, G Harry van Lenthe, Arzuv Charyyeva, Glenda Alquicer, Alena Pecinova, Tomas Mracek, Olga Horakova, Roman Coupeau, Morte

Early evolution of enamel matrix proteins is reflected by pleiotropy of physiological functions

牙釉质基质蛋白的早期进化反映出生理功能的多效性

Frantisek Spoutil, Goretti Aranaz-Novaliches, Michaela Prochazkova, Tomas Wald, Vendula Novosadova, Petr Kasparek, Radim Osicka, Janne E Reseland, Staale P Lyngstadaas, Hanna Tiainen, Kristyna Bousova, Jiri Vondrasek, Radislav Sedlacek, Jan Prochazka

Mitochondrially targeted tamoxifen alleviates markers of obesity and type 2 diabetes mellitus in mice.

线粒体靶向他莫昔芬可减轻小鼠的肥胖和 2 型糖尿病指标

Vacurova Eliska, Trnovska Jaroslava, Svoboda Petr, Skop Vojtech, Novosadova Vendula, Reguera David Pajuelo, Petrezselyová Silvia, Piavaux Benoit, Endaya Berwini, Spoutil Frantisek, Zudova Dagmar, Stursa Jan, Melcova Magdalena, Bielcikova Zuzana, Werner Lukas, Prochazka Jan, Sedlacek Radislav, Huttl Martina, Hubackova Sona Stemberkova, Haluzik Martin, Neuzil Jiri

Novel thiazolidinedione analog reduces a negative impact on bone and mesenchymal stem cell properties in obese mice compared to classical thiazolidinediones

与传统噻唑烷二酮相比,新型噻唑烷二酮类似物可减少对肥胖小鼠骨骼和间充质干细胞特性的负面影响

Andrea Benova, Michaela Ferencakova, Kristina Bardova, Jiri Funda, Jan Prochazka, Frantisek Spoutil, Tomas Cajka, Martina Dzubanova, Tim Balcaen, Greet Kerckhofs, Wouter Willekens, G Harry van Lenthe, Glenda Alquicer, Alena Pecinova, Tomas Mracek, Olga Horakova, Martin Rossmeisl, Jan Kopecky, Michae

Molecular interactions of adaptor protein PSTPIP2 control neutrophil-mediated responses leading to autoinflammation

衔接蛋白PSTPIP2的分子相互作用控制中性粒细胞介导的反应,从而导致自身炎症

Nataliia Pavliuchenko ,Iris Duric ,Jarmila Kralova ,Matej Fabisik ,Frantisek Spoutil ,Jan Prochazka ,Petr Kasparek ,Jana Pokorna ,Tereza Skopcova ,Radislav Sedlacek ,Tomas Brdicka