日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

MYH11 variants in thoracic aortic aneurysm pathophysiology: From bench to bedside

MYH11变异体在胸主动脉瘤病理生理学中的作用:从实验室到临床

Atash, Aria; Mees, Barend M E; Cramer, Maarten J; Baas, Annette F; Schurgers, Leon J; Doevendans, Pieter A; Stillitano, Francesca

Setting the stage for cardiomyopathy gene editing trials: a systematic review of isogenic pair use in human induced pluripotent stem cell-derived cardiomyocyte research

为心肌病基因编辑试验奠定基础:人类诱导多能干细胞衍生心肌细胞研究中同源细胞对使用的系统评价

van der Wilt, C Nina; Veltrop, Rogier J A; Janssens, Maaike H; Bakker, Iara; Stillitano, Francesca; Sluijter, Joost P G; van Laake, Linda W; van der Velden, Jolanda; Villard, Eric; Montag, Judith; Denning, Chris; van Tintelen, J Peter; Te Riele, Anneline S J M; van der Harst, Pim; Schurgers, Leon J; van Steenbeek, Frank G; Harakalova, Magdalena

Isoform changes of action potential regulators in the ventricles of arrhythmogenic phospholamban-R14del humanized mouse hearts

心律失常磷蛋白-R14del人源化小鼠心脏心室动作电位调节蛋白的亚型变化

Rogalska, Malgorzata E; Vafiadaki, Elizabeth; Erpapazoglou, Zoi; Haghighi, Kobra; Green, Lisa; Mantzoros, Christos S; Hajjar, Roger J; Tranter, Michael; Karakikes, Ioannis; Kranias, Evangelia G; Stillitano, Francesca; Kafasla, Panagiota; Sanoudou, Despina

Gene editing reverses arrhythmia susceptibility in humanized PLN-R14del mice: modelling a European cardiomyopathy with global impact

基因编辑逆转人源化PLN-R14del小鼠的心律失常易感性:模拟一种具有全球影响的欧洲心肌病

Dave, Jaydev; Raad, Nour; Mittal, Nishka; Zhang, Lu; Fargnoli, Anthony; Oh, Jae Gyun; Savoia, Maria Elisabetta; Hansen, Jens; Fava, Marika; Yin, Xiaoke; Theofilatos, Konstantinos; Ceholski, Delaine; Kohlbrenner, Erik; Jeong, Dongtak; Wills, Lauren; Nonnenmacher, Mathieu; Haghighi, Kobra; Costa, Kevin D; Turnbull, Irene C; Mayr, Manuel; Cai, Chen-Leng; Kranias, Evangelia G; Akar, Fadi G; Hajjar, Roger J; Stillitano, Francesca

Arrhythmia Mechanism and Dynamics in a Humanized Mouse Model of Inherited Cardiomyopathy Caused by Phospholamban R14del Mutation

磷蛋白R14del突变引起的遗传性心肌病的人源化小鼠模型中的心律失常机制和动力学

Raad, Nour; Bittihn, Philip; Cacheux, Marine; Jeong, Dongtak; Ilkan, Zeki; Ceholski, Delaine; Kohlbrenner, Erik; Zhang, Lu; Cai, Chen-Leng; Kranias, Evangelia G; Hajjar, Roger J; Stillitano, Francesca; Akar, Fadi G

Impaired Right Ventricular Calcium Cycling Is an Early Risk Factor in R14del-Phospholamban Arrhythmias.

右心室钙循环受损是 R14del-磷蛋白心律失常的早期危险因素

Haghighi Kobra, Gardner George, Vafiadaki Elizabeth, Kumar Mohit, Green Lisa C, Ma Jianyong, Crocker Jeffrey S, Koch Sheryl, Arvanitis Demetrios A, Bidwell Phillip, Rubinstein Jack, van de Leur Rutger, Doevendans Pieter A, Akar Fadi G, Tranter Michael, Wang Hong-Sheng, Sadayappan Sakthivel, DeMazumder Deeptankar, Sanoudou Despina, Hajjar Roger J, Stillitano Francesca, Kranias Evangelia G

Exosomal microRNA-21-5p Mediates Mesenchymal Stem Cell Paracrine Effects on Human Cardiac Tissue Contractility

外泌体microRNA-21-5p介导间充质干细胞对人类心脏组织收缩力的旁分泌效应

Mayourian, Joshua; Ceholski, Delaine K; Gorski, Przemek A; Mathiyalagan, Prabhu; Murphy, Jack F; Salazar, Sophia I; Stillitano, Francesca; Hare, Joshua M; Sahoo, Susmita; Hajjar, Roger J; Costa, Kevin D

Functional and transcriptomic insights into pathogenesis of R9C phospholamban mutation using human induced pluripotent stem cell-derived cardiomyocytes

利用人诱导多能干细胞衍生的心肌细胞,从功能和转录组学角度深入了解R9C磷蛋白突变的发病机制

Ceholski, Delaine K; Turnbull, Irene C; Kong, Chi-Wing; Koplev, Simon; Mayourian, Joshua; Gorski, Przemek A; Stillitano, Francesca; Skodras, Angelos A; Nonnenmacher, Mathieu; Cohen, Ninette; Björkegren, Johan L M; Stroik, Daniel R; Cornea, Razvan L; Thomas, David D; Li, Ronald A; Costa, Kevin D; Hajjar, Roger J

Cardiac Tissue Engineering Models of Inherited and Acquired Cardiomyopathies

遗传性和获得性心肌病的心脏组织工程模型

Turnbull, Irene C; Mayourian, Joshua; Murphy, Jack F; Stillitano, Francesca; Ceholski, Delaine K; Costa, Kevin D

Considerations for pre-clinical models and clinical trials of pluripotent stem cell-derived cardiomyocytes

多能干细胞衍生心肌细胞的临床前模型和临床试验的考量

Hulot, Jean-Sébastien; Stillitano, Francesca; Salem, Joe Elie; Kovacic, Jason C; Fuster, Valentin; Hajjar, Roger J