日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Z variant heterozygosity in alpha-1 antitrypsin deficiency: disease risk and treatment implications

α1-抗胰蛋白酶缺乏症中Z变异杂合性:疾病风险和治疗意义

Hersh, Craig P; Teckman, Jeffrey H; Strnad, Pavel; Hakim, Aaron; Carroll, Tomás P; Hall, Ian P; Ghosh, Auyon J; Barjaktarevic, Igor; McElvaney, Noel G; Kaserman, Joseph E; Lomas, David A; Strange, Charlie; Drummond, M Bradley; Rennard, Stephen; Hanna, Kathi E; Clark, Virginia C; Goldklang, Monica P; Iverson, Peg; Wilson, Andrew A

Two randomised controlled phase 2 studies of the oral neutrophil elastase inhibitor alvelestat in alpha-1 antitrypsin deficiency

两项随机对照 II 期研究评估了口服中性粒细胞弹性蛋白酶抑制剂阿维司他治疗 α1-抗胰蛋白酶缺乏症的疗效

Wells, J Michael; Titlestad, Ingrid L; Tanash, Hanan; Turner, Alice M; Chapman, Kenneth R; Hatipoğlu, Umur Ş; Goldklang, Monica P; D'Armiento, Jeanine M; Pirozzi, Cheryl S; Drummond, M Bradley; Barjaktarevic, Igor Z; Chatila, Wissam M; Devine, Megan S; Strange, Charlie; Sandhaus, Robert A; Parkin, Jacqueline M; Westfall, Elizabeth; Lin, Vivian Y; Parks, Robin; Kuo, Hui-Chien; Ekue, Adzoa; Moffitt, Kelly L; Inshaw, Jamie; Aban, Inmaculada; Dransfield, Mark T; Stockley, Robert A

The Use of Computed Tomography Densitometry for the Assessment of Emphysema in Clinical Trials: A Position Paper from the Fleischner Society

弗莱施纳学会关于在临床试验中应用计算机断层扫描密度测定法评估肺气肿的立场文件

San José Estépar, Raúl; Barr, R Graham; Fain, Sean B; Grenier, Philippe A; Hoffman, Eric A; Humphries, Stephen M; Kirby, Miranda; Obuchowski, Nancy; Ryerson, Christopher J; Seo, Joon Beom; Tal-Singer, Ruth; Ash, Samuel Y; Bankier, Alexander A; Crapo, James; Han, MeiLan K; Kellermeyer, Liz; Goldin, Jonathan; McCollough, Cynthia H; Newell, John D Jr; Miller, Bruce E; Nordenmark, Lars H; Remy-Jardin, Martine; Prokop, Mathias; Ohno, Yoshiharu; Silverman, Edwin K; Strange, Charlie; Washko, George R; Lynch, David A

Randomized Sham-controlled Trial of Targeted Lung Denervation in Patients with Chronic Obstructive Pulmonary Disease (AIRFLOW-3)

针对慢性阻塞性肺疾病患者的靶向肺去神经术的随机假对照试验(AIRFLOW-3)

Shah, Pallav L; Slebos, Dirk-Jan; Sue, Richard; Bhatt, Surya P; Ghattas, Christian; Strange, Charlie; Degano, Bruno; Valipour, Arschang; Eisenmann, Stephan; De Cardenas, Jose; Marquette, Charles-Hugo; Soto-Soto, Jose; Sciurba, Frank C; Conway, Francesca; Tonkin, James; Tana, Anand; Marchetti, Nathaniel; Hartman, Jorine E; Heluain, Valentin; Guibert, Nicolas; Criner, Gerard J

AAT-MSC-EVs: Novel implications for suppressing ferroptosis, fibrosis and pain associated with chronic pancreatitis

AAT-MSC-EVs:抑制慢性胰腺炎相关铁死亡、纤维化和疼痛的新意义

Shoeibi, Sara; Gou, Wenyu; Yeung, Tiffany; Helke, Kristi; Green, Erica; Strange, Charlie; Wang, Hongjun

Longitudinal Outcomes in Pi*MZ Alpha-1 Antitrypsin-Deficient Individuals with Tobacco Smoking History from the SPIROMICS Cohort

来自 SPIROMICS 队列的 Pi*MZ α-1 抗胰蛋白酶缺乏症患者(有吸烟史)的纵向结局

Barjaktarevic, Igor; Hixson, Roxana; Zhuang, Zian; Buhr, Russell G; Tejwani, Vickram; Barr, R Graham; Bateman, Lori A; Bhatt, Surya P; Bleecker, Eugene R; Cooper, Christopher B; Curtis, Jeffrey L; Drummond, M Bradley; Fortis, Spyridon; Ghosh, Auyon J; Han, MeiLan; Hansel, Nadia N; Hoffman, Eric A; Ohar, Jill; Martinez, Fernando J; Meyers, Deborah A; Paine, Robert 3rd; Pirozzi, Cheryl S; Sandhaus, Robert; Strange, Charlie; Tashkin, Donald P; Wells, J Michael; Woodruff, Prescott; Ortega, Victor E

Increased exacerbations and hospitalizations among PI*MZ compared to PI*MM individuals: an electronic health record analysis

与PI*MM个体相比,PI*MZ个体病情加重和住院率更高:一项电子健康记录分析

Tejwani, Vickram; Wang, Yifan; Tremblay, Lauren Munoz; Azzato, Elizabeth; Baldomero, Arianne K; Wendt, Christine; Attaway, Amy; Bowler, Russell; Hatipoglu, Umur; Hutton, Rebecca; Strange, Charlie; Wang, Xiaofeng; Ortega, Victor E; Zein, Joe; Stoller, James K

Matrix metalloproteinases and disease severity among PI*MZ and PI*ZZ individuals in the Genomic Research in Alpha-1 Antitrypsin Deficiency and Sarcoidosis (GRADS) cohort

α1-抗胰蛋白酶缺乏症和结节病基因组研究(GRADS)队列中PI*MZ和PI*ZZ个体的基质金属蛋白酶和疾病严重程度

Tejwani, Vickram; Bowler, Russell P; Serban, Karina A; Pratte, Katherine A; Ortega, Victor E; Stoller, James K; Kaminski, Naftali; Strange, Charlie

Rationale and Design of the Alpha-1 Biomarkers Consortium Study

Alpha-1生物标志物联盟研究的理论基础和设计

Goldklang, Monica P; Pirozzi, Cheryl; Barjaktarevic, Igor; Bhatt, Surya P; Bodduluri, Sandeep; Drummond, M Bradley; Fonseca, Laura; Hogarth, D Kyle; Keaveny, Alison; Liu, Zhongua; McElvaney, Noel G; McElvaney, Oliver J; Nuchovich, Nadine; Palumbo, Sabrina; Plant, Randel; Sandhaus, Robert; Wells, J Michael; Wilson, Andrew; Strange, Charlie; D'Armiento, Jeanine M

Improving the Likelihood of Identifying Alpha-1 Antitrypsin Deficiency Among Patients With COPD: A Novel Predictive Model Using Real-World Data

利用真实世界数据构建新型预测模型,提高慢性阻塞性肺疾病患者α1-抗胰蛋白酶缺乏症的检出率

Pfeffer, Daniel N; Dhakne, Rahul; El Massad, Omnya; Sehgal, Pulkit; Ardiles, Thomas; Calloway, Michael O; Runken, M Chris; Strange, Charlie