ADAMTSL6β protein rescues fibrillin-1 microfibril disorder in a Marfan syndrome mouse model through the promotion of fibrillin-1 assembly
ADAMTSL6β蛋白通过促进纤连蛋白-1的组装,挽救马凡氏综合征小鼠模型中的纤连蛋白-1微纤维紊乱。
期刊:Journal of Biological Chemistry
影响因子:3.9
doi:10.1074/jbc.M111.243451
Saito, Masahiro; Kurokawa, Misaki; Oda, Masahito; Oshima, Masamitsu; Tsutsui, Ko; Kosaka, Kazutaka; Nakao, Kazuhisa; Ogawa, Miho; Manabe, Ri-Ichiroh; Suda, Naoto; Ganjargal, Ganburged; Hada, Yasunobu; Noguchi, Toshihide; Teranaka, Toshio; Sekiguchi, Kiyotoshi; Yoneda, Toshiyuki; Tsuji, Takashi