日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Alpha-lipoic acid supplementation improves pathological alterations in cellular models of Friedreich ataxia.

α-硫辛酸补充剂可改善弗里德赖希共济失调细胞模型中的病理改变

Talaverón-Rey Marta, Reche-López Diana, Povea-Cabello Suleva, Álvarez-Córdoba Mónica, Gómez-Fernández David, Romero-González Ana, Cilleros-Holgado Paula, Romero-Domínguez José Manuel, López-Cabrera Alejandra, Piñero-Pérez Rocío, González-Granero Susana, García-Verdugo José Manuel, Sánchez-Alcázar José A

Vicious cycle of lipid peroxidation and iron accumulation in neurodegeneration

神经退行性疾病中脂质过氧化和铁积累的恶性循环

Villalón-García, Irene; Povea-Cabello, Suleva; Álvarez-Córdoba, Mónica; Talaverón-Rey, Marta; Suárez-Rivero, Juan M; Suárez-Carrillo, Alejandra; Munuera-Cabeza, Manuel; Reche-López, Diana; Cilleros-Holgado, Paula; Piñero-Pérez, Rocío; Sánchez-Alcázar, José A

Antioxidants Prevent Iron Accumulation and Lipid Peroxidation, but Do Not Correct Autophagy Dysfunction or Mitochondrial Bioenergetics in Cellular Models of BPAN

抗氧化剂可预防铁积累和脂质过氧化,但不能纠正BPAN细胞模型中的自噬功能障碍或线粒体生物能量学异常。

Suárez-Carrillo, Alejandra; Álvarez-Córdoba, Mónica; Romero-González, Ana; Talaverón-Rey, Marta; Povea-Cabello, Suleva; Cilleros-Holgado, Paula; Piñero-Pérez, Rocío; Reche-López, Diana; Gómez-Fernández, David; Romero-Domínguez, José Manuel; Munuera-Cabeza, Manuel; Díaz, Antonio; González-Granero, Susana; García-Verdugo, José Manuel; Sánchez-Alcázar, José A

mtUPR Modulation as a Therapeutic Target for Primary and Secondary Mitochondrial Diseases

线粒体未折叠蛋白反应(mtUPR)调节作为原发性和继发性线粒体疾病的治疗靶点

Cilleros-Holgado, Paula; Gómez-Fernández, David; Piñero-Pérez, Rocío; Reche-López, Diana; Álvarez-Córdoba, Mónica; Munuera-Cabeza, Manuel; Talaverón-Rey, Marta; Povea-Cabello, Suleva; Suárez-Carrillo, Alejandra; Romero-González, Ana; Suárez-Rivero, Juan Miguel; Romero-Domínguez, Jose Manuel; Sánchez-Alcázar, Jose Antonio

Patient-Derived Cellular Models for Polytarget Precision Medicine in Pantothenate Kinase-Associated Neurodegeneration

用于泛酸激酶相关神经退行性疾病多靶点精准医疗的患者来源细胞模型

Álvarez-Córdoba, Mónica; Talaverón-Rey, Marta; Povea-Cabello, Suleva; Cilleros-Holgado, Paula; Gómez-Fernández, David; Piñero-Pérez, Rocío; Reche-López, Diana; Munuera-Cabeza, Manuel; Suárez-Carrillo, Alejandra; Romero-González, Ana; Romero-Domínguez, Jose Manuel; López-Cabrera, Alejandra; Armengol, José Ángel; Sánchez-Alcázar, José Antonio

Neurodegeneration, Mitochondria, and Antibiotics

神经退行性疾病、线粒体和抗生素

Suárez-Rivero, Juan M; López-Pérez, Juan; Muela-Zarzuela, Inés; Pastor-Maldonado, Carmen; Cilleros-Holgado, Paula; Gómez-Fernández, David; Álvarez-Córdoba, Mónica; Munuera-Cabeza, Manuel; Talaverón-Rey, Marta; Povea-Cabello, Suleva; Suárez-Carrillo, Alejandra; Piñero-Pérez, Rocío; Reche-López, Diana; Romero-Domínguez, José M; Sánchez-Alcázar, José Antonio

Alpha-lipoic acid supplementation corrects pathological alterations in cellular models of pantothenate kinase-associated neurodegeneration with residual PANK2 expression levels

补充α-硫辛酸可纠正泛酸激酶相关神经变性细胞模型中的病理改变,并保留 PANK2 表达水平

Marta Talaverón-Rey, Mónica Álvarez-Córdoba, Irene Villalón-García, Suleva Povea-Cabello, Juan M Suárez-Rivero, David Gómez-Fernández, Ana Romero-González, Alejandra Suárez-Carrillo, Manuel Munuera-Cabeza, Paula Cilleros-Holgado, Diana Reche-López, Rocío Piñero-Pérez, José A Sánchez-Alcázar

Pterostilbene in Combination With Mitochondrial Cofactors Improve Mitochondrial Function in Cellular Models of Mitochondrial Diseases

紫檀芪与线粒体辅助因子联合应用可改善线粒体疾病细胞模型中的线粒体功能

Juan M Suárez-Rivero,Carmen J Pastor-Maldonado,Ana Romero-González,David Gómez-Fernandez,Suleva Povea-Cabello,Mónica Álvarez-Córdoba,Irene Villalón-García,Marta Talaverón-Rey,Alejandra Suárez-Carrillo,Manuel Munuera-Cabeza,José A Sánchez-Alcázar

Activation of the Mitochondrial Unfolded Protein Response: A New Therapeutic Target?

线粒体未折叠蛋白反应的激活:一个新的治疗靶点?

Suárez-Rivero, Juan M; Pastor-Maldonado, Carmen J; Povea-Cabello, Suleva; Álvarez-Córdoba, Mónica; Villalón-García, Irene; Talaverón-Rey, Marta; Suárez-Carrillo, Alejandra; Munuera-Cabeza, Manuel; Reche-López, Diana; Cilleros-Holgado, Paula; Piñero-Pérez, Rocío; Sánchez-Alcázar, José A

UPRmt activation improves pathological alterations in cellular models of mitochondrial diseases

UPRmt 激活可改善线粒体疾病细胞模型中的病理改变

Juan M Suárez-Rivero, Carmen J Pastor-Maldonado, Suleva Povea-Cabello, Mónica Álvarez-Córdoba, Irene Villalón-García, Marta Talaverón-Rey, Alejandra Suárez-Carrillo, Manuel Munuera-Cabeza, Diana Reche-López, Paula Cilleros-Holgado, Rocío Piñero-Perez, José A Sánchez-Alcázar