日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Lower efficacy of transfusion of red blood cells from donors with sickle cell trait

输注镰状细胞性状供者的红细胞疗效较低。

Dzieciatkowska, Monika; Stephenson, Daniel; Hay, Ariel; Wang, Xunde; Keele, Gregory R; Nemkov, Travis; Deng, Xutao; Stone, Mars; Hansen, Kirk C; Kleinman, Steve; Norris, Philip J; Busch, Michael P; Page, Grier P; Spitalnik, Steven L; Roubinian, Nareg; Zimring, James C; Thein, Swee-Lay; D'Alessandro, Angelo

Pyruvate kinase deficiency modifies sickle hemoglobin carrier and sickle cell disease phenotypes in mice

丙酮酸激酶缺乏症会改变小鼠镰状血红蛋白携带者和镰状细胞病的表型。

Wang, Xunde; Smith, Meghann; Kamimura, Sayuri; Li, Quan; Shah, Niharika; Quezado, Martha; Almeida, Luis Ef; Vogel, Sebastian; Tegegn, Mickias B; Sun, Kevin Y; Villasmil, Rafael; Liu, Chengyu; Eaton, William A; Thein, Swee Lay; Quezado, Zenaide Mn

A population-scale Red Blood Cell proteome atlas of 13,000 donors uncovers genetically encoded aging clocks predicting hemolysis, transfusion efficacy, and donor activity a decade later

一项包含13000名献血者的群体规模红细胞蛋白质组图谱揭示了基因编码的衰老时钟,该时钟可预测十年后的溶血、输血疗效和献血者活性。

Dzieciatkowska, Monika; Issaian, Aaron V; Keele, Gregory R; Saviola, Anthony; Stephenson, Daniel; Bevers, Shaun; Reisz, Julie A; Haiman, Zachary B; Nemkov, Travis; Fang, Fang; Moore, Amy L; Deng, Xutao; Stone, Mars; Kleinman, Steve; Norris, Philip J; Wang, Xunde; Thein, Swee-Lay; Hod, Eldad A; Busch, Michael P; Roubinian, Nareg H; Page, Grier P; Hansen, Kirk C; D'Alessandro, Angelo

A machine learning-based workflow for predicting transplant outcomes in patients with sickle cell disease

基于机器学习的镰状细胞病患者移植结果预测工作流程

Li, Haiou; Sachdev, Vandana; Tian, Xin; Nguyen, My-Le; Hsieh, Matthew; Fitzhugh, Courtney; Limerick, Emily; Coles, Wynona; Asomaning, Nancy; Conrey, Anna; Wu, Colin O; Thein, Swee Lay

Fetal hemoglobin enables malaria parasite growth in sickle cells but augments production of transmission stage parasites

胎儿血红蛋白能够促进疟原虫在镰状细胞中的生长,但也会增强传播期疟原虫的产生。

Lavazec, Catherine; Loucoubar, Cheikh; Dupuy, Florian; Bureau, Jean-François; Casadémont, Isabelle; Gonçalves, Bronner; Thein, Swee Lay; Lathrop, Mark; Laurance, Sandrine; Roussel, Camille; Le Van Kim, Caroline; Colin, Yves; De Montalembert, Mariane; Sakuntabhai, Anavaj; Paul, Richard E

Sickle cell allele HBB-rs334(T) is associated with decreased risk of childhood Burkitt lymphoma in East Africa

镰状细胞等位基因HBB-rs334(T)与东非儿童伯基特淋巴瘤风险降低相关。

Hong, Hyokyoung G; Gouveia, Mateus H; Ogwang, Martin D; Kerchan, Patrick; Reynolds, Steven J; Tenge, Constance N; Were, Pamela A; Kuremu, Robert T; Wekesa, Walter N; Masalu, Nestory; Kawira, Esther; Kinyera, Tobias; Wang, Xunde; Zhou, Jiefu; Leal, Thiago Peixoto; Otim, Isaac; Legason, Ismail D; Nabalende, Hadijah; Dhudha, Herry; Mumia, Mediatrix; Baker, Francine S; Okusolubo, Temiloluwa; Ayers, Leona W; Bhatia, Kishor; Goedert, James J; Woo, Joshua; Manning, Michelle; Cole, Nathan; Luo, Wen; Hicks, Belynda; Chagaluka, George; Johnston, W Thomas; Mutalima, Nora; Borgstein, Eric; Liomba, George N; Kamiza, Steve; Mkandawire, Nyengo; Mitambo, Collins; Molyneux, Elizabeth M; Newton, Robert; Hutchinson, Amy; Yeager, Meredith; Adeyemo, Adebowale A; Thein, Swee Lay; Rotimi, Charles N; Chanock, Stephen J; Prokunina-Olsson, Ludmila; Mbulaiteye, Sam M

Functional and multi-omics signatures of mitapivat efficacy upon activation of pyruvate kinase in red blood cells from patients with sickle cell disease

米塔匹伐特激活镰状细胞病患者红细胞中丙酮酸激酶的功能和多组学特征

D'Alessandro, Angelo; Le, Kang; Lundt, Maureen; Li, Quan; Dunkelberger, Emily B; Cellmer, Troy; Worth, Andrew J; Patil, Spurthi; Huston, Chris; Grier, Abby; Dzieciatkowska, Monika; Stephenson, Daniel; Eaton, William A; Thein, Swee Lay

In vivo measurement of RBC survival in patients with sickle cell disease before or after hematopoietic stem cell transplantation

镰状细胞病患者造血干细胞移植前后红细胞存活率的体内测量

Alexis K Leonard, Dana Furstenau, Zaina Inam, Christina Luckett, Rebecca Chu, Selami Demirci, Khaled Essawi, Bjorg Gudmundsdottir, Malikiya Hinds, Julia DiNicola, Quan Li, William A Eaton, Troy Cellmer, Xunde Wang, Swee Lay Thein, Elizabeth R Macari, Sara VanNest, Matthew M Hsieh, Melissa Bonner, Fr

Therapeutic potential of the latest oxygen affinity-modifying agent, GBT021601, for treating sickle cell disease is questionable

最新氧亲和力调节剂GBT021601治疗镰状细胞病的疗效尚存疑问。

Alaimo, Braydon; Metaferia, Belhu; Cellmer, Troy; Thein, Swee Lay; Bunn, H Franklin; Eaton, William A

Mouse models of sickle cell disease: Imperfect and yet very informative

镰状细胞病小鼠模型:虽不完美,但信息量丰富

Kamimura, Sayuri; Smith, Meghann; Vogel, Sebastian; Almeida, Luis E F; Thein, Swee Lay; Quezado, Zenaide M N